Choroid plexus papillomas of the cerebellopontine angle in a child

Choroid plexus papillomas (CPP) are uncommon benign brain tumors that usually arise in the fourth ventricle in adults and lateral ventricles in children. Extraventricular CPPs are rare and can be found primarily in the cerebellopontine angle (CPA). We present a case of primary extraventricular CPP in the right CPA successfully resected with retrosigmoid approach. Detailed surgical techniques of retrosigmoid craniotomy and tumor dissection are presented in high definition video with narration.The video can be found here: http://youtu.be/6591en3nWlY.

Download Full-text

Not So Benign: A Rare Atypical Ectopic Choroid Plexus Papilloma

Journal of Ophthalmology and Visual Sciences ◽

10.26420/jophthalmolvissci.2021.1050 ◽

2021 ◽

Vol 6 (2) ◽

Author(s):

Patel R ◽

◽

Lukins D ◽

Villano JL ◽

Sudhakar P ◽

...

Keyword(s):

Choroid Plexus ◽

Cerebellopontine Angle ◽

Radiation Necrosis ◽

Cranial Nerves ◽

Choroid Plexus Papilloma ◽

Seer Database ◽

Unique Case ◽

Leptomeningeal Seeding ◽

Choroid Plexus Papillomas ◽

Plexus Papilloma

Choroid Plexus Papillomas (CPPs) are rare neoplasms (0.4-0.6 % of all brain tumors) arising from cuboidal epithelial cells of the choroid plexus. Atypical choroid plexus papillomas are even more rare and characterized by aggressive features of increased mitotic activity and frequent metastases even at diagnosis. Atypical choroid plexus papillomas accounted for 9% of choroid plexus tumors in the Surveillance Epidemiology and End Results (SEER) Database from 1978 to 2009. We describe a 56 year-old woman with a rare atypical choroid plexus papilloma ectopically located in the cerebellopontine angle and mistaken for a vestibular schwannoma or glossopharyngeal schwannoma. She demonstrated leptomeningeal seeding involving multiple cranial nerves and spinal cord. Besides papilledema she developed several neuro-ophthalmic features slowly over time from involvement of cranial nerves and subsequent intraparenchymal spread and radiation necrosis in the brainstem. Besides being rare, the cerebellopontine angle location of this tumor is also extremely uncommon making this a very unique case.

Download Full-text

Torticollis as a Rare Presentation of Cerebellopontine Angle Choroid Plexus Papilloma in Children

Iranian Journal of Neurosurgery ◽

10.32598/irjns.6.4.6 ◽

2020 ◽

Vol 6 (4) ◽

pp. 219-224

Author(s):

Mohammad Faraji-Rad ◽

◽

Einollah Alipour ◽

Elnaz Farajirad ◽

◽

...

Keyword(s):

Choroid Plexus ◽

Cerebellopontine Angle ◽

Choroid Plexus Papilloma ◽

Pathological Examination ◽

Rare Presentation ◽

Case Presentation ◽

Adults And Children ◽

Approach Method ◽

The Right ◽

Choroid Plexus Papillomas

Background and Importance: The rare intracranial neoplasms are Choroid Plexus Papillomas (CPPs), especially in the cerebellopontine angle. The main location of choroid plexus papillomas in adults and children are 4th ventricle and lateral ventricles, respectively. Case Presentation: We report on a little girl with a cerebellopontine angle CPP who presented with symptoms of torticollis. Assessment of Magnetic Resonance Imaging showed a mass in the right cerebellopontine angle, next to the brain stem. The tumor was completely resected using the right retrosigmoid approach method. A pathological examination determine a typical CPP that this being should be considered an extremely rare cause of a lesion in the posterior fossa. Conclusion: CPP is usually presented in the atrium of the lateral ventricle in children; however, we reported a rare case in the cerebellopontine angle.

Download Full-text