Doege-Potter syndrome due to a hepatic solitary fibrous tumour

Author(s):  
Alba Correa Bonito ◽  
Patricia Muñoz-Hernández ◽  
Ángela de la Hoz Rodríguez ◽  
Jesús Delgado Valdueza ◽  
Elena Martín Pérez
2000 ◽  
Vol 37 (2) ◽  
pp. 189-191 ◽  
Author(s):  
G Magro ◽  
A Sidoni ◽  
M Bisceglia

2021 ◽  
pp. 1-4
Author(s):  
Jan Roman ◽  
Petr Vávra ◽  
Michaela Vávrová ◽  
Vladimír Židlík ◽  
Anton Pelikán

2019 ◽  
Vol 26 ◽  
pp. 100974
Author(s):  
Félix Couture ◽  
Benjamin Legault ◽  
Nadia Ekindi ◽  
Maxime Noel-Lamy ◽  
Michel Pavic ◽  
...  

2008 ◽  
Vol 20 (3) ◽  
pp. 160-163 ◽  
Author(s):  
Tsukasa Tsuji ◽  
Hideaki Kitada ◽  
Shinnosuke Abe ◽  
Hitoshi Ikeda

2005 ◽  
Vol 110 (3) ◽  
pp. 312-314 ◽  
Author(s):  
David Scheie ◽  
Finn P. Reinholt ◽  
Haldor Slettebø ◽  
Kari Skullerud

2014 ◽  
Vol 49 (5) ◽  
pp. e108-e110 ◽  
Author(s):  
Maher Kurdi ◽  
Larry Allen ◽  
Bret Wehrli ◽  
Subrata Chakrabarti

2021 ◽  
Vol 49 (3) ◽  
pp. 030006052199694
Author(s):  
Zhi-Ke Li ◽  
Jie Liu ◽  
Chen Chen ◽  
Ke-Yi Yang ◽  
Yao-Tiao Deng ◽  
...  

Preoperative diagnosis of solitary fibrous tumour (SFT) may not provide a complete tumour picture and may be inaccurate. There is no standard treatment for locally advanced or metastasised malignant SFT (MSFT). Here, the case of a 17-year-old male patient with final pathology diagnosis of MSFT is reported. Preoperative biopsy pathology results suggested an Ewing sarcoma that was positive for CD99 antigen, vimentin, friend leukaemia integration 1 transcription factor, apoptosis regulator Bcl-2, and synaptophysin; and negative for CD34 antigen, S-100 protein (S-100), smooth muscle antigen, cytokeratin, and Wilms tumour 1 associated protein. The Ki67 positive rate was 8%, so the patient initially received eight cycles of conversion chemotherapy (vincristine, etoposide, ifosfamide and pirarubicin for one cycle, and vincristine, doxorubicin, and cyclophosphamide/ifosfamide and etoposide for 7 cycles in total). The tumour shrunk significantly and was surgically removed. The final pathology diagnosis was MSFT that was positive for CD99 and signal transducer and activator of transcription 6, and negative for CD34, tumour protein 63, S-100, desmin, and epithelial membrane antigen. Fluorescence in situ hybridization showed no gene translocation in EWS RNA binding protein 1, SS18 subunit of BAF chromatin remodelling complex or FUS RNA binding protein. The patient finally accepted adjuvant radiotherapy of 5600 cGy. Disease-free survival has been > 1 year, with no recurrence or metastasis detected to date. MSFT is rare and treatment for locally advanced or metastatic MSFT remains controversial. The efficacy of the present therapeutic strategy requires further research.


2021 ◽  
Vol 14 (10) ◽  
pp. e244603
Author(s):  
Swaminathan Perinkulam Sathyanarayanan ◽  
Khizar Hamid ◽  
Kayla Hoerschgen ◽  
Tony Oliver

Solitary fibrous tumours (SFTs) are rare mesenchymal tumours that are mostly seen in the pleura. Lately, they have also been described in other locations. Recent discovery of the NAB2-STAT6 fusion gene which is specific for SFTs has led to an accurate diagnosis of SFTs. The occurrence of SFTs in the mesentery is very rarely reported in the literature. We report a case of a 63-year-old female who presented with abdominal pain, rectal bleeding and Fusobacterium bacteraemia, who was ultimately found to have a mesenteric SFT.


2010 ◽  
Vol 2010 ◽  
pp. 1-4 ◽  
Author(s):  
Maria Archontaki ◽  
Dimitris P. Korkolis ◽  
Niki Arnogiannaki ◽  
Stelios Hatzijiannis ◽  
Panagiotis Dendrinos ◽  
...  

Solitary fibrous tumour (SFT) is a rare oncological entity that most often arises in the pleura. Over the past 10 years, the tumour has been described at numerous extrapleural locations. We present the case of a 42-year-old female Caucasian patient with an extrapleural SFT located at the anterior thoracic wall for 22 years, with atypical histological characteristics and clinical features of malignancy. Management consisted of a wide surgical resection, plastic reconstruction, and postoperative radiotherapy. Although extrapleural SFT usually behaves as a benign soft tissue tumour, it can also present with a more aggressive local behavior, including locoregional recurrence or metastasis. In that case, a multidisciplinary approach is required for accurate diagnosis and proper management.


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