Red Ear Syndrome: um relato de caso sobre uma síndrome rara associada a cefaleia

Context: The Red Ear Syndrome” (RES) is a rare condition characterized by ear hyperemia associated with burning pain. This syndrome is classified into secondary and idiopathic forms, which pathophysiological mechanisms are still unclear. Idiopathic forms occur isolated or associated with primary headaches and secondary forms are associated to cervical disorders. The aim of this study is to report a case of RES related to migraine, the new published cases make this syndrome earn more attention and investigation. Case report: A 31-year-old woman presented with acute pain, edema and marked erythema, occasionally accompanied by hyperhidrosis and local burning. These episodes occurred spontaneously or were induced by triggers. During attacks, cooling was the only means of relief. The patient reported a clear association between RES and some migraine attacks. Extensive laboratory and radiological investigation showed no abnormalities. Conclusions: RES is mainly determined by sudden or induced attacks of burning pain and redness in the ear. Attacks can last from minutes to hours in conjunction with primary headaches. The uncertainty about the etiology of this syndrome is an obstacle to treatment.

Some rare headache disorders, including Alice in Wonderland syndrome, blip syndrome, cardiac cephalalgia, epicrania fugax, exploding head syndrome, Harlequin syndrome, lacrimal neuralgia, neck–tongue syndrome, and red ear syndrome

A fascinating array of rare headache disorders—Alice in Wonderland syndrome, blip syndrome, cardiac cephalalgia, epicrania fugax, exploding head syndrome, harlequin syndrome, lacrimal headache, ictal epileptic headache, neck–tongue syndrome, and red ear syndrome—are reviewed in this chapter. Appropriate diagnosis and treatment as appropriate can be most reassuring to the patient. There are additional rare headache disorders just waiting to be described by astute clinicians.