scholarly journals A case of perioperative management in a patient with congenital protein C deficiency and repeating purpura fulminans since the neonatal period

2021 ◽  
Vol 67 (4) ◽  
pp. 248-253
Author(s):  
Yukari FUJIMOTO ◽  
Kosuke SAIDA ◽  
Yoshihide OKUMURA ◽  
Asa KIMURA ◽  
Aika HIRAI ◽  
...  
Keyword(s):  
Protein C ◽  
Perioperative Management ◽  
Neonatal Period ◽  
Purpura Fulminans ◽  
Protein C Deficiency ◽  
Congenital Protein C Deficiency

Purpura Fulminans in a Chinese Boy With Congenital Protein C Deficiency

PEDIATRICS ◽  
1986 ◽  
Vol 77 (5) ◽  
pp. 670-676
Author(s):  
Patrick Yuen ◽  
Alfred Cheung ◽  
Hsiang Ju Lin ◽  
Faith Ho ◽  
Jun Mimuro ◽  
...  
Keyword(s):  
Disseminated Intravascular Coagulation ◽  
Protein C ◽  
Purpura Fulminans ◽  
Fresh Frozen Plasma ◽  
Protein C Deficiency ◽  
Intravascular Coagulation ◽  
The Family ◽  
Fresh Frozen ◽  
Frozen Plasma ◽  
Congenital Protein C Deficiency

Severe and recurrent purpura fulminans developed in a Chinese boy at one day of age. Results of coagulation studies performed on the patient during attacks were compatible with the diagnosis of disseminated intravascular coagulation. Subsequent investigations have revealed that the patient is homozygous and that his parents are heterozygous for protein C deficiency. Cryoprecipitate and fresh frozen plasma induced a remission, and administration of warfarin has been successful in preventing recurrence of attacks for as long as 8 months without infusion of any plasma components. None of the family members who are heterozygous for protein C deficiency have had thrombotic episodes.

Purpura fulminans in congenital protein C deficiency successfully treated with fresh frozen plasma and thrombomodulin

2017 ◽  
Vol 45 (6) ◽  
pp. e165-e166
Author(s):  
Takuma Hayami ◽  
Akihiko Yamaguchi ◽  
Takeshi Kato ◽  
Toshihiro Tanaka ◽  
Yuka Nishizawa ◽  
...  
Keyword(s):  
Protein C ◽  
Purpura Fulminans ◽  
Fresh Frozen Plasma ◽  
Protein C Deficiency ◽  
Fresh Frozen ◽  
Frozen Plasma ◽  
Congenital Protein C Deficiency

scholarly journals Perioperative management of a patient with purpura fulminans syndrome due to protein C deficiency

2001 ◽  
Vol 48 (11) ◽  
pp. 1070-1074 ◽  
Author(s):  
Kojiro Kumagai ◽  
Kimitoshi Nishiwaki ◽  
Kosei Sato ◽  
Hanae Kitamura ◽  
Kayo Yano ◽  
...  
Keyword(s):  
Protein C ◽  
Perioperative Management ◽  
Purpura Fulminans ◽  
Protein C Deficiency

scholarly journals Neonatal purpura fulminans in newborn with severe congenital protein C deficiency: Case report

2017 ◽  
Vol 21 (2) ◽  
pp. 104-106
Author(s):  
Sultan A. Jafarri ◽  
Khalid M. AlAttas ◽  
Sultan M. Bajawi ◽  
Mohammad K. Ahsan ◽  
Ali M. Al-Sheikh ◽  
...  
Keyword(s):  
Case Report ◽  
Protein C ◽  
Purpura Fulminans ◽  
Protein C Deficiency ◽  
Congenital Protein C Deficiency

Perioperative management of severe congenital protein C deficiency

2017 ◽  
Vol 28 (8) ◽  
pp. 646-649 ◽  
Author(s):  
Kentaro Watanabe ◽  
Motohiro Kato ◽  
Tetsuya Ishimaru ◽  
Mitsuteru Hiwatari ◽  
Tomonori Suzuki ◽  
...  
Keyword(s):  
Protein C ◽  
Perioperative Management ◽  
Protein C Deficiency ◽  
Congenital Protein C Deficiency
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