YOUNG LADY WITH SYNCOPE- ATRIAL SEPTAL DEFECT MASQUERADING AS ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY

We report on a case of a large ostium secundum atrial septal defect (ASD) that was initially diagnosed as arrhythmogenic right ventricular cardiomyopathy (ARVC). We discuss the initial work up, diagnosis, and treatment of this patient’s ASD and explore how the pathophysiology of ARVC may mimic congenital heart disease where there is a large left-to-right shunt.

Download Full-text

A case of desmoplakin mutation and delayed arrhythmogenic right ventricular cardiomyopathy/dysplasia after atrial septal defect closure

Journal of Cardiology Cases ◽

10.1016/j.jccase.2018.09.005 ◽

2019 ◽

Vol 19 (4) ◽

pp. 111-114

Author(s):

Ayano Yoshida ◽

Atsushi Suzuki ◽

Erisa Kawada ◽

Takashige Tobita ◽

Naoki Serizawa ◽

...

Keyword(s):

Right Ventricular ◽

Atrial Septal Defect ◽

Septal Defect ◽

Arrhythmogenic Right Ventricular Cardiomyopathy ◽

Defect Closure ◽

Ventricular Cardiomyopathy ◽

Atrial Septal Defect Closure

Download Full-text

Right-to-left Shunt via Iatrogenic Atrial Septal Defect Requiring Emergency Surgical Repair following Cryoballoon Atrial Fibrillation Ablation in a Patient with Arrhythmogenic Right Ventricular Cardiomyopathy

10.22541/au.164101955.51237215/v1 ◽

2022 ◽

Author(s):

Ryohsuke Narui ◽

Seigo Yamashita ◽

Michio Yoshitake ◽

Tomohisa Nagoshi ◽

Takashi Kunihara ◽

...

Keyword(s):

Atrial Fibrillation ◽

Right Ventricular ◽

Atrial Septal Defect ◽

Septal Defect ◽

Arrhythmogenic Right Ventricular Cardiomyopathy ◽

Balloon Catheter ◽

Atrial Fibrillation Ablation ◽

Transseptal Puncture ◽

Ventricular Cardiomyopathy ◽

Iatrogenic Atrial Septal Defect

An 81-year-old woman with arrhythmogenic right ventricular cardiomyopathy underwent catheter ablation for atrial fibrillation and atrial flutter. Hypoxemia refractory to the administration of oxygen was seen after transseptal puncture. Transthoracic echocardiography revealed right to left shunt via an iatrogenic atrial septal defect (IASD) that was increased by tricuspid regurgitation flow. Her hypoxemia improved after IASD occlusion with the inflation of a venogram balloon catheter. Emergent surgical IASD closure was successfully performed. IASD after transseptal puncture for atrial fibrillation ablation infrequently causes severe complications that require emergent repair.

Download Full-text

Transcatheter closure of atrial septal defect associated with arrhythmogenic right ventricular cardiomyopathy: a case report and literature review

Cardiology in the Young ◽

10.1017/s1047951114001553 ◽

2014 ◽

Vol 25 (3) ◽

pp. 403-407

Author(s):

Haiyan Wang ◽

Hongyu Ding ◽

Lei Lei ◽

Xiaohong Zhang ◽

Yuling Gong ◽

...

Keyword(s):

Right Ventricular ◽

Atrial Septal Defect ◽

Ventricular Arrhythmias ◽

Septal Defect ◽

Medical Literature ◽

Transcatheter Closure ◽

Arrhythmogenic Right Ventricular Cardiomyopathy ◽

Interventional Treatment ◽

Ventricular Cardiomyopathy

AbstractArrhythmogenic right ventricular cardiomyopathy is characterised by progressive, fibrofatty replacement of myocardium, and ventricular arrhythmias, and its prognosis is usually poor. Arrhythmogenic right ventricular cardiomyopathy associated with atrial septal defect is very rare, and this combination may make the diagnosis, treatment, and prognosis difficult. We present a case of a patient with this association who underwent interventional treatment with a septal defect occluder. Transcatheter closure of atrial septal defect in a patient with arrhythmogenic right ventricular cardiomyopathy is hitherto unreported. During a 3-year follow-up he remained relatively stable. We also review the cases reported in the medical literature describing this uncommon association between arrhythmogenic right ventricular cardiomyopathy and atrial septal defect or patent foramen ovale.

Download Full-text