The ΔF508 Mutation Disrupts Packing of the Transmembrane Segments of the Cystic Fibrosis Transmembrane Conductance Regulator

Journal of Biological Chemistry ◽

10.1074/jbc.m407887200 ◽

2004 ◽

Vol 279 (38) ◽

pp. 39620-39627 ◽

Author(s):

Eva Y. Chen ◽

M. Claire Bartlett ◽

Tip W. Loo ◽

David M. Clarke

Keyword(s):

Cystic Fibrosis ◽

Transmembrane Conductance Regulator ◽

Transmembrane Conductance ◽

Transmembrane Segments ◽

Cystic Fibrosis Transmembrane

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Cooperativity and Flexibility of Cystic Fibrosis Transmembrane Conductance Regulator Transmembrane Segments Participate in Membrane Localization of a Charged Residue

Journal of Biological Chemistry ◽

10.1074/jbc.m205759200 ◽

2002 ◽

Vol 277 (42) ◽

pp. 39507-39514 ◽

Author(s):

Kristin Carveth ◽

Teresa Buck ◽

Victoria Anthony ◽

William R. Skach

Keyword(s):

Cystic Fibrosis ◽

Membrane Localization ◽

Transmembrane Conductance Regulator ◽

Transmembrane Conductance ◽

Charged Residue ◽

Transmembrane Segments ◽

Cystic Fibrosis Transmembrane

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Intracellular Loop between Transmembrane Segments IV and V of Cystic Fibrosis Transmembrane Conductance Regulator Is Involved in Regulation of Chloride Channel Conductance State

Journal of Biological Chemistry ◽

10.1074/jbc.270.47.28084 ◽

1995 ◽

Vol 270 (47) ◽

pp. 28084-28091 ◽

Author(s):

Junxia Xie ◽

Mitchell L. Drumm ◽

Jianjie Ma ◽

Pamela B. Davis

Keyword(s):

Cystic Fibrosis ◽

Chloride Channel ◽

Transmembrane Conductance Regulator ◽

Channel Conductance ◽

Intracellular Loop ◽

Transmembrane Conductance ◽

Transmembrane Segments ◽

Cystic Fibrosis Transmembrane ◽

Conductance State

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Der Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) und Sphingolipide regulieren die hypoxisch pulmonale Vasokonstriktion

Pneumologie ◽

10.1055/s-0036-1571988 ◽

2016 ◽

Vol 70 (S 01) ◽

Author(s):

C Tabeling ◽

H Yu ◽

L Wang ◽

H Ranke ◽

NM Goldenberg ◽

...

Keyword(s):

Cystic Fibrosis ◽

Transmembrane Conductance Regulator ◽

Transmembrane Conductance ◽

Cystic Fibrosis Transmembrane

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Faculty Opinions recommendation of Curcumin stimulates cystic fibrosis transmembrane conductance regulator Cl- channel activity.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.1024340.288770 ◽

2005 ◽

Author(s):

William H Colledge

Keyword(s):

Cystic Fibrosis ◽

Transmembrane Conductance Regulator ◽

Channel Activity ◽

Transmembrane Conductance ◽

Cystic Fibrosis Transmembrane

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Faculty Opinions recommendation of Sequential quality-control checkpoints triage misfolded cystic fibrosis transmembrane conductance regulator.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.1046329.496274 ◽

2006 ◽

Author(s):

Davis Ng

Keyword(s):

Cystic Fibrosis ◽

Quality Control ◽

Transmembrane Conductance Regulator ◽

Transmembrane Conductance ◽

Cystic Fibrosis Transmembrane

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Faculty Opinions recommendation of Resistance to Pseudomonas aeruginosa chronic lung infection requires cystic fibrosis transmembrane conductance regulator-modulated interleukin-1 (IL-1) release and signaling through the IL-1 receptor.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.1065903.518850 ◽

2007 ◽

Author(s):

Joanna Goldberg

Keyword(s):

Cystic Fibrosis ◽

Pseudomonas Aeruginosa ◽

Interleukin 1 ◽

Lung Infection ◽

Transmembrane Conductance Regulator ◽

Transmembrane Conductance ◽

Cystic Fibrosis Transmembrane ◽

Chronic Lung Infection

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Faculty Opinions recommendation of Identification of new small molecule inhibitors of cystic fibrosis transmembrane conductance regulator protein: in vitro and in vivo studies.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.1069767.522696 ◽

2007 ◽

Author(s):

Kim Barrett

Keyword(s):

Cystic Fibrosis ◽

Small Molecule ◽

Small Molecule Inhibitors ◽

In Vivo Studies ◽

Transmembrane Conductance Regulator ◽

Transmembrane Conductance ◽

Regulator Protein ◽

Cystic Fibrosis Transmembrane

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Faculty Opinions recommendation of MicroRNA regulation of expression of the cystic fibrosis transmembrane conductance regulator gene.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.13361055.14731200 ◽

2011 ◽

Author(s):

Pradeep Dudeja ◽

Arivarasu Natarajan Anbazhagan

Keyword(s):

Cystic Fibrosis ◽

Transmembrane Conductance Regulator ◽

Regulator Gene ◽

Transmembrane Conductance ◽

Regulation Of Expression ◽

Microrna Regulation ◽

Cystic Fibrosis Transmembrane

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Faculty Opinions recommendation of Cystic fibrosis transmembrane conductance regulator is expressed in mucin granules from Calu-3 and primary human airway epithelial cells.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.718017856.793479176 ◽

2013 ◽

Author(s):

Steven M Rowe ◽

Sammeta Vamsee Raju

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Airway Epithelial Cells ◽

Transmembrane Conductance Regulator ◽

Airway Epithelial ◽

Transmembrane Conductance ◽

Human Airway ◽

Cystic Fibrosis Transmembrane ◽

Human Airway Epithelial Cells

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Faculty Opinions recommendation of Atomic structure of the cystic fibrosis transmembrane conductance regulator.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.727060497.793525983 ◽

2016 ◽

Author(s):

Ronald Kaback ◽

Lan Guan

Keyword(s):

Cystic Fibrosis ◽

Atomic Structure ◽

Transmembrane Conductance Regulator ◽

Transmembrane Conductance ◽

Cystic Fibrosis Transmembrane

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