Primary middle-ear lymphoma in a child

2003 ◽  
Vol 117 (3) ◽  
pp. 205-207 ◽  
Author(s):  
Emer E. Lang ◽  
Rory M. Walsh ◽  
Mary Leader
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Temporal Bone ◽  
Middle Ear ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Conductive Hearing Loss ◽  
Motor Neurone ◽  
Hodgkin's Lymphoma ◽  
Conductive Hearing

The case of a five year old boy who presented with a lower motor neurone facial nerve palsy secondary to primary non-Hodgkin’s lymphoma (NHL) of the middle ear is discussed. Any child who presents with a facial nerve palsy and conductive hearing loss requires thorough evaluation to exclude the possibility of temporal bone malignancy.

Hearing loss

2018 ◽  
Author(s):  
James Ramsden
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Middle Ear ◽  
Cranial Nerve ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Conductive Hearing Loss ◽  
Ear Canal ◽  
Eighth Cranial Nerve ◽  
Conductive Hearing

Hearing loss must be divided into conductive hearing loss (CHL) and sensorineural hearing loss (SNHL). CHL is caused by sound not reaching the cochlear (abnormality of the ear canal, tympanic membrane, middle ear, or ossicles), whereas SNHL is a condition affecting the cochlear or auditory (eighth cranial) nerve. Hearing loss may be accompanied by other cardinal signs of ear disease, such as pain or discharge from the ear, vertigo, facial nerve palsy, and tinnitus, which guide the diagnosis. This chapter describes the approach to the patient with hearing loss.

Double Intratemporal Congenital Cholesteatomas Combined with Ossicular Anomalies

1986 ◽  
Vol 95 (4) ◽  
pp. 401-403 ◽  
Author(s):  
Tsun-Sheng Huang
Keyword(s):  
Hearing Loss ◽  
Early Detection ◽  
Temporal Bone ◽  
Nerve Palsy ◽  
Surgical Intervention ◽  
Facial Nerve Palsy ◽  
Conductive Hearing Loss ◽  
The Other ◽  
Presenting Symptoms ◽  
Conductive Hearing

A 15-year-old patient had unilateral double congenital cholesteatomas, one isolated to the mastoid and the other located in the petrous pyramid. The presenting symptoms were facial palsy and a conductive hearing loss on the affected side. The case is interesting, not only in that there were two isolated cholesteatomas in the same temporal bone, but also because of the combination of ossicular anomalies. The unusually early detection and surgical intervention in this instance suggest that similar cases of multicentric cholesteatomas may have occurred, but may have been concealed because of the later detection and possible linkage of the cholesteatomas. I would therefore emphasize Sheehy's recommendation that temporal bone radiography never be omitted where idiopathic facial nerve palsy exists.

Neglected keratosis obturans causing facial nerve palsy

2006 ◽  
Vol 120 (9) ◽  
pp. 784-785 ◽  
Author(s):  
F Glynn ◽  
I J Keogh ◽  
H Burns
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
External Auditory Canal ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Conductive Hearing Loss ◽  
Conductive Hearing

Keratosis obturans is characterized by the accumulation of desquamated keratinous material in the bony portion of the external auditory canal. Classically, it is reported to present with severe otalgia, conductive hearing loss and global widening of the external auditory canal. Extensive erosion of the bony meatus, with exposure of the facial nerve, has been previously reported, but no case of facial nerve palsy has as yet been published. We report the first published case, to our knowledge, of a unilateral facial nerve palsy secondary to neglected keratosis obturans.

A bifid intra-tympanic facial nerve in association with a normal stapes

2006 ◽  
Vol 120 (5) ◽  
pp. 414-415 ◽  
Author(s):  
J Ahmed ◽  
P Chatrath ◽  
J Harcourt
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Middle Ear ◽  
Conductive Hearing Loss ◽  
Anatomical Variations ◽  
Middle Ear Surgery ◽  
Ear Surgery ◽  
Ossicular Reconstruction ◽  
Conductive Hearing

A rare facial nerve anomaly was incidentally discovered whilst performing a tympanoplasty and ossicular reconstruction on a patient with an acquired unilateral conductive hearing loss. The nerve was seen to bifurcate and straddle a normal stapes superstructure as it ran posteriorly through the middle ear, a unique and as yet unreported combination. This case highlights the importance of vigilance regarding facial nerve anatomical variations encountered during middle-ear surgery thus avoiding inadvertent damage. The purported embryological mechanism responsible for such anomalies of the intra-tympanic facial nerve is discussed.

Congenital internal auditory canal stenosis

2003 ◽  
Vol 117 (10) ◽  
pp. 784-787 ◽  
Author(s):  
Seung Kuk Baek ◽  
Sung Won Chae ◽  
Hak Hyun Jung
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Facial Nerve ◽  
Ct Scan ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Internal Auditory Canal ◽  
Canal Stenosis

Congenital internal auditory canal stenosis is a rare cause of sensorineural hearing loss in children. A retrospective analysis including clinical manifestation and radiological findings was made for seven patients who were diagnosed with congenital internal auditory canal stenosis from 1996 to 2002. Chief presenting symptoms were hearing loss, facial nerve palsy, dizziness, and tinnitus. Hearing loss including deafness was found in five cases, vestibular function loss in four cases, and profound functional loss of facial nerve in two cases. In all cases, the diameter of the internal auditory canal was less than 2 mm on high-resolution temporal bone computed tomography (CT) scan. Two cases revealed bilateral internal auditory canal stenosis, and others were unilaterally involved cases. Congenital internal auditory canal stenosis can be an important cause of sensorineural hearing loss, facial nerve palsy, and vestibular dysfunction. High resolution temporal bone CT scan and magnetic resonance (MR) imaging were important tools for diagnosis.

scholarly journals Salivary Gland Choristoma of the Middle Ear in a Child: A Case Report

2021 ◽  
pp. 014556132199502
Author(s):  
Jana Jančíková ◽  
Soňa Šikolová ◽  
Josef Machač ◽  
Marta Ježová ◽  
Denisa Pavlovská ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Salivary Gland ◽  
Case Report ◽  
Facial Nerve ◽  
Middle Ear ◽  
Conductive Hearing Loss ◽  
Hearing Aid ◽  
Bone Anchored Hearing Aid ◽  
Conductive Hearing

Salivary gland choristoma is an extremely rare middle ear pathology. We present the case of a 10-year-old girl with unilateral conductive hearing loss. Tympanotomy showed a nonspecific middle ear mass, absence of stapes, anomaly of incus, and displaced facial nerve. It was not possible to remove the mass completely. Histology confirmed salivary gland choristoma. The hearing in this case can be improved with a bone-anchored hearing aid.

scholarly journals Demineralization of the Otic Capsule in Otosclerosis (Otospongiosis)

2009 ◽  
Vol 24 (1) ◽  
pp. 35-36
Author(s):  
Nathaniel W. Yang
Keyword(s):  
Hearing Loss ◽  
Temporal Bone ◽  
Middle Ear ◽  
Conductive Hearing Loss ◽  
Ct Imaging ◽  
Focal Region ◽  
Otic Capsule ◽  
Organ Systems ◽  
Temporal Bone Ct ◽  
Conductive Hearing

A 34-year old Filipina presents with bilateral progressive hearing loss and tinnitus of three years' duration. Otologic examination reveals normal external auditory canals and tympanic membranes, with good tympanic membrane mobility on pneumatic otoscopy. Standard audiometric examination shows a bilateral moderate conductive hearing loss. Temporal bone CT imaging reveals the presence of a focal region of bone demineralization involving the dense bone of the otic capsule surrounding the cochlear lumen (Figure 1), a finding consistent with a diagnosis of active otospongiosis.  The diagnosis was confirmed by visualization of an otosclerotic focus during transcanal middle ear exploration, where stapedectomy with placement of a stainless steel stapes prosthesis was performed. Otosclerosis is a condition unique to the temporal bone characterized by abnormal resorption and deposition of bone in the otic capsule and ossicles. Although it occurs more rarely in Asiatic populations compared to Europeans, Americans of Caucasian origin and Indians, it must be considered in patients presenting with primarily conductive hearing loss, especially if there is bilateral involvement. CT imaging of the temporal bone may help to differentiate this condition from other causes of conductive hearing loss, such as tympanosclerosis and bony epitympanic fixation of the ossicular chain from chronic infection and inflammation of the middle ear. One must be cognizant of the fact that a normal temporal bone CT scan does not rule a diagnosis of otosclerosis, because an inactive, highly sclerotic focus that appears as a uniform hyperdense mass may be difficult to distinguish from the normal compact labyrinth capsule (1). Other causes of otic capsule demineralization include osteogenesis imperfecta, Paget disease, otosyphilis, and Camurati-Engelmann disease. These may be differentiated by their individually characteristic patterns of bone involvement and evidence of disease in other organ systems.2  

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