Surgical Treatment of Tetralogy of Fallot with Pulmonary Valve Agenesis in a 22 Years Old Patient

Summary Tetralogy of Fallot is the most common cyanogenic congenital heart defect. The diagnosis is based on clinical signs, ECG examination, ultrasound examination of the heart, additional imaging methods and invasive testing. The therapeutic approach to the patient with tetralogy is complex and based on conservative and radical methods. Patients who have not undergone a radical surgical intervention have a poor prognosis, whereas the prognosis is much better for patients who have been operated. The most common complication of the surgical treatment is the pulmonary valve insufficiency which usually requires reintervention, as was the case with our patient.

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Surgical treatment of tetralogy of Fallot with absent pulmonary valve syndrome

Asian Cardiovascular and Thoracic Annals ◽

10.1177/0218492315577726 ◽

2015 ◽

Vol 24 (5) ◽

pp. 470-472

Author(s):

Yuki Tanaka ◽

Takashi Miyamoto ◽

Yuji Naito ◽

Shuichi Yoshitake

Keyword(s):

Surgical Treatment ◽

Tetralogy Of Fallot ◽

Pulmonary Valve ◽

Absent Pulmonary Valve ◽

Absent Pulmonary Valve Syndrome

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Pulmonary valve preservation and restoration strategies for repair of tetralogy of Fallot

Cardiology in the Young ◽

10.1017/s1047951114001991 ◽

2014 ◽

Vol 24 (6) ◽

pp. 1088-1094 ◽

Cited By ~ 7

Author(s):

Constantine D. Mavroudis ◽

Jennifer Frost ◽

Constantine Mavroudis

Keyword(s):

Surgical Treatment ◽

Tetralogy Of Fallot ◽

Pulmonary Valve ◽

Right Ventricular Outflow Tract ◽

Ventricular Outflow Tract ◽

Pulmonary Insufficiency ◽

Transannular Patch ◽

Preservation And Restoration ◽

Restoration Strategies ◽

Initial Correction

AbstractDespite tremendous advances in surgical treatment of tetralogy of Fallot, augmenting the small right ventricular outflow tract remains a challenge. Transannular patch augmentation revolutionised surgical management, but did so at the expense of rendering patients with pulmonary insufficiency and the resulting problems associated therewith. Recent surgical efforts have focused on pulmonary valve preservation at initial correction and pulmonary valve restoration after transannular patching, with favourable results. In this manuscript, we review methods of pulmonary valve preservation and restoration.

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Changes in 99m Technegas ventilation lung scan in a newborn with absent pulmonary valve syndrome

Cardiology in the Young ◽

10.1017/s1047951101001093 ◽

2001 ◽

Vol 11 (6) ◽

pp. 673-675

Author(s):

Kazuhiro Takahashi ◽

Takashi Kuwahara ◽

Masayoshi Nagatsu

Keyword(s):

Surgical Treatment ◽

Tetralogy Of Fallot ◽

Respiratory Symptoms ◽

Pulmonary Valve ◽

Pulmonary Arteries ◽

Absent Pulmonary Valve ◽

Lung Scan ◽

Two Stages ◽

Lung Scanning ◽

Absent Pulmonary Valve Syndrome

A newborn infant with tetralogy of Fallot and absent pulmonary valve was successfully corrected in two stages. Absent pulmonary valve syndrome presenting in early infancy manifests severe respiratory symptoms that still make challenging both management and surgical treatment. This is ascribed to tracheobronchial compression by the extremely dilated pulmonary arteries, and to the resultant pulmonary obstructive lesions. We report herein the first findings of 99m Technegas ventilation lung scanning in an infant with the syndrome to assess the pulmonary obstructive lesions.

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