HYPOPLASTIC LEFT HEART SYNDROME IS NOT A PREDICTOR OF OUTCOMES FOLLOWING THE FONTAN OPERATION: A COHORT STUDY

2016 ◽  
Vol 32 (10) ◽  
pp. S185-S186
Author(s):  
B. Martin ◽  
M. Al Aklabi ◽  
I.M. Rebeyka ◽  
D.B. Ross
Keyword(s):  
Cohort Study ◽  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

scholarly journals BLUNTED EXERCISE PRESSOR REFLEX IN CHILDREN WITH HYPOPLASTIC LEFT HEART SYNDROME AFTER THE FONTAN OPERATION

2017 ◽  
Vol 33 (10) ◽  
pp. S97
Author(s):  
S. Fusnik ◽  
T. Bradley ◽  
A. Kakadekar ◽  
S. Pharis ◽  
C. Pockett ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Exercise Pressor Reflex ◽  
Pressor Reflex ◽  
Left Heart Syndrome

scholarly journals Changing Epidemiology of Hypoplastic Left Heart Syndrome: Results of a National Swedish Cohort Study

2019 ◽  
Vol 8 (2) ◽  
Author(s):  
Annika Öhman ◽  
Milad El‐Segaier ◽  
Gunnar Bergman ◽  
Katarina Hanséus ◽  
Torsten Malm ◽  
...  
Keyword(s):  
Cohort Study ◽  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome ◽  
Swedish Cohort

scholarly journals Geometry of the pulmonary arteries before the Fontan operation: can we influence it during the Norwood procedure?

2020 ◽  
Vol 57 (6) ◽  
pp. 1098-1104
Author(s):  
Katarzyna Januszewska ◽  
Pawel Nawrocki ◽  
Anja Lehner ◽  
Julia Stegger ◽  
Felix Kleinerueschkamp ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Pulmonary Arteries ◽  
Norwood Procedure ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Second Stage ◽  
The Right ◽  
Left Heart Syndrome ◽  
The Impact

Abstract OBJECTIVES The right ventricle-to-pulmonary artery (RV-PA) shunt provides stable haemodynamics after the Norwood procedure but can influence development of the central pulmonary arteries (PAs). The goal of this study was to analyse the geometry of the central PAs in children with hypoplastic left heart syndrome before the Fontan operation with respect to the RV-PA shunt site and the type of the second-stage operation. METHODS A total of 161 children with hypoplastic left heart syndrome, median age 2.7 (range 1.3–9.8) years and median weight 12.7 (range 7.6–26.1) kg, underwent the Fontan operation after having had the Norwood procedure with an RV-PA shunt. The patients were divided into 2 groups: left-sided RV-PA (L-RV-PA) (n = 129) with the shunt on the left and right-sided RV-PA (n = 32) with the shunt on the right side of the neoaorta. Angiographic data obtained before the Fontan and all cardiac catheterization interventions were analysed retrospectively. RESULTS Between the second and third stages, as well as directly before the Fontan operation, the L-RV-PA group required more PA catheter interventions (P = 0.001 and P = 0.03). In this group, the minimal left PA diameter was smaller than that in the R-RV-PA group (P = 0.021). Leaving the shunt open until the Fontan operation increased the rate of PA interventions in the L-RV-PA group (P = 0.001), but there is no evidence of the impact on the development of the left PAs (P = 0.075). There is also no evidence that the type of the second-stage procedure influences the intervention rate before the Fontan procedure (P = 0.14). CONCLUSIONS Children who have the L-RV-PA shunt require more PA catheter interventions. The right-sided RV-PA shunt and the subsequent Glenn anastomosis in the place of the shunt are associated with distortion-free and more symmetrical development of the central PAs.

scholarly journals Fontan operation for hypoplastic left heart syndrome with absent aortic valve

2004 ◽  
Vol 128 (2) ◽  
pp. 315-316 ◽  
Author(s):  
Narutoshi Hibino ◽  
Yorikazu Harada ◽  
Takeshi Hiramatsu ◽  
Satoshi Yasukochi ◽  
Gengi Satomi
Keyword(s):  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Absent Aortic Valve ◽  
Left Heart Syndrome

scholarly journals Tricuspid annular plane systolic excursion correlates with exercise capacity in a cohort of patients with hypoplastic left heart syndrome after Fontan operation

2016 ◽  
Vol 33 (12) ◽  
pp. 1897-1902 ◽  
Author(s):  
David J. Goldberg ◽  
Benjamin French ◽  
Anita L. Szwast ◽  
Michael G. McBride ◽  
Stephen M. Paridon ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Exercise Capacity ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Right Ventricle and Tricuspid Valve Function at Midterm After the Fontan Operation for Hypoplastic Left Heart Syndrome: Impact of Shunt Type

2010 ◽  
Vol 32 (2) ◽  
pp. 160-166 ◽  
Author(s):  
Victor Bautista-Hernandez ◽  
Mark Scheurer ◽  
Ravi Thiagarajan ◽  
Joshua Salvin ◽  
Frank A. Pigula ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Hypoplastic Left Heart Syndrome ◽  
Tricuspid Valve ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Valve Function ◽  
Left Heart Syndrome

scholarly journals Primary Norwood Operation Strategy for Hypoplastic Left Heart Syndrome and its Mid-term Outcome up to the Fontan Operation

2017 ◽  
Vol 33 (3) ◽  
pp. 197-201
Author(s):  
Hidenori Hayashi ◽  
Koichi Sughimoto ◽  
Yuta Tsuchida ◽  
Tsuyoshi Yoshii ◽  
Shin Kondo ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Operation Strategy ◽  
Left Heart ◽  
Norwood Operation ◽  
Hypoplastic Left Heart ◽  
Term Outcome ◽  
Left Heart Syndrome

Neurodevelopmental outcome of patients after the Fontan operation: A comparison between children with hypoplastic left heart syndrome and other functional single ventricle lesions

2000 ◽  
Vol 137 (5) ◽  
pp. 646-652 ◽  
Author(s):  
Caren S. Goldberg ◽  
Edward M. Schwartz ◽  
James A. Brunberg ◽  
Ralph S. Mosca ◽  
Edward L. Bove ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Single Ventricle ◽  
Fontan Operation ◽  
Neurodevelopmental Outcome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Echocardiography of hypoplastic left heart syndrome

2011 ◽  
Vol 21 (S2) ◽  
pp. 28-37 ◽  
Author(s):  
Thieu Nguyen ◽  
Michelle Miller ◽  
Javier Gonzalez ◽  
Katherine Nardell ◽  
James Galas ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Cardiac Monitoring ◽  
Left Heart ◽  
Norwood Operation ◽  
Hypoplastic Left Heart ◽  
Cavopulmonary Anastomosis ◽  
Operation Stage ◽  
Before And After ◽  
Left Heart Syndrome

AbstractEchocardiography is critical in the assessment of patients with hypoplastic left heart syndrome. Fundamental techniques and standardised approaches are useful when evaluating patients with hypoplastic left heart syndrome prenatally, after birth, and before the Norwood operation (Stage 1); after the Norwood operation, before and after the superior cavopulmonary anastomosis (Stage 2); before and after the Fontan operation (Stage 3); and for chronic surveillance after the Fontan operation. From foetal assessment to ongoing surveillance after the Fontan procedure, echocardiography remains the primary technique for cardiac monitoring in this growing population of children and adults.

A 10-year single-centre experience in percutaneous interventions for multi-stage treatment of hypoplastic left heart syndrome

2013 ◽  
Vol 24 (1) ◽  
pp. 54-63 ◽  
Author(s):  
Tomasz Moszura ◽  
Pawel Dryzek ◽  
Sebastian Goreczny ◽  
Anna Mazurek-Kula ◽  
Jacek J. Moll ◽  
...  
Keyword(s):  
Surgical Treatment ◽  
Pulmonary Artery ◽  
Hypoplastic Left Heart Syndrome ◽  
Stent Implantation ◽  
Fontan Operation ◽  
Pulmonary Arteries ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Percutaneous Interventions ◽  
Left Heart Syndrome

AbstractObjectivesThe purpose of this paper is to report our 10 years of experience of interventional treatment of patients with hypoplastic left heart syndrome and to focus on the frequency, type, and results of percutaneous interventions during all the stages of palliation, considering the different techniques, devices, and complications.BackgroundConstant progress in surgical treatment of congenital heart defects in the last decade has significantly improved the prognosis for children with hypoplastic left heart syndrome. However, morbidity and mortality remain relatively high. Modern interventional procedures complement or occasionally replace surgical treatment.MethodsBetween January, 2001 and December, 2010, 161 percutaneous interventions were performed in 88 patients with hypoplastic left heart syndrome. Patients were divided into four groups: (a) before the first surgical treatment including hybrid approach, (b) after first-stage Norwood operation, (c) after second-stage bidirectional Glenn operation, and (d) after third-stage Fontan operation.ResultsPercutaneous interventions resulted in statistically significant changes in pulmonary artery pressures, vessel diameters, and O2saturation. Complications occurred in 4.3% of interventions and were related mainly to stent implantation in stenosed pulmonary arteries.ConclusionsPercutaneous interventions may result in haemodynamic stability and reduction in the number of operations. They may result in significant changes in pulmonary artery pressures, vessel diameters, O2saturation, with a low rate of complications, which are mainly related to stent implantation in the pulmonary arteries.

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