scholarly journals Single Ventricle—A Comprehensive Review

Children ◽  
2021 ◽  
Vol 8 (6) ◽  
pp. 441
Author(s):  
P. Syamasundar Rao
Keyword(s):  
Single Ventricle ◽  
Management Strategies ◽  
Fontan Circulation ◽  
Cardiac Defects ◽  
Comprehensive Review ◽  
Single Ventricle Physiology ◽  
Alternative Approaches

In this paper, the author enumerates cardiac defects with a functionally single ventricle, summarizes single ventricle physiology, presents a summary of management strategies to address the single ventricle defects, goes over the steps of staged total cavo-pulmonary connection, cites the prevalence of inter-stage mortality, names the causes of inter-stage mortality, discusses strategies to address the inter-stage mortality, reviews post-Fontan issues, and introduces alternative approaches to Fontan circulation.

scholarly journals Combined heart-liver transplantation for failing Fontan circulation in a late survivor with single-ventricle physiology

2017 ◽  
Vol 4 (4) ◽  
pp. 675-678 ◽  
Author(s):  
Phuoc Duong ◽  
Louise Coats ◽  
John O'Sullivan ◽  
David Crossland ◽  
Beate Haugk ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Single Ventricle ◽  
Fontan Circulation ◽  
Single Ventricle Physiology ◽  
Failing Fontan

scholarly journals Single-Ventricle Physiology

2020 ◽  
Vol 13 (2) ◽  
pp. 94-98
Author(s):  
Lydia Taranto ◽  
Tabitha Moe
Keyword(s):  
Single Ventricle ◽  
Venous Return ◽  
Heart Defects ◽  
Fontan Procedure ◽  
Management Strategies ◽  
Single Ventricle Physiology ◽  
Passive Flow ◽  
Patient’S Experience ◽  
The Common ◽  
The Right

Single-ventricle physiology occurs in patients with hypoplastic ventricular heart defects, either on the right or left, who have undergone stepwise palliation surgeries ending with the Fontan procedure. After Fontan completion, these patients are dependent on passive venous return to the pulmonary circulation. The implications of passive flow are potentially devastating to the patient. We discuss some of the basic changes to the patient’s experience after a Fontan procedure, as well as the common complications. We also touch on some of the emerging management strategies for the common complications.

Preoperative Stabilization of Infants With Hypoplastic Left Heart Syndrome Before Stage I Palliation

2016 ◽  
Vol 36 (1) ◽  
pp. 52-59 ◽  
Author(s):  
Amy Donnellan ◽  
Lindsey Justice
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Single Ventricle ◽  
Management Strategies ◽  
Ventilatory Support ◽  
Practice Variation ◽  
Severe Form ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Single Ventricle Physiology ◽  
Left Heart Syndrome

Hypoplastic left heart syndrome is a severe form of congenital heart disease that results in single-ventricle physiology. Although surgical palliation in infants with this syndrome is widely agreed on in practice, variation occurs in both surgical and medical management. Perinatal factors that affect preoperative management include the subtype of the syndrome and the patient’s birth weight, gestational age, and genetic abnormalities. The general aspects of perioperative stabilization and management are monitoring, use of vasoactive infusions, ventilatory support, and nutrition. Management strategies for balancing single-ventricle physiology are aimed at addressing the 3 major causes of desaturation: diminished pulmonary blood flow, low mixed venous oxygen saturation, and pulmonary venous desaturation.

The neuroendocrinal system of the heart after construction of a Glenn anastomosis or the Fontan circulation

2005 ◽  
Vol 15 (S3) ◽  
pp. 21-25 ◽  
Author(s):  
Simona Vittorini ◽  
Simona Storti ◽  
Maria Serena Parri ◽  
Riccardo Moschetti ◽  
Luigi Scebba ◽  
...  
Keyword(s):  
Single Ventricle ◽  
Fontan Circulation ◽  
Relative Resistance ◽  
Cardiac Defects ◽  
Vascular Beds

Many complex cardiac defects produce a functionally single ventricle, in which there is mixing of the systemic and pulmonary circulations. The output from the functionally single ventricle is divided between the two circulations: the proportion going to the systemic and pulmonary vascular beds being determined by the relative resistance to flows within the respective circulations.

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