Duplicated left pulmonary artery: an unknown disease? Three case reports and review of the literature

2015 ◽  
Vol 26 (2) ◽  
pp. 340-346 ◽  
Author(s):  
Valentina Giudici ◽  
Mazyar Kanani ◽  
Nagarajan Muthialu ◽  
Michelle Carr ◽  
Alistair D. Calder ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Surgical Repair ◽  
Case Reports ◽  
Vascular Ring ◽  
Symptomatic Patient ◽  
Left Pulmonary Artery ◽  
Kabuki Syndrome ◽  
Cross Sectional ◽  
Abnormal Finding ◽  
Pulmonary Sling

AbstractWe report three cases of an abnormal finding of duplicated left pulmonary artery: two of these occurring in children with Kabuki syndrome and configuring the setting of a pseudo-pulmonary sling without any clinical or cardiac cross-sectional evidence of tracheal compression. The other case instead represents duplicated left pulmonary artery with pulmonary sling caused by the retro-tracheal course of the lower left pulmonary artery associated with “Christmas Tree” arrangement of the tracheo-bronchial system.In both patients with pseudo-pulmonary sling and Kabuki syndrome, the abnormal finding was incidental during echocardiographic examination and neither of the patients required surgical repair for the condition. To the best of our knowledge, they represent the third and fourth cases in which such an anomaly of the pulmonary artery branches not forming a sling is seen in association with Kabuki syndrome. Another case represents our second experience and the second case reported in literature with duplicated left pulmonary artery in the setting of a complex tracheal anatomy. In this symptomatic patient, surgical repair of atrial septal defect and relief of the vascular ring were indicated, and the surgical repair was performed successfully at the age of 3 years.

A pulmonary artery sling with a vascular ring in a toddler: an uncommon combination

2018 ◽  
Vol 28 (5) ◽  
pp. 783-785 ◽  
Author(s):  
Ziyad M. Binsalamah ◽  
Charles D. Fraser ◽  
Carlos M. Mery
Keyword(s):  
Pulmonary Artery ◽  
Surgical Repair ◽  
Vascular Ring ◽  
Median Sternotomy ◽  
Left Pulmonary Artery ◽  
Pulmonary Artery Sling ◽  
Screening Process ◽  
Vascular Rings ◽  
Limb Malformations ◽  
Left Pulmonary Artery Sling

AbstractPulmonary artery slings and vascular rings are very rare congenital anomalies. It is even rarer to have both anomalies in the same setting. We present a case of a toddler who was diagnosed with a left pulmonary artery sling and a vascular ring as part of the screening process for the VACTERL association – co-occurrence of vertebral, anorectal, cardiac, tracheoesophageal, renal, and limb malformations. He underwent a successful surgical repair via median sternotomy and on cardiopulmonary bypass with an uneventful postoperative course.

Isolated origin of the left subclavian artery from the left pulmonary artery

2000 ◽  
Vol 10 (2) ◽  
pp. 120-125 ◽  
Author(s):  
Jennifer L Russell ◽  
Jeffrey F. Smallhorn ◽  
Michael D. Black ◽  
Lisa K. Hornberger
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Subclavian Artery ◽  
Surgical Repair ◽  
Left Subclavian Artery ◽  
Vascular Ring ◽  
Left Pulmonary Artery ◽  
Right Aortic Arch ◽  
Cardiac Malformation ◽  
Fourth Arch

AbstractWe describe two children with isolated origin of the left subclavian artery from the left pulmonary artery detected by echocardiography during the assessment of their congenital cardiac malformations. Both patients demonstrated pre-operative evidence of subclavian steal. This entity results from persistence of the dorsal segment of the sixth left arch, with regression of the left fourth arch and interruption of the left dorsal arch distal to the origin of the seventh left intersegmental artery. The significance of this finding relates to the potential for pulmonary overcirculation, which could have significant post-operative ramifications if not detected prior to surgical repair of an associated cardiac malformation. This entity differs from cases with a right aortic arch and aberrant left subclavian artery which has the potential to form a vascular ring, unlike cases with isolated origin of the left subclavian artery from the pulmonary artery that do not cause compression of the airway.

Anomalous origin of a pulmonary artery in a teenager with tetralogy of Fallot with associated double aortic arch and coronary arteriovenous fistula

2019 ◽  
Vol 29 (5) ◽  
pp. 727-729
Author(s):  
Vishal Agrawal ◽  
Parth Solanki ◽  
Ritesh Shah ◽  
Divyakant Parmar ◽  
Amit Mishra
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Vascular Ring ◽  
Right Ventricular Outflow Tract ◽  
Left Pulmonary Artery ◽  
Ventricular Outflow Tract ◽  
Double Aortic Arch ◽  
Anomalous Origin ◽  
Tract Fistula

AbstractWe report the case of a 14-year-old female who had tetralogy of Fallot along with anomalous origin of the left pulmonary artery from the ascending aorta with co-dominant double aortic arch forming a complete vascular ring compressing the oesophagus along with a left main coronary artery to right ventricular outflow tract fistula. She underwent surgical correction without conduit placement.

scholarly journals Prenatal Diagnosis of Left Pulmonary Artery-to-Pulmonary Vein Fistula and Its Successful Surgical Repair in a Neonate

2015 ◽  
Vol 42 (2) ◽  
pp. 169-171 ◽  
Author(s):  
Oleksii Ostras ◽  
Andrii Kurkevych ◽  
Lyubomyr Bohuta ◽  
Tetyana Yalynska ◽  
Tammo Raad ◽  
...  
Keyword(s):  
Prenatal Diagnosis ◽  
Pulmonary Artery ◽  
Arteriovenous Fistula ◽  
Rare Disease ◽  
Pulmonary Vein ◽  
Medical Literature ◽  
Surgical Repair ◽  
Left Pulmonary Artery ◽  
Pulmonary Arteriovenous Fistula ◽  
Left Pulmonary Vein

Pulmonary arteriovenous fistula is a rare disease. To the best of our knowledge, prenatal diagnosis of a fistula between the left pulmonary artery and the left pulmonary vein has not been described in the medical literature. We report a case of the prenatal diagnosis of a left pulmonary artery-to-pulmonary vein fistula, followed by successful neonatal surgical repair.

Echocardiographic follow-up of percutaneous closure of the arterial duct in infants

1992 ◽  
Vol 2 (4) ◽  
pp. 335-337
Author(s):  
Luis Fernández Piñeda ◽  
Hugo Torrealday ◽  
Ramón Bermúdez Cañete ◽  
María J. Maitre Azcárate ◽  
Manuel Quero Jiménez
Keyword(s):  
Pulmonary Artery ◽  
Left Atrium ◽  
Color Doppler ◽  
Excellent Result ◽  
High Sensitivity ◽  
Left Pulmonary Artery ◽  
Left Ventricular ◽  
Cross Sectional ◽  
Arterial Duct

SummarySince February 1990, we have attempted nonsurgical occlusion of persistent patency of the arterial duct using the Rashkind double-disk occluding device, of either 12 or 17 mm diameter. Results are presented from 31 patients (23 female and eight male, ages 15 months to 16 years). M-Mode, cross-sectional, Doppler and color Doppler echocardiographic studies were made prior to closure, in the following 24 hours, and six months later. Left ventricular diastolic dimension and shortening fraction, systolic intervals, and left atrium/aortic ratio were evaluated by M-Mode echo. We examined carefully the location of the device relative to the left pulmonary artery and descending aorta, also checking for disturbed flows and residual shunts. These studies showed a clear tendency for the left ventricular diameter to decrease, and revealed a significant normalization of the left atrium/aortic ratio. Successful closure of the duct was achieved in 27 cases. Follow-up studies six months later showed residual shunting in four cases. In one patient, a second device was implanted with an excellent result. At the immediate follow-up, turbulences were noted in the area of the device (nine cases) and in the left pulmonary artery (seven cases). Distortion of the anatomic orientation of the left pulmonary artery was observed in three cases in which we discovered 20 mm Hg systolic gradients. In our opinion, echocardiography is the best technique with which to follow-up these patients. The high sensitivity of color Doppler echocardiography revealed minimal distortion of the left pulmonary artery, probably generated by regional anatomic adjustment to the insertion of the device.

Bronchial Obstruction Due to Pulmonary Artery Anomalies. I. Vascular Sling

PEDIATRICS ◽  
1958 ◽  
Vol 22 (1) ◽  
pp. 48-48
Keyword(s):  
Pulmonary Artery ◽  
Clinical Symptoms ◽  
Early Recognition ◽  
Vascular Ring ◽  
Left Lung ◽  
Posterior Wall ◽  
Left Pulmonary Artery ◽  
Bronchial Obstruction ◽  
Vascular Sling ◽  
The Right

The authors report three cases of respiratory embarrassment in infants from compression of the right bronchus and trachea by a "vascular sling" formed by an aberrant left pulmonary artery coursing anterior to the right main-stem bronchus and posterior to the trachea. Five similar cases have been described in earlier literature. The embryologic origin of this anomaly appears to be a disturbed time-sequence in the growth and union of the left pulmonary artery and the left lung bud. The clinical symptoms are those of respiratory distress in the neonatal period produced by tracheobronchial compression, associated with obstructive emphysema of the right lung. Bronchoscopic examination reveals extrinsic pressure on the right bronchus and posterior wall of the trachea. The esophagram does not reveal any posterior indentation and is thereby helpful in distinguishing this entity from the more common "vascular ring" which is a systemic arterial malformation causing constriction of the trachea and esophagus. Early recognition of an anomalous left pulmonary artery is particularly important in view of the fact that the condition can be corrected surgically.

scholarly journals Concurrent vascular ring and occult left pulmonary artery associated with ventricular septal defect: A report of an uncommon constellation

1999 ◽  
Vol 118 (6) ◽  
pp. 1127-1129
Author(s):  
Kulbhushan Singh Dagar ◽  
Tain-Yen Hsia ◽  
Robert Yates ◽  
James F.N. Taylor ◽  
Marc R. de Leval ◽  
...  
Keyword(s):  
Ventricular Septal Defect ◽  
Pulmonary Artery ◽  
Septal Defect ◽  
Vascular Ring ◽  
Left Pulmonary Artery
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