Faculty Opinions recommendation of Speech and language outcomes of cochlear implantation in children with isolated auditory neuropathy versus cochlear hearing loss.

2014 ◽  
Author(s):  
Marc Bennett
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Auditory Neuropathy ◽  
Language Outcomes ◽  
Speech And Language ◽  
Cochlear Hearing Loss

Speech and Language Outcomes of Cochlear Implantation in Children With Isolated Auditory Neuropathy Versus Cochlear Hearing Loss

2013 ◽  
Vol 34 (9) ◽  
pp. 1615-1621 ◽  
Author(s):  
Cameron L. Budenz ◽  
Kelly Starr ◽  
Caroline Arnedt ◽  
Steven A. Telian ◽  
Henry Alexander Arts ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Auditory Neuropathy ◽  
Language Outcomes ◽  
Speech And Language ◽  
Cochlear Hearing Loss

Outcomes of Cochlear Implantation in Children With Isolated Auditory Neuropathy Versus Cochlear Hearing Loss

2013 ◽  
Vol 34 (3) ◽  
pp. 477-483 ◽  
Author(s):  
Cameron L. Budenz ◽  
Steven A. Telian ◽  
Caroline Arnedt ◽  
Kelly Starr ◽  
Henry Alexander Arts ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Auditory Neuropathy ◽  
Cochlear Hearing Loss

Cochlear Implant Outcomes in Patients with Neurosarcoidosis

2021 ◽  
pp. 1-7
Author(s):  
Dario Ebode ◽  
Fleur Cohen-Aubart ◽  
Stéphanie Trunet ◽  
Evelyne Ferrary ◽  
Ghizlène Lahlou ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Case Series ◽  
Corticosteroid Treatment ◽  
Auditory Neuropathy ◽  
Disease Exacerbation ◽  
Profound Hearing Loss ◽  
Hearing Recovery ◽  
Speech Performance

<b><i>Introduction:</i></b> Audiovestibular symptoms are rare in sarcoidosis, but they may also be the first manifestation of the disease. Sudden or progressive bilateral hearing loss is usually associated with vestibular impairment. The mechanism of hearing loss remains unclear, but clinical presentation and magnetic resonance imaging suggest a retrocochlear site for the lesion in most patients. Several cases of hearing recovery after corticosteroid treatment have been reported. In patients with severe or profound hearing loss, the benefit of cochlear implantation is challenging to predict in the case of auditory neuropathy and is rarely described. We present a case series of cochlear implantation in patients with documented neurosarcoidosis. <b><i>Results:</i></b> Seven cases of cochlear implantation in 4 patients with neurosarcoidosis are reported. All of the patients showed a great improvement very quickly in both quiet and noise. Speech performance remained stable over time with a follow-up ranging from 4 to 11 years, even in patients who had disease exacerbation. <b><i>Conclusion:</i></b> Cochlear implantation is possible in deaf patients with neurosarcoidosis. The excellent benefit obtained in our patients suggests a particular type of neuropathy, but endocochlear involvement cannot be entirely ruled out.

scholarly journals Preschool speech intelligibility and vocabulary skills predict long-term speech and language outcomes following cochlear implantation in early childhood

2013 ◽  
Vol 15 (4) ◽  
pp. 200-210 ◽  
Author(s):  
Irina Castellanos ◽  
William G Kronenberger ◽  
Jessica Beer ◽  
Shirley C Henning ◽  
Bethany G Colson ◽  
...  
Keyword(s):  
Early Childhood ◽  
Cochlear Implantation ◽  
Speech Intelligibility ◽  
Language Outcomes ◽  
Speech And Language ◽  
Vocabulary Skills

scholarly journals Cochlear Implants and Children with Vestibular Impairments

2018 ◽  
Vol 39 (03) ◽  
pp. 305-320 ◽  
Author(s):  
Blake Papsin ◽  
Sharon Cushing
Keyword(s):  
Hearing Loss ◽  
Cochlear Implants ◽  
Sensory Deficit ◽  
Screening Methods ◽  
Language Outcomes ◽  
Speech And Language ◽  
Vestibular Loss ◽  
Acquired Hearing Loss ◽  
Speech And Language Development ◽  
The Impact

AbstractSensorineural hearing loss (SNHL) in children occurs in 1 to 3% of live births and acquired hearing loss can additionally occur. This sensory deficit has far reaching consequences that have been shown to extend beyond speech and language development. Thankfully there are many therapeutic options that exist for these children with the aim of decreasing the morbidity of their hearing impairment. Of late, focus has shifted beyond speech and language outcomes to the overall performance of children with SNHL in real-world environments. To account for their residual deficits in such environments, clinicians must understand the extent of their sensory impairments. SNHL commonly coexists with other sensory deficits such as vestibular loss. Vestibular impairment is exceedingly common in children with SNHL with nearly half of children exhibiting vestibular end-organ dysfunction. These deficits naturally lead to impairments in balance and delay in motor milestones. However, this additional sensory deficit likely leads to further impairment in the performance of these children. This article focuses on the following:1. Defining the coexistence of vestibular impairment in children with SNHL and cochlear implants.2. Describing screening methods aimed at identifying vestibular dysfunction in children with SNHL.3. Understanding the functional implications of this dual-sensory impairment.4. Exploring possible rehabilitative strategies to minimize the impact of vestibular impairment in children with SNHL

The audiovestibular profile of Brown-Vialetto-Van Laere syndrome

2021 ◽  
Vol 135 (11) ◽  
pp. 1000-1009
Author(s):  
R Omar ◽  
K Rajput ◽  
T Sirimanna ◽  
S Rajput ◽  
W Pagarkar
Keyword(s):  
Hearing Loss ◽  
Characteristic Feature ◽  
Motor Function ◽  
Cochlear Implantation ◽  
Cranial Nerve ◽  
Vestibular Function ◽  
Auditory Neuropathy ◽  
Spectrum Disorder ◽  
Significant Heterogeneity ◽  
Auditory Neuropathy Spectrum Disorder

AbstractBackgroundBrown-Vialetto-Van Laere syndrome, a rare disorder associated with motor, sensory and cranial nerve neuropathy, is caused by mutations in riboflavin transporter genes SLC52A2 and SLC52A3. Hearing loss is a characteristic feature of Brown-Vialetto-Van Laere syndrome and has been shown in recent studies to be characterised by auditory neuropathy spectrum disorder.MethodThis study reports the detailed audiovestibular profiles of four cases of Brown-Vialetto-Van Laere syndrome with SLC52A2 and SLC52A3 mutations. All of these patients had auditory neuropathy spectrum disorder.ResultsThere was significant heterogeneity in vestibular function and in the benefit gained from cochlear implantation. The audiological response to riboflavin therapy was also variable, in contrast to generalised improvement in motor function.ConclusionWe suggest that comprehensive testing of vestibular function should be conducted in Brown-Vialetto-Van Laere syndrome, in addition to serial behavioural audiometry as part of the systematic examination of the effects of riboflavin.

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