1870 Prognostic value of aortic elasticity on aortic complications in patients with Marfan syndrome

2003 ◽  
Vol 24 (5) ◽  
pp. 358
Author(s):  
G NOLLEN
2016 ◽  
Vol 80 (11) ◽  
pp. 2369-2375 ◽  
Author(s):  
Yohei Akazawa ◽  
Noriko Motoki ◽  
Akira Tada ◽  
Shoko Yamazaki ◽  
Akira Hachiya ◽  
...  

2003 ◽  
Vol 91 (5) ◽  
pp. 637-640 ◽  
Author(s):  
Gijs J. Nollen ◽  
Lilian J. Meijboom ◽  
Maarten Groenink ◽  
Janneke Timmermans ◽  
Jelle O. Barentsz ◽  
...  

Heart ◽  
1998 ◽  
Vol 80 (2) ◽  
pp. 163-169 ◽  
Author(s):  
M Groenink ◽  
L Rozendaal ◽  
M S J Naeff ◽  
R C M Hennekam ◽  
A A M Hart ◽  
...  

2018 ◽  
Vol 24 (C) ◽  
pp. 68
Author(s):  
Andrea Guala ◽  
Jose Rodríguez-Palomares ◽  
Aroa Ruiz-Muñoz ◽  
Minerva Gandara ◽  
Violeta Sanchez ◽  
...  

Author(s):  
Douglas R. Keene ◽  
Magaret Fairhurst ◽  
Catherine C. Ridgway ◽  
Lynn Y. Sakai

Matrix microfibrils are present in the connective tissue matrices of all tissues. Following standard TEM processing, they appear in cross section as cylindrical fibrils 8-10 nm in diameter, often associated with amorphous elastin. They are also seen in the absence of amorphous elastin, for example in the shallow papillary layer of skin, and also in cartilage matrix (Figure 1). Negative stain and rotary shadowing studies suggest that microfibrils are composed of laterally associated globular structures connected by fine filamentous strands (“ beaded strings”), and that they are extendable. Immunoelectron microscopy has demonstrated that fibrillin, a 350 Kd glycoprotein, is distributed along all microfibrils with a relaxed periodicity of about 54 nm The gene coding for fibrillin has recently been identified and is defective in the Marfan syndrome.


2001 ◽  
Vol 120 (5) ◽  
pp. A298-A299
Author(s):  
A SAFATLERIBEIRO ◽  
U RIBEIRO ◽  
C KOBATA ◽  
C CORBETT ◽  
K IRIYA ◽  
...  

2007 ◽  
Vol 177 (4S) ◽  
pp. 360-360
Author(s):  
Ana Agud ◽  
Maria J. Ribal ◽  
Lourdes Mengual ◽  
Mercedes Marin-Aguilera ◽  
Laura Izquierdo ◽  
...  

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