Transcatheter closure of Abernethy malformation associated with interrupted inferior caval vein and other systemic venous anomalies

2021 ◽  
pp. 1-3
Author(s):  
Samir Shakya ◽  
Anita Saxena ◽  
Sivasubramanian Ramakrishnan
Keyword(s):  
Pulmonary Hypertension ◽  
Transcatheter Closure ◽  
Rare Entity ◽  
Severe Pulmonary Hypertension ◽  
Device Closure ◽  
Venous Anatomy ◽  
Vascular Plug ◽  
Caval Vein ◽  
Abernethy Malformation ◽  
Inferior Caval Vein

Abstract Abernethy malformation is a rare entity. We report a 5-year-old boy presenting with severe pulmonary hypertension in whom Abernethy malformation and inferior caval vein interruption were diagnosed by CT angiography. In addition, the iliac veins were thrombosed with multiple venous collateral drainage. This abnormal venous anatomy caused difficulty in device closure of the Abernethy malformation, which was successfully closed using a vascular plug.

The Abernethy malformation with inferior caval vein hypoplasia: a tailored technique for transcatheter closure and an insight into embryological perspective

2018 ◽  
Vol 28 (9) ◽  
pp. 1169-1171
Author(s):  
Ronak Sheth ◽  
Kothandam Sivakumar
Keyword(s):  
Transcatheter Closure ◽  
Hepatopulmonary Syndrome ◽  
Portosystemic Shunt ◽  
Caval Vein ◽  
Abernethy Malformation ◽  
Venous Anomalies ◽  
Inferior Caval Vein ◽  
Insight Into

AbstractAbernethy malformations manifest as hepatopulmonary syndrome, pulmonary vasculopathy, or encephalopathy. A novel intervention in a child with portosystemic shunt and inferior caval vein hypoplasia led to complete normalisation of hypoxia and relief of obstruction in the inferior caval vein. Embryological explanations of venous anomalies may indicate that inferior caval vein anomalies are frequent but under-recognised in patients with Abernethy malformation.

Haemodynamic consequences following closure of an Abernethy malformation in a patient following a total cavopulmonary shunt

2018 ◽  
Vol 28 (5) ◽  
pp. 768-770 ◽  
Author(s):  
Deepa Sasikumar ◽  
Bijulal Sasidharan ◽  
Anoop Ayyappan
Keyword(s):  
Septal Defect ◽  
Pulmonary Stenosis ◽  
Vascular Plug ◽  
Caval Vein ◽  
Abernethy Malformation ◽  
Inferior Caval Vein ◽  
Hypoplastic Right Ventricle ◽  
Situs Ambiguous ◽  
Cavopulmonary Shunt ◽  
Kawashima Operation

AbstractA 17-year-old girl with situs ambiguous, hypoplastic right ventricle with a large ventricular septal defect, and severe pulmonary stenosis had undergone Kawashima operation 10 years back. She had significant desaturation because of a large Abernethy malformation, with reverse shunting from the inferior caval vein to the portal vein. It was closed with a vascular plug, with improvement in oxygen saturation. She developed extensive inferior caval vein thrombus following the procedure, which was managed conservatively by anti-coagulation.

Transcatheter closure of a large left ventricular pseudoaneurysm using an Amplatzer Vascular Plug 4 and stenting of the inferior caval vein in a child

2011 ◽  
Vol 22 (1) ◽  
pp. 106-109 ◽  
Author(s):  
Osman Baspinar ◽  
Ahmet Mete ◽  
Vedat Davutoglu
Keyword(s):  
Treatment Option ◽  
Transcatheter Closure ◽  
Left Ventricular ◽  
Amplatzer Vascular Plug ◽  
Vascular Plug ◽  
Caval Vein ◽  
Left Ventricular Pseudoaneurysm ◽  
Inferior Caval Vein ◽  
Amplatzer Vascular Plug 4

AbstractLeft ventricular pseudoaneurysm is especially rare in childhood, and its main treatment option should be surgery. We describe the case of a 9.5-year-old boy who first underwent mitral vegetation excision and then an unsuccessful pseudoaneurysm operation. Owing to pseudoaneurysmal sac dimensions, inferior caval vein syndrome developed. We delivered the Amplatzer Vascular Plug 4 into the pseudoaneurysm and treated the inferior caval vein syndrome with a bare Cheatham–Platinum stent. The patient was asymptomatic at the last follow-up.

Left-sided hepatic vein connected to the coronary sinus

1996 ◽  
Vol 6 (2) ◽  
pp. 190-192 ◽  
Author(s):  
László Király ◽  
John E. Deanfield ◽  
Marc R. de Leval
Keyword(s):  
Hepatic Vein ◽  
Coronary Sinus ◽  
Left Atrial ◽  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Rare Entity ◽  
Biventricular Repair ◽  
Caval Vein ◽  
Inferior Caval Vein ◽  
Complete Atrioventricular

AbstractA left-sided hepatic vein connected to the coronary sinus is reported in a case of a 22-month-old boy with isomerism of the left atrial appendages, complete atrioventricular septal defect and azygous continuation of the inferior caval vein. The diagnosis of the anomalous hepatic vein was made intraoperatively and successful biventricular repair has been accomplished. To the best of our knowledge, this is the first communication on this peculiar entity diagnosed during life, notwithstanding Nabarro's description of a similar autopsy finding in 1903. Aspects of the development of this rare entity are discussed.

scholarly journals Transcatheter Closure of Adult Patent Ductus Arteriosus with Severe Pulmonary Hypertension

2008 ◽  
Vol 31 (11) ◽  
pp. 1997-2002 ◽  
Author(s):  
Qiang Ji ◽  
Jing Feng ◽  
Yunqing Mei ◽  
Xisheng Wang ◽  
Jiangzhi Cai ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Patent Ductus Arteriosus ◽  
Transcatheter Closure ◽  
Ductus Arteriosus ◽  
Severe Pulmonary Hypertension ◽  
Patent Ductus

Transcatheter closure of atrial septal defect in a patient with absent inferior caval vein connection: a novel technique using a steerable guide catheter

2016 ◽  
Vol 26 (5) ◽  
pp. 1033-1035 ◽  
Author(s):  
Yoichi Takaya ◽  
Teiji Akagi ◽  
Hiroshi Ito
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Transcatheter Closure ◽  
Defect Closure ◽  
Caval Vein ◽  
Atrial Septal Defect Closure ◽  
Novel Technique ◽  
Inferior Caval Vein ◽  
Guide Catheter ◽  
Alternative Approach

AbstractAn alternative approach for transcatheter closure of atrial septal defect is necessary in patients with absent inferior caval vein connection. In this report, we describe the successful transcatheter atrial septal defect closure via the transjugular approach using a steerable guide catheter.

Intermediate- and long-term follow-up of device closure of patent arterial duct with severe pulmonary hypertension: factors predicting outcome

2016 ◽  
Vol 27 (1) ◽  
pp. 26-36 ◽  
Author(s):  
Masood Sadiq ◽  
Asif U. Rehman ◽  
Najam Hyder ◽  
Ahmad U. Qureshi ◽  
Tehmina Kazmi ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Artery ◽  
Pulmonary Vascular Resistance ◽  
Vascular Resistance ◽  
Resistance Index ◽  
Severe Pulmonary Hypertension ◽  
Device Closure ◽  
Pulmonary Vascular Resistance Index

AbstractBackgroundIn patients with large patent arterial ducts and severe pulmonary hypertension, the natural history of progression of pulmonary hypertension is very variable. Whether to close or not to close is often a difficult decision, as there are no established haemodynamic parameters predicting reversibility.ObjectivesThe objectives of this study were to evaluate the results of device closure of large patent arterial ducts with severe pulmonary hypertension after 2 years of age and to determine haemodynamic variables associated with its regression during long-term follow-up.MethodsA total of 45 patients, with median age of 10 (2–27) years, with large patent arterial ducts and severe pulmonary hypertension, were considered. Haemodynamic variables were assessed in air, oxygen, and after occlusion. The follow-up was performed to assess regression of pulmonary hypertension.ResultsDevice closure was successful in 43 (96%) patients. Pulmonary artery systolic and mean pressures decreased from 79 to 67 mmHg and from 59 to 50 mmHg, respectively (p<0.001). At a median follow-up of 80 (41–151) months, severe pulmonary hypertension persisted in four (9.7%) patients. Multivariate analysis showed pulmonary vascular resistance index ⩽6 WU m2 and pulmonary artery systolic and mean pressures ⩽75 and ⩽55 mmHg (all in oxygen), having 97.8% predictive value for regression of pulmonary hypertension (p<0.001) in the long term. In 24 patients with catheterisation-based criteria, regression of pulmonary hypertension was associated with pulmonary vascular resistance index <8 WU m2 (p=0.001) and its fall of >25% (both in oxygen) (p=0.007).ConclusionsDevice closure of large patent arterial ducts with severe pulmonary hypertension is safe and effective. Pulmonary vascular resistance index and systolic and mean pulmonary artery pressures in oxygen are the key prognostic variables predicting regression of pulmonary hypertension.

Transcatheter closure of a multiperforated atrial septal defect extending from the oval fossa to the mouth of the inferior caval vein

2003 ◽  
Vol 13 (2) ◽  
pp. 200-202 ◽  
Author(s):  
Matthias Peuster ◽  
Julia Reckers ◽  
Christoph Fink
Keyword(s):  
Septal Defect ◽  
Transcatheter Closure ◽  
Close Relation ◽  
Interatrial Septum ◽  
Right Atrial ◽  
Caval Vein ◽  
Posterior Portion ◽  
Inferior Caval Vein ◽  
Amplatzer Device ◽  
The Right

We report a novel technique using an Amplatzer atrial septal occluder to close a defect located in the inferior-posterior portion of the interatrial septum that extended into the mouth of the inferior caval vein. Because of the close relation of the defect to the inferior caval vein, the right atrial disc was opened into the inferior caval vein and pushed toward the right atrium by use of the delivery cable. There was no residual shunting immediately and 3 months after the intervention. We conclude that even defects located infero-posteriorly within the oval fossa may be successfully closed by transcatheter techniques using the Amplatzer device.

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