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Brain RNA-Seq Profiling of the Mucopolysaccharidosis Type II Mouse Model
International Journal of Molecular Sciences
◽
10.3390/ijms18051072
◽
2017
◽
Vol 18
(5)
◽
pp. 1072
◽
Cited By ~ 9
Author(s):
Marika Salvalaio
◽
Francesca D’Avanzo
◽
Laura Rigon
◽
Alessandra Zanetti
◽
Michela D’Angelo
◽
...
Keyword(s):
Mouse Model
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Rna Seq
◽
Mucopolysaccharidosis Type Ii
Download Full-text
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Cited By
References
Characterization of a novel mucopolysaccharidosis type II mouse model and recombinant AAV2/8 vector-mediated gene therapy
Molecules and Cells
◽
10.1007/s10059-010-0083-2
◽
2010
◽
Vol 30
(1)
◽
pp. 13-18
◽
Cited By ~ 25
Author(s):
Sung-Chul Jung
◽
Eun-Sook Park
◽
Eun Nam Choi
◽
Chi Hwa Kim
◽
Su Jin Kim
◽
...
Keyword(s):
Gene Therapy
◽
Mouse Model
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
Download Full-text
Neurologic improvement in a mouse model of Hunter syndrome (mucopolysaccharidosis type II) by treatment with AAV9 vector after the development of cognitive dysfunction
Molecular Genetics and Metabolism
◽
10.1016/j.ymgme.2016.11.274
◽
2017
◽
Vol 120
(1-2)
◽
pp. S107-S108
Author(s):
Kelly M Podetz-Pedersen
◽
Kanut Laoharawee
◽
Tam T Nguyen
◽
Sajya M Singh
◽
Lucy Vulchanova
◽
...
Keyword(s):
Mouse Model
◽
Cognitive Dysfunction
◽
Hunter Syndrome
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
Download Full-text
Blood-brain barrier-penetrating iduronate-2-sulfatase reduces brain glycosaminoglycans in mouse model of mucopolysaccharidosis type II
Molecular Genetics and Metabolism
◽
10.1016/j.ymgme.2017.12.368
◽
2018
◽
Vol 123
(2)
◽
pp. S134
Author(s):
Hiroyuki Sonoda
◽
Hideto Morimoto
◽
Eiji Yoden
◽
Yuri Koshimura
◽
Masafumi Kinoshita
◽
...
Keyword(s):
Mouse Model
◽
Blood Brain Barrier
◽
Brain Barrier
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
◽
Blood Brain
Download Full-text
1024. Electrogene Transfer in Mucopolysaccharidosis Type II Mouse Model Induces High-Level Production of Iduronate-2-Sulfatase in the Skeletal Muscle
Molecular Therapy
◽
10.1016/s1525-0016(16)41466-8
◽
2003
◽
Vol 7
(5)
◽
pp. S395
Keyword(s):
Skeletal Muscle
◽
Mouse Model
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
◽
High Level
◽
Level Production
Download Full-text
Identification of age-dependent motor and neuropsychological behavioural abnormalities in a mouse model of Mucopolysaccharidosis Type II
PLoS ONE
◽
10.1371/journal.pone.0172435
◽
2017
◽
Vol 12
(2)
◽
pp. e0172435
◽
Cited By ~ 10
Author(s):
Hélène F. E. Gleitz
◽
Claire O’Leary
◽
Rebecca J. Holley
◽
Brian W. Bigger
Keyword(s):
Mouse Model
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
◽
Age Dependent
Download Full-text
A commentary on high-dose enzyme replacement therapy attenuates cerebroventriculomegaly in a mouse model of mucopolysaccharidosis type II
Journal of Human Genetics
◽
10.1038/jhg.2013.115
◽
2013
◽
Vol 58
(12)
◽
pp. 767-768
Author(s):
Maria L Escolar
Keyword(s):
Mouse Model
◽
Enzyme Replacement Therapy
◽
Replacement Therapy
◽
High Dose
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
◽
Enzyme Replacement
Download Full-text
Effect of systemic high dose enzyme replacement therapy on the improvement of CNS defects in a mouse model of mucopolysaccharidosis type II
Orphanet Journal of Rare Diseases
◽
10.1186/s13023-015-0356-0
◽
2015
◽
Vol 10
(1)
◽
Cited By ~ 9
Author(s):
Sung Yoon Cho
◽
Jeehun Lee
◽
Ah-Ra Ko
◽
Min Jung Kwak
◽
Sujin Kim
◽
...
Keyword(s):
Mouse Model
◽
Enzyme Replacement Therapy
◽
Replacement Therapy
◽
High Dose
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
◽
Enzyme Replacement
Download Full-text
Genistein reduces glycosaminoglycan levels in a mouse model of mucopolysaccharidosis type II
British Journal of Pharmacology
◽
10.1111/j.1476-5381.2009.00565.x
◽
2010
◽
Vol 159
(5)
◽
pp. 1082-1091
◽
Cited By ~ 52
Author(s):
A Friso
◽
R Tomanin
◽
M Salvalaio
◽
M Scarpa
Keyword(s):
Mouse Model
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
Download Full-text
High-dose enzyme replacement therapy attenuates cerebroventriculomegaly in a mouse model of mucopolysaccharidosis type II
Journal of Human Genetics
◽
10.1038/jhg.2013.92
◽
2013
◽
Vol 58
(11)
◽
pp. 728-733
◽
Cited By ~ 8
Author(s):
So Yoon Ahn
◽
Yun Sil Chang
◽
Dong Kyung Sung
◽
Ah-ra Ko
◽
Chi Hwa Kim
◽
...
Keyword(s):
Mouse Model
◽
Enzyme Replacement Therapy
◽
Replacement Therapy
◽
High Dose
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
◽
Enzyme Replacement
Download Full-text
484. In Vivo Zinc-Finger Nuclease Mediated Iduronate-2-Sulfatase (IDS) Target Gene Insertion and Correction of Metabolic Disease in a Mouse Model of Mucopolysaccharidosis Type II (MPS II)
Molecular Therapy
◽
10.1016/s1525-0016(16)33293-2
◽
2016
◽
Vol 24
◽
pp. S192
◽
Cited By ~ 1
Author(s):
Kanut Laoharawee
◽
Russell DeKelver
◽
Kelly M. Podetz-Petersen
◽
Susan Tom
◽
Robert Radeke
◽
...
Keyword(s):
Metabolic Disease
◽
Mouse Model
◽
Zinc Finger
◽
Target Gene
◽
Mucopolysaccharidosis Type
◽
Type Ii
◽
Mucopolysaccharidosis Type Ii
◽
Gene Insertion
◽
Mps Ii
Download Full-text
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