Localised forms of pulmonary amyloidosis

ABSTRACT Amyloidosis is a heterogeneous group of diseases characterized by the extracellular deposition of misfolded proteins that can affect either systemically or locally confined to one system. Pulmonary amyloidosis is rare and can be classified into three forms according to the anatomic site of involvement: nodular pulmonary amyloidosis, tracheobronchial amyloidosis and diffuse alveolar-septal amyloidosis. The former two usually represent localized amyloid disease and the latter represents systemic disease. Typically lung parenchymal and tracheobronchial amyloidosis do not present together in localized forms of pulmonary amyloidosis. Here we report a unique case of localized pulmonary immunoglobulin light-chain amyloidosis, manifested as both parenchymal nodules and tracheobronchial amyloid deposition.

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Pulmonary amyloidosis and cystic lung disease in primary Sjögren’s syndrome: a case report and literature review

Clinical Rheumatology ◽

10.1007/s10067-021-05596-9 ◽

2021 ◽

Author(s):

Haiyun Li ◽

Yuewu Lu

Keyword(s):

Case Report ◽

Literature Review ◽

Lung Disease ◽

Sjogren's Syndrome ◽

Primary Sjögren’S Syndrome ◽

Primary Sjogren’S Syndrome ◽

Primary Sjögren's Syndrome ◽

Cystic Lung ◽

Cystic Lung Disease ◽

Pulmonary Amyloidosis

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Intralobular septal thickening on chest CT in a patient with pulmonary amyloidosis: a rare case study

Thorax ◽

10.1136/thoraxjnl-2016-209036 ◽

2016 ◽

Vol 72 (7) ◽

pp. 673-674

Author(s):

Yasuhito Suzuki ◽

Junpei Saito ◽

Ryuichi Togawa ◽

Hiroyuki Minemura ◽

Mitsuru Munakata

Keyword(s):

Rare Case ◽

Chest Ct ◽

Pulmonary Amyloidosis

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On primary pulmonary amyloidosis

European Journal of Radiology ◽

10.1016/j.ejrad.2011.04.005 ◽

2012 ◽

Vol 81 (8) ◽

pp. 1968 ◽

Cited By ~ 1

Author(s):

Xin Jiang ◽

Guifang Wang

Keyword(s):

Pulmonary Amyloidosis

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PULMONARY AMYLOIDOSIS IN FAMILIAL MEDITERRANEAN FEVER

Acta Clinica Belgica ◽

10.1179/acb.2006.024 ◽

2006 ◽

Vol 61 (3) ◽

pp. 147-151 ◽

Cited By ~ 6

Author(s):

C. Şahan ◽

K. Cengiz

Keyword(s):

Familial Mediterranean Fever ◽

Mediterranean Fever ◽

Pulmonary Amyloidosis

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Multiple calcified nodules in pulmonary amyloidosis

Journal of the Belgian Society of Radiology ◽

10.5334/jbr-btr.133 ◽

2014 ◽

Vol 97 (6) ◽

pp. 370 ◽

Cited By ~ 1

Author(s):

C Gernay ◽

L Médart

Keyword(s):

Pulmonary Amyloidosis

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A Case of Solitary Nodular Pulmonary Amyloidosis

CHEST Journal ◽

10.1378/chest.1994702 ◽

2014 ◽

Vol 146 (4) ◽

pp. 625A

Author(s):

Augustine Andoh-Duku ◽

Dhaval Raval ◽

Samaan Rafeq ◽

Hisushi Tsukada

Keyword(s):

Pulmonary Amyloidosis

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Pulmonary amyloidosis

Oxford Textbook of Medicine ◽

10.1093/med/9780199204854.003.181408 ◽

2010 ◽

pp. 3451-3452

Author(s):

D.J. Hendrick

Keyword(s):

Lung Nodules ◽

Diffuse Infiltration ◽

Interstitial Disease ◽

Pulmonary Amyloidosis ◽

Parenchymal Lung

Amyloidosis rarely affects the lungs, but when it does, primary (AL) disease usually produces benign masses of amyloid tissue in the central airways or the parenchyma, and secondary (AA) disease typically causes diffuse infiltration of alveolar walls and interstitium. Laryngotracheobronchial deposits sometimes require resection if they are causing obstruction; parenchymal lung nodules rarely need to be removed, providing their histological nature is not in doubt; the prognosis of diffuse alveolar–interstitial disease is poor....

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