The impact of cochlear implantation on speech and language outcomes in children with asymmetric sensorineural hearing loss

Author(s):  
Prashant S. Malhotra ◽  
Jaron Densky ◽  
Manasa Melachuri ◽  
Samyuktha Melachuri ◽  
Amanda Onwuka ◽  
...  
2021 ◽  
Vol 141 ◽  
pp. 110558
Author(s):  
Chengetai Mahomva ◽  
Anne Kim ◽  
Judith E.C. Lieu ◽  
Donald M. Goldberg ◽  
Samantha Anne

Author(s):  
Dmitry Zabolotny ◽  
Viktor Lutsenko ◽  
Irina Belyakova ◽  
Tetiana Kholodenko

Relevance: Any kind of the hearing loss, especially in the childhood, affects the mental and intellectual development negatively as well as behavior and social position of a deaf patient in the hearing world. Cochlear implantation is the most effective and reliable method of medical and educational auditory-speech rehabilitation for both adults and children with severe hearing loss and deafness. One of the key performance indicators of the cochlear implantation is a result of speech audiometry, especially on the noise background. The aim is to study the state of auditory function according to the subjective audiometry in the noise background and the influence of various factors on the effectiveness of rehabilitation of the children after cochlear implantation. Materials and methods: The study involved 150 children with severe sensorineural hearing loss and deafness after cochlear implantation. In age, they ranged from 3 to 18 years old. Evaluation of the efficiency of cochlear implantation was carried out in several stages. All studies were done in the free-field with the cochlear implant on. At first, we performed the pure tone audiometry. Then we defined the 50% intelligibility threshold of numeral test. After that, we defined a word recognition percentage. And finally we defined the impact of masker on speech intelligibility at SPL of useful signal 50, 60 and 80 dB. Results: Based on the analysis of the received data, all children with severe sensorineural hearing loss and deafness after cochlear implantation were divided into 3 groups depending on the speech intelligibility. The first group (high efficiency of cochlear implantation) included 68 children (45,3%). This group was divided into two subgroups depending on the difference between the values of the speech intelligibility in the free sound field and in the noise background. The second group (average efficiency) consisted of 45 children (30%). The third group (low efficiency) were 37 children (24,7%). The influence of various factors on the efficiency of cochlear implantation was analyzed. Conclusion: Speech intelligibility in the noise background must be examinated in all children after cochlear implantation. The main factors affecting the effectiveness of cochlear implantation according to test of speech intelligibility in the noise background are the ethiology of hearing loss and duration of post-operation period. Results of speech intelligibility in the noise background test will help specialists who practice the rehabilitation of children after cochlear implantation (teachers for deaf, speech therapists) to pay attention to the decrease of speech intelligibility in children in the real conditions of communication and to focus their efforts on its improving with the appropriate methods.


2016 ◽  
Vol 130 (4) ◽  
pp. 408-411 ◽  
Author(s):  
R Omichi ◽  
S Kariya ◽  
Y Maeda ◽  
K Nishizaki

AbstractBackground:Superficial siderosis is a rare disease that results from chronic bleeding in the subarachnoid space. Haemosiderin deposits throughout the subpial layers of the brain and spinal cord lead to progressive sensorineural hearing loss, which is seen in 95 per cent of patients with superficial siderosis. The impact of cochlear implantation on the quality of life of superficial siderosis patients is under debate.Case report:A 38-year-old male with superficial siderosis presented with bilateral progressive sensorineural hearing loss. The patient underwent cochlear implantation and his quality of life was improved as evaluated by the Abbreviated Profile of Hearing Aid Benefit inventory.Conclusion:The remarkable improvement in Abbreviated Profile of Hearing Aid Benefit scores shown in this study indicates that cochlear implantation leads to a better quality of life in superficial siderosis patients.


2021 ◽  
pp. 014556132110091
Author(s):  
Robin Rupp ◽  
Joachim Hornung ◽  
Matthias Balk ◽  
Matti Sievert ◽  
Sarina Müller ◽  
...  

Objective: To investigate the anatomical status of the round window niche and hearing outcome of cochlear implantation (CI) after explorative tympanotomy (ExT) with sealing of the round window membrane in patients with sudden sensorineural hearing loss at a tertiary referral medical center. Methods: Between January 1, 2007, and July 30, 2020, 1602 patients underwent CI at our department. Out of these, all patients previously treated by ExT with sealing of the round window membrane because of unilateral sudden hearing loss were included in the study. A retrospective chart review was conducted concerning method of round window membrane sealing, intraoperative findings during CI, postoperative imaging, and hearing results. Results: Twenty one patients (9 females; 8 right ears; 54.3 years [± 12.9 years]) underwent ExT with sealing of the round window membrane with subsequent CI after 26.6 months (± 32.9 mo) on average. During CI, in 76% of cases (n = 16), the round window niche was blocked by connective tissue due to the previous intervention but could be removed completely in all cases. The connective tissue itself and its removal had no detrimental effects on the round window membrane. Postoperative computed tomography scan showed no electrode dislocation. Mean postoperative word recognition score after 3 months was 57.4% (± 17.2%) and improved significantly to 73.1% (± 16.4%, P = .005) after 2 years. Conclusion: Performing CI after preceding ExT, connective tissue has to be expected blocking the round window niche. Remaining tissue can be removed safely and does not alter the round window membrane allowing for a proper electrode insertion. Short- and long-term hearing results are satisfactory. Consequently, ExT with sealing of the round window membrane in patients with sudden sensorineural hearing loss does not impede subsequent CI that can still be performed safely.


2013 ◽  
Vol 127 (7) ◽  
pp. 708-711 ◽  
Author(s):  
A C Hall ◽  
A C Leong ◽  
D Jiang ◽  
A Fitzgerald-O'Connor

AbstractBackground:Bilateral sensorineural hearing loss associated with recurrent urticarial skin lesions may be signs of underlying Muckle–Wells syndrome. Previous reports have described the hearing loss to be progressive in nature.Method:To our knowledge, this paper presents the first published case of sudden onset, bilateral sensorineural hearing loss associated with urticarial vasculitis due to underlying Muckle–Wells syndrome.Results:The patient underwent a cochlear implantation with a modest outcome.Conclusion:Cochlear implantation may help to rehabilitate sudden hearing loss associated with this condition, but early diagnosis may allow treatment with interleukin-1β inhibitors such as anakinra.


Author(s):  
Gaelle Vofo ◽  
Marrigje Aagje de Jong ◽  
Michal Kaufman ◽  
Julia Meyler ◽  
Ron Eliashar ◽  
...  

Abstract Objectives Idiopathic sudden sensorineural hearing loss (SSNHL) represents a frequently encountered otological entity, of various types and severity, with an array of associated symptoms including vertigo. This is a devastating life-changing condition with a blurry prognosis. The objective of this study was to determine the clinical association of vestibular impairment by electronystagmography (ENG) and caloric tests, and their ability to predict prognosis. Methods An observational, crossectional study was carried out amongst patients admitted with SSNHL. Each consenting patient had an audiometry test performed on admission as well as ENG and caloric tests. Treatment included oral steroids and carbogen with intratympanic steroids used only as salvage treatment. Follow-up was completed after 6 months when hearing gains were evaluated. Finally, an association was sought between the rate of recovery and ENG and caloric test results. Results Of 35 patients included, marked recovery was seen in patients without vertigo when compared to those with vertigo (p=0.003). A statistically significant association was found between the presence of vertigo and hearing deterioration (p=0.008). More so, normal electronystagmography results were associated with marked recovery (p=0.04). Conclusions The vestibular end organs are both subjectively and objectively affected in SSNHL as demonstrated by the abnormal ENG and caloric tests in our study despite the small sample size. Concomitant vestibular involvement carries poorer prognosis and routine identification may help foresee the recovery of patients with SSNHL and as such, aid in patient counseling. ENG and caloric tests are easily available and may be recommended for all patients with SSNHL.


2008 ◽  
Vol 123 (7) ◽  
pp. 811-816 ◽  
Author(s):  
A D Mace ◽  
M S Ferguson ◽  
M Offer ◽  
K Ghufoor ◽  
M J Wareing

AbstractObjective:To present the first published case of a child with bilateral profound sudden sensorineural hearing loss found in association with sickle cell anaemia, and to demonstrate the importance of early recognition, investigation and empirical treatment of sudden sensorineural hearing loss.Method:Case report and review of world literature.Case report:The authors present the case of a seven-year-old child with known sickle cell anaemia, who presented with bilateral profound sensorineural hearing loss developing over a period of five days. There was a history of ophthalmological disease in the preceding weeks, and inflammatory markers were raised. The differential diagnosis included a vaso-occlusive or inflammatory aetiology such as Cogan's syndrome, and treatment for both was instigated. Hearing thresholds did not recover, and the patient underwent cochlear implantation 12 weeks later.Conclusion:Sudden sensorineural hearing loss has a variable aetiology and is rare in children. Immediate treatment for all possible aetiologies is essential, along with targeted investigations and early referral for cochlear implantation if no recovery is demonstrated.


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