scholarly journals Hereditary Angioedema-Associated Acute Pancreatitis in C1-Inhibitor Deficient and Normal C1-Inhibitor Patients: Case Reports and Literature Review

2019 ◽  
Vol 6 ◽  
Author(s):  
Camila Lopes Veronez ◽  
Régis Albuquerque Campos ◽  
Rosemeire Navickas Constantino-Silva ◽  
Priscila Nicolicht ◽  
João Bosco Pesquero ◽  
...  
2013 ◽  
Vol 88 (4) ◽  
pp. 578-584 ◽  
Author(s):  
Amanda Rodrigues Miranda ◽  
Ana Paula Fusel de Ue ◽  
Dominique Vilarinho Sabbag ◽  
Wellington de Jesus Furlani ◽  
Patricia Karla de Souza ◽  
...  

In this article, three cases of hereditary angioedema (HAE) type III (estrogen-dependent or with normal C1 inhibitor) are reported. The HAE was initially described in women of the same family in association with high-leveled estrogenic conditions such as the use of oral contraceptives and pregnancy. There is no change in the C1 inhibitor as happens in other types of hereditary angioedema, and mutations are observed in the encoding gene of the XII factor of coagulation in several patients. The current diagnosis is mainly clinical and treatment consists in the suspension of the triggering factors and control of acute symptoms. A brief review of physiopathology, clinical features, genetic alterations and treatment are also presented.


2020 ◽  
Vol 8 (6) ◽  
pp. 1875-1880.e3
Author(s):  
Joel P. Brooks ◽  
Cristine Radojicic ◽  
Marc A. Riedl ◽  
Scott D. Newcomer ◽  
Aleena Banerji ◽  
...  

2011 ◽  
Vol 34 (1) ◽  
pp. 60-63 ◽  
Author(s):  
Ibolya Czaller ◽  
Katalin Molnár ◽  
Dorottya Csuka ◽  
Lilian Varga ◽  
Henriette Farkas

Lupus ◽  
2020 ◽  
pp. 096120332096570
Author(s):  
Juliana P Ocanha-Xavier ◽  
Camila O Cola-Senra ◽  
Jose Candido C Xavier-Junior

Reticular erythematous mucinosis (REM) was first described 50 years ago, but only around 100 case reports in English have been published. Its relation with other inflammatory skin disorders is still being debated. We report a case of REM, including the clinical and histopathological findings. Also, a systematic review of 94 English-language reported cases is provided. The described criteria for clinical and histopathological diagnosis are highlighted in order to REM can be confidently diagnosed.


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