A Revision Surgery for Cochlear Implantation in a Case of Incomplete Partition Type I

Background: Patients with cochlear malformations were long considered poor candidates for cochlear implantation (CI), and surgical approaches different than the standard facial recess approach were used to access the inner ear. There is no previous long-term follow-up of a patient with significantly malformed inner ear operated through an untraditional route and requiring a revision surgery. Purpose: This case provides a long-term follow-up from the initial surgery, a short-term follow-up from the revision surgery, and it illustrates the evolving classification of inner ear malformations as well as the potential problems associated with nonstandard approaches to the cochlea. Research Design: A case report. Intervention: Herein, we report a case of revision CI in a patient with incomplete partition type I, through the round window via a facial recess approach, 18 yr after an initial implantation via a transmastoid labyrinthotomy approach. Results: The patient had an uncomplicated surgery, and after activation, she noted auditory perception on all electrodes without facial stimulation. A sound field sound awareness threshold was obtained at 15 dB HL. Conclusions: As the prior generation of cochlear implant recipients ages, the probability of a revision surgery for various causes increases. Cochlear implant surgeons should be aware of the potential pitfalls associated in these often challenging cases.

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Long-Term Follow-Up After Maxillary Sinus Balloon Sinuplasty and ESS

Ear Nose & Throat Journal ◽

10.1177/0145561320986030 ◽

2021 ◽

pp. 014556132098603

Author(s):

Anni Koskinen ◽

Marie Lundberg ◽

Markus Lilja ◽

Jyri Myller ◽

Matti Penttilä ◽

...

Keyword(s):

Maxillary Sinus ◽

Revision Surgery ◽

University Hospital ◽

Sinus Surgery ◽

Control Group ◽

University Hospitals ◽

Balloon Sinuplasty ◽

Long Term Follow Up

Objectives: The aim of this controlled follow-up study was to compare the need for revision surgery, long-term efficacy, and satisfaction in chronic rhinosinusitis patients who had undergone maxillary sinus operation with either balloon sinuplasty or traditional endoscopic sinus surgery (ESS) technique. Methods: Thirty-nine ESS patients and 36 balloon patients of our previously described cohort, who had been primarily operated in 2008 to 2010, were contacted by phone. Symptoms, satisfaction, and need for revision surgery were asked. In addition, we collected data of patients who had undergone primary maxillary sinus balloon sinuplasty in the Helsinki University Hospital during the years 2005 to 2019. As a control group, we collected data of patients who had undergone primary maxillary sinus ESS at 3 Finnish University Hospitals, and 1 Central Hospital in years 2005, 2008, and 2011. Results: Altogether, 77 balloon patients and 82 ESS patients were included. The mean follow-up time was 5.3 years in balloon group and 9.8 years in ESS group. Revision surgery was performed on 17 balloon patients and 6 ESS patients. In the survival analysis, the balloon sinuplasty associated significantly with a higher risk of revision surgery compared to ESS. According to the phone interviews, 82% of ESS patients and 75% of balloon patients were very satisfied with the primary operation. Conclusion: Although the patient groups expressed equal satisfaction and change in symptoms after the operations, the need for revision surgery was higher after balloon sinuplasty than after ESS. This should be emphasized when counselling patients regarding surgical options.

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Long-term follow-up of patients with Bartter syndrome type I and II

Nephrology Dialysis Transplantation ◽

10.1093/ndt/gfq119 ◽

2010 ◽

Vol 25 (9) ◽

pp. 2976-2981 ◽

Cited By ~ 30

Author(s):

E. Puricelli ◽

A. Bettinelli ◽

N. Borsa ◽

F. Sironi ◽

C. Mattiello ◽

...

Keyword(s):

Bartter Syndrome ◽

Type I ◽

Syndrome Type ◽

Long Term Follow Up

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Long-term follow-up of a girl with oro-facio-digital syndrome type I due to a mutation in the OFD 1 gene

Annales de Génétique ◽

10.1016/s0003-3995(02)01116-4 ◽

2002 ◽

Vol 45 (2) ◽

pp. 59-62 ◽

Cited By ~ 9

Author(s):

C. Stoll ◽

P. Sauvage

Keyword(s):

Type I ◽

Syndrome Type ◽

Long Term Follow Up

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Long Term Follow-Up of 103 Untreated Adult Patients with Type 1 Gaucher Disease

Journal of Clinical Medicine ◽

10.3390/jcm8101662 ◽

2019 ◽

Vol 8 (10) ◽

pp. 1662 ◽

Cited By ~ 10

Author(s):

Dinur ◽

Zimran ◽

Becker-Cohen ◽

Arkadir ◽

Cozma ◽

...

Keyword(s):

Gaucher Disease ◽

Substrate Reduction Therapy ◽

Type I ◽

Specific Therapy ◽

Substrate Reduction ◽

Long Term Follow Up ◽

Disease Specific

The introduction of disease-specific therapy for patients with type I Gaucher disease (GD1) was a revolution in the management of patients, but not without cost. Thus, the management of mildly affected patients is still debated. We herein report a long-term follow-up (median (range) of 20 (5–58) years) of 103 GD1 patients who have never received enzymatic or substrate reduction therapy. The median (range) platelet count and hemoglobin levels in last assessment of all but six patients who refused therapy (although recommended and approved) were 152 (56–408) × 103/mL and 13.1 (7.6–16.8) g/dL, respectively. Most patients had mild hepatosplenomegaly. Nine patients were splenectomized. No patient developed clinical bone disease. The median (range) lyso-Gb1 levels at last visit was 108.5 (8.1–711) ng/mL; lowest for patients with R496H/other and highest for patients refusing therapy. This rather large cohort with long follow-up confirms that mildly affected patients may remain stable for many years without GD-specific therapy. The challenge for the future, when newborn screening may detect all patients, is to be able to predict which of the early diagnosed patients is at risk for disease-related complications and therefore for early treatment, and who may remain asymptomatic or minimally affected with no need for disease-specific therapy.

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Successful cochlear implantation in a patient with Epstein syndrome during long-term follow-up

Auris Nasus Larynx ◽

10.1016/j.anl.2020.09.008 ◽

2020 ◽

Author(s):

Anjin Mori ◽

Hidehiko Takeda ◽

Marina Kobayashi ◽

Takeru Misawa ◽

Ryoko Watanabe ◽

...

Keyword(s):

Cochlear Implantation ◽

Long Term Follow Up ◽

Epstein Syndrome

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Neoglottis Reconstruction Following Total Laryngectomy: The Emory Experience

Otolaryngology ◽

10.1177/019459988209000509 ◽

1982 ◽

Vol 90 (5) ◽

pp. 569-575 ◽

Cited By ~ 8

Author(s):

Fred M.S. McConnel ◽

John Teichgraeber

Keyword(s):

Medical School ◽

Revision Surgery ◽

Total Laryngectomy ◽

Perioperative Complications ◽

Vocal Rehabilitation ◽

Early Results ◽

Emory University ◽

Long Term Follow Up

A number of studies over the last decade have reported on a viability of the primary neoglottis reconstruction after total laryngectomy. Early results have been encouraging, although operative and perioperative complications are higher than with a classic laryngectomy. This article reports on a series of 13 neoglottis reconstructions performed at Emory University Medical School using the techniques developed by Mario Staffiert, MD. During the course of the study, the overall success rate has fallen from 80% at three years to 54% at five years. With each succeeding year there has been an increasing need for revision surgery. The series emphasizes the need for long-term follow-up in any vocal rehabilitation procedure.

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