Side selection for cochlear implantation in a case of Cogan's syndrome

2007 ◽  
Vol 122 (3) ◽  
pp. 310-313 ◽  
Author(s):  
G J Im ◽  
H H Jung
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Steroid Treatment ◽  
Radiological Findings ◽  
Cogan’S Syndrome ◽  
Cogan's Syndrome ◽  
Interstitial Keratitis ◽  
Selection For ◽  
Bilateral Deafness ◽  
Selection Of

AbstractCogan's syndrome is a rare clinical entity that is characterised by non-syphilitic interstitial keratitis and audiovestibular symptoms. The cause of Cogan's syndrome is considered to be autoimmune disease, which is supported by the resolution of hearing loss after steroid treatment, and the association with other autoimmune diseases. The sensorineural hearing loss of Cogan's syndrome is progressive over a few months, and sudden, bilateral deafness often occurs, which may be an indication for cochlear implantation. This paper presents the case of a young woman suffering from Cogan's syndrome and sudden, bilateral deafness. With reference to this case, we describe problems regarding cochlear implantation for Cogan's syndrome and radiological findings aiding selection of cochlear implantation side.

scholarly journals Interstitial Keratitis, Vertigo, and Vasculitis: Typical Cogan’s Syndrome

2014 ◽  
Vol 2014 ◽  
pp. 1-4 ◽  
Author(s):  
Ahad Azami ◽  
Nasrollah Maleki ◽  
Mohammadreza Kalantar Hormozi ◽  
Zahra Tavosi
Keyword(s):  
Hearing Loss ◽  
Systemic Vasculitis ◽  
Unknown Etiology ◽  
Inflammatory Disorder ◽  
Conjunctival Hyperemia ◽  
Cogan’S Syndrome ◽  
Auditory Brain Stem Response ◽  
Chronic Inflammatory Disorder ◽  
Cogan's Syndrome ◽  
Interstitial Keratitis

Cogan’s syndrome (CS) is a chronic inflammatory disorder of unknown etiology that most commonly affects young adults. Clinical hallmarks are bilateral interstitial keratitis and vestibuloauditory dysfunction. Association between CS and systemic vasculitis as well as aortitis also exists. The diagnosis of CS is based upon presence of characteristic inflammatory eye disease and vestibuloauditory dysfunction. We describe classic Cogan’s syndrome in a 47-year-old female from Ardabil. The patient was admitted with headache, vertigo, nausea, vomiting, right leg claudication, musculoskeletal pains, bilateral hearing loss, and blindness for the past two months. Ophthalmologic examination revealed that visual acuity was 0.1 bilaterally. Conjunctival hyperemia, bilateral cataract, and interstitial keratitis were detected with a slit lamp examination. Pure tone audiogram (PTA) and auditory brain stem response (ABR) showed bilateral sensorineural hearing loss. The other differential diagnosis of CS was studied and ruled out. Pulse i.v. methylprednisolone and cyclophosphamide were given and were followed by oral prednisolone and cyclophosphamide. Clinical follow-up showed partial improvement.

scholarly journals Atypical Cogan's Syndrome

2013 ◽  
Vol 2013 ◽  
pp. 1-4
Author(s):  
João Queirós ◽  
Sofia Maia ◽  
Mariana Seca ◽  
António Friande ◽  
Maria Araújo ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Treatment Strategies ◽  
Rare Clinical Entity ◽  
Cogan’S Syndrome ◽  
Peripheral Facial Palsy ◽  
Systemic Corticosteroids ◽  
Cogan's Syndrome ◽  
Biological Tests ◽  
Appropriate Therapy ◽  
Bilateral Deafness

Background. Cogan’s syndrome is a rare clinical entity whose etiopathology is still unknown, and the treatment strategies are not clearly defined.Case. A 23-year-old male presented with symptoms of headache, peripheral facial palsy, persistent right hearing loss and bilateral papillitis. Workup excluded all infectious, granulomatous, neoplastic, and immune causes. The diagnosis of atypical Cogan’s syndrome was established, and the patient was treated with systemic corticosteroids and later on with cyclophosphamide and methotrexate. There were improvement of visual symptoms and stabilisation of left hearing.Conclusion. Cogan’s syndrome is a very rare disease with no specific biological tests for the diagnosis. The diagnostic exams are mostly important to exclude other etiologies. The atypical ocular and audiovestibular manifestations make the diagnosis difficult, delaying the institution of appropriate therapy which may result in profound bilateral deafness.

scholarly journals Autoimmune ear disease: clinical and diagnostic relevance in Cogan’s sydrome

2017 ◽  
Vol 7 (1) ◽  
Author(s):  
Luigi Maiolino ◽  
Salvatore Cocuzza ◽  
Angelo Conti ◽  
Luisa Licciardello ◽  
Agostino Serra ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Inner Ear ◽  
Systemic Vasculitis ◽  
Clinical Syndrome ◽  
Inflammatory Disorder ◽  
Cogan’S Syndrome ◽  
Cogan's Syndrome ◽  
Interstitial Keratitis ◽  
Inner Ear Disease ◽  
Autoimmune Inner Ear Disease

The autoimmune inner ear disease is a clinical syndrome with uncertain pathogenesis that is often associated to rapidly progressive hearing loss that, especially at the early stages of disease, may be at monoaural localization, although more often it is at binaural localization. It usually occurs as a sudden deafness, or a rapidly progressive sensorineural hearing loss. In this study a particular form of autoimmune inner ear disease is described, Cogan’s syndrome. Cogan’s syndrome is a chronic inflammatory disorder that most commonly affects young adults. Clinical hallmarks are interstitial keratitis, vestibular and auditory dysfunction. Associations between Cogan’s syndrome and systemic vasculitis, as well as aortitis, also exist. We report a case of a young woman who presented audiological and systemic characteristics attributable to Cogan’s syndrome. In the description of the case we illustrate how the appearance and evolution of the disease presented.

scholarly journals Interstitial keratitis in patients with Cogan’s Syndrome

2017 ◽  
Vol 76 (1) ◽  
Author(s):  
Thiago Gonçalves dos Santos Martins ◽  
Ana Luiza Fontes de Azevedo Costa ◽  
Thomaz Gonçalves dos Santos Martins
Keyword(s):  
Cogan’S Syndrome ◽  
Cogan's Syndrome ◽  
Interstitial Keratitis

scholarly journals Sudden sensorineural hearing loss in atypical Cogan's syndrome: A case report

2018 ◽  
Vol 30 ◽  
pp. 50-53
Author(s):  
José Luis Treviño González ◽  
German A. Soto-Galindo ◽  
Rafael Moreno Sales ◽  
Josefina A. Morales Del Ángel
Keyword(s):  
Hearing Loss ◽  
Case Report ◽  
Sensorineural Hearing Loss ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Cogan’S Syndrome ◽  
Cogan's Syndrome

scholarly journals Cochlear Ossification in a Patient with Cogan’s Syndrome Undergoing Bilateral Cochlear Implantation

2018 ◽  
Vol 2018 ◽  
pp. 1-2
Author(s):  
Adam M. Cassis
Keyword(s):  
Medical Treatment ◽  
Cochlear Implantation ◽  
Rapid Onset ◽  
Young Female ◽  
The Body ◽  
Cogan’S Syndrome ◽  
Vestibular Loss ◽  
Cogan's Syndrome ◽  
Eye Symptoms ◽  
Cochlear Ossification

We present the case of a young female patient diagnosed with Cogan’s syndrome after the rapid onset of profond hearing and vestibular loss with concomitant eye symptoms. After appropriate medical treatment, her hearing did not respond and she underwent bilateral simultaneous cochlear implantation with findings of extensive cochlear ossification in both ears. The case and outcome are described in the body of the paper.

Late onset Cogan's syndrome

1989 ◽  
Vol 103 (5) ◽  
pp. 512-514 ◽  
Author(s):  
H. Fidler ◽  
N. S. Jones
Keyword(s):  
Young Adults ◽  
Hearing Loss ◽  
Sedimentation Rate ◽  
Late Onset ◽  
Sudden Hearing Loss ◽  
Older Patient ◽  
Cogan’S Syndrome ◽  
Prompt Treatment ◽  
Erythrocyte Sedimentation ◽  
Cogan's Syndrome

AbstractPrevious reports describe Cogan's syndrome occurring in young adults this case shows that it can be diagnosed in an older patient, and that prompt treatment is often successful, making it a worthwhile diagnosis to consider in patients with sudden hearing loss. The erythrocyte sedimentation rate was a useful marker for disease activity in this patient.

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