Pneumothorax associated with long-term non-invasive positive pressure ventilation in Duchenne muscular dystrophy

2004 ◽  
Vol 14 (6) ◽  
pp. 353-355 ◽  
Author(s):  
Andrea Vianello ◽  
Giovanna Arcaro ◽  
Federico Gallan ◽  
Carlo Ori ◽  
Matteo Bevilacqua
Keyword(s):  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Positive Pressure Ventilation ◽  
Positive Pressure ◽  
Non Invasive

Left ventricular dysfunction in Duchenne muscular dystrophy

2020 ◽  
Vol 30 (2) ◽  
pp. 171-176
Author(s):  
Katherine A. James ◽  
Jane Gralla ◽  
Leslie A. Ridall ◽  
ThuyQuynh N. Do ◽  
Angela S. Czaja ◽  
...  
Keyword(s):  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Ejection Fraction ◽  
Left Ventricular Dysfunction ◽  
Positive Pressure Ventilation ◽  
Ventricular Dysfunction ◽  
Left Ventricular ◽  
Positive Pressure ◽  
Left Ventricle Function ◽  
Non Invasive

AbstractBackground:Duchenne muscular dystrophy is associated with progressive cardiorespiratory failure, including left ventricular dysfunction.Methods and Results:Males with probable or definite diagnosis of Duchenne muscular dystrophy, diagnosed between 1 January, 1982 and 31 December, 2011, were identified from the Muscular Dystrophy Surveillance Tracking and Research Network database. Two non-mutually exclusive groups were created: patients with ≥2 echocardiograms and non-invasive positive pressure ventilation-compliant patients with ≥1 recorded ejection fraction. Quantitative left ventricular dysfunction was defined as an ejection fraction <55%. Qualitative dysfunction was defined as mild, moderate, or severe. Progression of quantitative left ventricular dysfunction was modelled as a continuous time-varying outcome. Change in qualitative left ventricle function was assessed by the percentage of patients within each category at each age. Forty-one percent (n = 403) had ≥2 ejection fractions containing 998 qualitative assessments with a mean age at first echo of 10.8 ± 4.6 years, with an average first ejection fraction of 63.1 ± 12.6%. Mean age at first echo with an ejection fraction <55 was 15.2 ± 3.9 years. Thirty-five percent (140/403) were non-invasive positive pressure ventilation-compliant and had ejection fraction information. The estimated rate of decline in ejection fraction from first ejection fraction was 1.6% per year and initiation of non-invasive positive pressure ventilation did not change this rate.Conclusions:In our cohort, we observed that left ventricle function in patients with Duchenne muscular dystrophy declined over time, independent of non-invasive positive pressure ventilation use. Future studies are needed to examine the impact of respiratory support on cardiac function.

Acute colonic distension in a patient with severe muscular dystrophy receiving non-invasive positive pressure ventilation

2018 ◽  
Vol 28 (1) ◽  
pp. 60-61 ◽  
Author(s):  
Andrea Vianello ◽  
Giovanna Arcaro ◽  
Piera Peditto ◽  
Silvia Iovino ◽  
Rosario Marchese-Ragona
Keyword(s):  
Muscular Dystrophy ◽  
Positive Pressure Ventilation ◽  
Positive Pressure ◽  
Non Invasive ◽  
Colonic Distension

Long-term Nasal Intermittent Positive Pressure Ventilation in Advanced Duchenne's Muscular Dystrophy

CHEST Journal ◽  
1994 ◽  
Vol 105 (2) ◽  
pp. 445-448 ◽  
Author(s):  
Andrea Vianello ◽  
Matteo Bevilacqua ◽  
Vittorino Salvador ◽  
Claudio Cardaioli ◽  
Ezio Vincenti
Keyword(s):  
Muscular Dystrophy ◽  
Positive Pressure Ventilation ◽  
Intermittent Positive Pressure Ventilation ◽  
Positive Pressure ◽  
Duchenne's Muscular Dystrophy

scholarly journals Effect of long term intermittent nocturnal non-invasive positive pressure ventilation on patient with severe kyphoscoliosis and hypoxaemia

2009 ◽  
Vol 2009 (mar02 1) ◽  
pp. bcr0820080737-bcr0820080737
Author(s):  
S.-W. Huang ◽  
C.-L. Wu ◽  
C.-C. Lin ◽  
C.-L. Hung ◽  
L.-K. Kuo ◽  
...  
Keyword(s):  
Positive Pressure Ventilation ◽  
Positive Pressure ◽  
Non Invasive
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