scholarly journals Cardiac and pleuropulmonary involvement in Erdheim-Chester disease without bone lesions: A case report

2022 ◽  
Vol 17 (3) ◽  
pp. 525-530
Author(s):  
Rene Epunza Kanza ◽  
Olivier Houle ◽  
Pierre-Luc Simard ◽  
Jonathan St-Gelais ◽  
Catherine Raymond
Keyword(s):  
Case Report ◽  
Bone Lesions ◽  
Erdheim Chester Disease ◽  
Erdheim Chester ◽  
Chester Disease

Erdheim-Chester disease: a case report with pulmonary, kidney involvement and bone lesions

2009 ◽  
Vol 30 (5) ◽  
pp. 651-654 ◽  
Author(s):  
Aziza Mounach ◽  
Abderrzak Nouijai ◽  
Lahsen Achemlal ◽  
Abdellah El Maghraoui ◽  
Ahmed Bezza
Keyword(s):  
Case Report ◽  
Bone Lesions ◽  
Erdheim Chester Disease ◽  
Kidney Involvement ◽  
Erdheim Chester ◽  
Chester Disease

scholarly journals Erdheim chester disease: A case report and review of the literature

2020 ◽  
Vol 7 (1) ◽  
pp. 22
Author(s):  
Rémie Philippe Elia ◽  
ATALLAH Adnan ◽  
AKIKI Béatrice ◽  
WAKED Hani ◽  
ZEIDAN Marwan ◽  
...  
Keyword(s):  
Case Report ◽  
Braf V600e ◽  
Bone Lesions ◽  
Review Of The Literature ◽  
Rare Form ◽  
Immune Profile ◽  
Systemic Involvement ◽  
Erdheim Chester Disease ◽  
Erdheim Chester ◽  
Chester Disease

Erdheim Chester disease is a rare form of non-Langerhans histiocytosis with frequent BRAF V600E mutations. It is mainly characterized by multifocal osteosclerotic bone lesions with or without systemic involvement. The histologic image is consistent with a histiocytic proliferation of foamy cells in a polymorphic background. The main difference from the Langerhans histiocytosis is the immune profile with mainly S100, CD1a, and langerin negative. The overall prognosis is dependent on extraskeletal involvement. Herein, we present a typical presentation of Erdheim Chester disease with a review of the literature.

scholarly journals Rare Form of Erdheim-Chester Disease Presenting with Isolated Central Skeletal Lesions Treated with a Combination of Alfa-Interferon and Zoledronic Acid

2015 ◽  
Vol 2015 ◽  
pp. 1-4 ◽  
Author(s):  
E. N. Bulycheva ◽  
V. V. Baykov ◽  
M. I. Zaraĭskiĭ ◽  
G. N. Salogub
Keyword(s):  
Case Report ◽  
Zoledronic Acid ◽  
Clinical Symptoms ◽  
Young Male ◽  
Axial Skeleton ◽  
Bone Lesions ◽  
Rare Form ◽  
Erdheim Chester Disease ◽  
Erdheim Chester ◽  
Chester Disease

Erdheim-Chester disease (ECD) represents a clonal non-Langerhans histiocytosis, which manifests under an extensive variety of clinical symptoms. This creates a challenge for the physician, who is required to recognize and diagnose the disease in the early stages. Despite this considerable challenge, in the last decade there has been a dramatic increase in ECD diagnoses, in most part due to an increasing awareness of this rare disorder. Involvement of the axial skeleton is exclusively uncommon with no official recommendations for the treatment of the bone lesions. Here, we present a case report of a young male patient with isolated lesions of the spine, ribs, and pelvis, who was successfully treated with a combination therapy of alfa-interferon and zoledronic acid.

Case report of Erdheim-Chester disease in a female cardiac surgery patient

2011 ◽  
Vol 59 (S 01) ◽  
Author(s):  
HR Mahoozi ◽  
A Zittermann ◽  
K Hakim-Meibodi ◽  
J Gummert ◽  
N Mirow
Keyword(s):  
Cardiac Surgery ◽  
Case Report ◽  
Cardiac Surgery Patient ◽  
Erdheim Chester Disease ◽  
Surgery Patient ◽  
Erdheim Chester ◽  
Chester Disease

Erdheim-Chester disease with orbital involvement: Case report and ophthalmic literature review

Orbit ◽  
2016 ◽  
Vol 35 (4) ◽  
pp. 221-226 ◽  
Author(s):  
Helen Merritt ◽  
Margaret L. Pfeiffer ◽  
Karina Richani ◽  
Margaret E. Phillips
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Orbital Involvement ◽  
Erdheim Chester Disease ◽  
Erdheim Chester ◽  
Chester Disease

scholarly journals Erdheim–Chester Disease and Acute Myeloid Leukemia with Mutated NPM1 in a Patient with Clonal Hematopoiesis: A Case Report

2020 ◽  
Vol Volume 13 ◽  
pp. 11689-11695
Author(s):  
Sotirios G Papageorgiou ◽  
Aspasia Divane ◽  
Maria Roumelioti ◽  
Christine Kottaridi ◽  
Anthi Bouchla ◽  
...  
Keyword(s):  
Acute Myeloid Leukemia ◽  
Case Report ◽  
Myeloid Leukemia ◽  
Clonal Hematopoiesis ◽  
Erdheim Chester Disease ◽  
Erdheim Chester ◽  
Chester Disease ◽  
Acute Myeloid

scholarly journals Erdheim-Chester disease with intracranial involvement causing hydrocephalus: Case report

2020 ◽  
Vol 21 ◽  
pp. 100722
Author(s):  
Lívio Pereira de Macêdo ◽  
Ulyscélio Santos Moraes Ferreira ◽  
Yally Dayanne Oliveira Ferreira ◽  
Eduardo Vieira de Carvalho Júnior ◽  
Igor Vilela Faquini ◽  
...  
Keyword(s):  
Case Report ◽  
Erdheim Chester Disease ◽  
Intracranial Involvement ◽  
Erdheim Chester ◽  
Chester Disease

scholarly journals Erdheim-Chester disease: a case report

1999 ◽  
Vol 14 (3) ◽  
pp. 323 ◽  
Author(s):  
Yong Koo Park ◽  
Kyung Nam Ryu ◽  
Bang Huh ◽  
Jae Do Kim
Keyword(s):  
Case Report ◽  
Erdheim Chester Disease ◽  
Erdheim Chester ◽  
Chester Disease
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