A case of rapidly progressive Rosai-Dorfman disease restricted to the central nervous system

2006 ◽  
Vol 52 (1) ◽  
pp. 73
Author(s):  
U. Gies ◽  
D. Gruia ◽  
H. Lassmann ◽  
M. Bergmann
2015 ◽  
Vol 157 (9) ◽  
pp. 1565-1571 ◽  
Author(s):  
Yongji Tian ◽  
Junmei Wang ◽  
Mingtao Li ◽  
Song Lin ◽  
Guihuai Wang ◽  
...  

2006 ◽  
Vol 104 (5) ◽  
pp. 840-844 ◽  
Author(s):  
Christopher M. McPherson ◽  
Justin Brown ◽  
Angela W. Kim ◽  
Franco Demonte

✓ Rosai–Dorfman disease (RDD) is an idiopathic histioproliferative disorder usually presenting with massive, painless lymphadenopathy. Extranodal involvement has been reported including at least 50 cases affecting the central nervous system (CNS). The treatment of CNS RDD as reported in the literature has primarily involved a surgical technique. The authors report on the case of a 53-year-old man presenting with multiple skull base lesions mimicking meningiomas. The patient suffered visual deterioration and underwent a right orbitopterional craniotomy as well as optic nerve decompression. Histopathological analysis revealed histiocytic cells and emperipolesis consistent with RDD. Following surgery, corticosteroid agents were administered, leading to marked resolution of both the remaining surgically untreated lesions and the balance of the patient's symptoms. This report represents the first case of the resolution of intracranial RDD following corticosteroid therapy. Corticosteroid agents should be considered an effective option in the treatment of CNS RDD.


2011 ◽  
Vol 121 (S4) ◽  
pp. S234-S234 ◽  
Author(s):  
Grace G. Kim ◽  
Marc E. Friedel ◽  
Jean Anderson Eloy ◽  
Robert W. Jyung ◽  
James K. Liu

Medicine ◽  
2014 ◽  
Vol 93 (3) ◽  
pp. 165-175 ◽  
Author(s):  
Jose D. Sandoval-Sus ◽  
Ana C. Sandoval-Leon ◽  
Jennifer R. Chapman ◽  
Jose Velazquez-Vega ◽  
Maria J. Borja ◽  
...  

Neurology ◽  
2021 ◽  
pp. 10.1212/WNL.0000000000012035
Author(s):  
Kia Gilani ◽  
Stephanie Kuntz ◽  
David G. Munoz ◽  
Raphael Schneider

Medicine ◽  
2019 ◽  
Vol 98 (19) ◽  
pp. e15365 ◽  
Author(s):  
Jia-Hua Wen ◽  
Chao Wang ◽  
Yun-Yun Jin ◽  
Duo Xu ◽  
Biao Jiang ◽  
...  

2012 ◽  
Vol 46 (1) ◽  
pp. 54-56 ◽  
Author(s):  
Aida Antuña Ramos ◽  
Marco Antonio Alvarez Vega ◽  
Juan Vicente Darriba Alles ◽  
María Jesús Antuña Garcia ◽  
Angela Meilán Martínez

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