Congenital internal auditory canal stenosis

2003 ◽  
Vol 117 (10) ◽  
pp. 784-787 ◽  
Author(s):  
Seung Kuk Baek ◽  
Sung Won Chae ◽  
Hak Hyun Jung
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Facial Nerve ◽  
Ct Scan ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Internal Auditory Canal ◽  
Canal Stenosis

Congenital internal auditory canal stenosis is a rare cause of sensorineural hearing loss in children. A retrospective analysis including clinical manifestation and radiological findings was made for seven patients who were diagnosed with congenital internal auditory canal stenosis from 1996 to 2002. Chief presenting symptoms were hearing loss, facial nerve palsy, dizziness, and tinnitus. Hearing loss including deafness was found in five cases, vestibular function loss in four cases, and profound functional loss of facial nerve in two cases. In all cases, the diameter of the internal auditory canal was less than 2 mm on high-resolution temporal bone computed tomography (CT) scan. Two cases revealed bilateral internal auditory canal stenosis, and others were unilaterally involved cases. Congenital internal auditory canal stenosis can be an important cause of sensorineural hearing loss, facial nerve palsy, and vestibular dysfunction. High resolution temporal bone CT scan and magnetic resonance (MR) imaging were important tools for diagnosis.

scholarly journals Unilateral internal auditory canal stenosis with progressive facial weakness

2012 ◽  
Vol 18 (2) ◽  
pp. 179-182
Author(s):  
Sathiya Murali ◽  
Arpana Shekhar ◽  
S Shyam Sudhakar ◽  
Kiran Natarajan ◽  
Mohan Kameswaran
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Facial Nerve ◽  
Temporal Bone ◽  
Internal Auditory Canal ◽  
Facial Weakness ◽  
Profound Hearing Loss ◽  
Canal Stenosis ◽  
Temporal Bone Ct ◽  
Magnetic Resonance Imaging Mri

Internal auditory canal (IAC) stenosis is a rare cause of sensorineural hearing loss. Patient may present with symptoms of progressive facial nerve palsy, hearing loss, tinnitus and giddiness. High resolution temporal bone CT-scan and magnetic resonance imaging (MRI) are the important tools for diagnosis. No specific management has been devised. Here is presentation of a case of unilateral (left) IAC stenosis with profound hearing loss and progressive House Brackmann Grade III-IV facial weakness. The diameter of the IAC was less than 2 mm on high resolution temporal bone computed tomography (HRCT) scan. It was managed by facial nerve decompression by translabyrinthine approach in an attempt to prevent further deterioration of facial palsy. DOI: http://dx.doi.org/10.3329/bjo.v18i2.12014 Bangladesh J Otorhinolaryngol 2012; 18(2): 179-182

scholarly journals Bilateral Internal Auditory Canal (IAC) Duplication with Congenital Sensorineural Hearing Loss (SNHL)-A Case Report

2021 ◽  
Vol 20 (4) ◽  
Author(s):  
Nik Adilah Nik Othman ◽  
Nur Saadah Mohamad ◽  
Ahmad Aizuddin Mohamad Jamali ◽  
Mohd Shafie Abdullah ◽  
Mohd Khairi Md Daud
Keyword(s):  
Hearing Loss ◽  
Down Syndrome ◽  
Facial Nerve ◽  
Sensorineural Hearing Loss ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Internal Auditory Canal ◽  
Sensorineural Hearing ◽  
Image Finding ◽  
Suitable Treatment

Duplication of the internal auditory canal is a rare entity. It can be unilateral or bilateral involvement and usually found during an investigation of sensorineural hearing loss or facial nerve palsy. We report this image finding in a child with Down syndrome with bilateral profound sensorineural hearing loss. There was no facial nerve palsy. We highlight the rarity of this image finding and the importance of imaging for detection of middle and inner ear abnormality in a case of congenital sensorineural hearing loss as it helps in decision making for the suitable treatment. Keywords: Duplicate IAC; Bilateral Duplicate IAC; sensorineural hearing loss; Down syndrome

Primary middle-ear lymphoma in a child

2003 ◽  
Vol 117 (3) ◽  
pp. 205-207 ◽  
Author(s):  
Emer E. Lang ◽  
Rory M. Walsh ◽  
Mary Leader
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Temporal Bone ◽  
Middle Ear ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Conductive Hearing Loss ◽  
Motor Neurone ◽  
Hodgkin's Lymphoma ◽  
Conductive Hearing

The case of a five year old boy who presented with a lower motor neurone facial nerve palsy secondary to primary non-Hodgkin’s lymphoma (NHL) of the middle ear is discussed. Any child who presents with a facial nerve palsy and conductive hearing loss requires thorough evaluation to exclude the possibility of temporal bone malignancy.

scholarly journals A Rare Case of Vertebrobasilar Dolichoectasia Presenting with Ipsilateral Facial Paresis and Concomitant Severe Sensorineural Hearing Loss

2014 ◽  
Vol 29 (1) ◽  
pp. 20-22
Author(s):  
Mee Ling Tang ◽  
Govindaraju Revadi ◽  
Raman Rajagopalan ◽  
Sushil Brito-Mutunayagam
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Sensorineural Hearing Loss ◽  
Basilar Artery ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Sensorineural Hearing ◽  
Prior History ◽  
Vertebrobasilar Dolichoectasia ◽  
Nerve Paresis

Objective: To report a case of vertebrobasilar dolichoectasia presenting with ipsilateral facial nerve paresis and concomitant severe sensorineural hearing loss.   Methods:                Design: Case Report                Setting: Secondary Government Hospital                Patient: One   Results:  We report a case of vertebrobasilar dolichoectasia with concomitant ipsilateral facial nerve paresis and severe sensorineural hearing loss in an elderly female.  She presented to us with left facial nerve palsy House-Brackmann Grade III with prior history of ipsilateral sensorineural hearing loss.  MRI of the brain showed normal inner ear structures, but revealed a dilated and tortuous basilar artery with compression on the left medulla and possible branches of anterior inferior cerebellar artery as it coursed superiorly, and possible partial thrombosis of proximal basilar artery.    Conclusion:  Concommitant facial nerve paresis and sensorineural hearing loss can be the clinical presentations of this rare but important condition.  MRI is vital in diagnosing vertebrobasilar dolichoectasia.   Keywords: Vertebrobasilar dolichoectasia, facial nerve palsy, sensorineural hearing loss, basilar artery

scholarly journals Cochlear Otosclerosis: An Undiagnosed Cause of Progressive Sensorineural Hearing Loss

2020 ◽  
Vol 28 (2) ◽  
pp. 127-137
Author(s):  
Asish Kumar Lahiri ◽  
Anandita Gupta ◽  
Rakesh Vohra ◽  
Shalabh Sharma ◽  
Satinder Singh
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Ct Scan ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Young Patients ◽  
Oval Window ◽  
Sensorineural Hearing ◽  
Unknown Etiology ◽  
High Resolution Ct

Introduction Otosclerosis presents as conductive or mixed hearing loss depending upon the stage of the disease. Isolated sensorineural hearing loss though known to occur has been rarely reported. Pure cochlear otosclerosis presenting as sensorineural hearing loss should be considered as a differential diagnosis in young patients presenting with progressive hearing loss. The aim of this article is to note the prevalence of cochlear otosclerosis in young patients presenting with progressive sensorineural hearing loss.  Materials and Methods Retrospective chart analysis of 19 patients who presented with progressive SNHL with unknown etiology was done. Results Otosclerosis involving the pericochlear region was diagnosed in 27 ears which was identified by high resolution CT scan of temporal bone. In four ears, in addition, there was demineralization just anterior to oval window without clinical evidence of stapes fixation. Conclusion In young patients with progressive SNHL, high resolution CT scan of temporal bone should be done to identify progressive cochlear otosclerosis. Medical management should be initiated in these patients to halt the progression of disease.

scholarly journals High resolution temporal bone computerized tomography in paediatric sensorineural hearing loss prior to cochlear implantation

2020 ◽  
Vol 6 (2) ◽  
pp. 282
Author(s):  
Suhail Rafiq ◽  
Fahad Shafi ◽  
Ajaz Mohiuddin ◽  
Sajjad A. Dar
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Cochlear Implant ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Computerized Tomography ◽  
Cochlear Implantation ◽  
Internal Auditory Canal ◽  
Vestibular Aqueduct ◽  
Hrct Temporal Bone

<p class="abstract"><strong>Background:</strong> Congenital sensorineural hearing loss (SNHL) is one of the most common birth defects with incidence of approximately 1:1000 live births. Imaging plays an important role in the work up of cochlear implant candidates not only to identify inner ear congenital and acquired abnormalities or cochlear nerve anomalies but also to detect temporal bone abnormalities or variations that may alter surgical approach. Preoperative evaluation of cochleovestibular anatomy is an important component of the cochlear implant evaluation. The objective of the study was high resolution computerized tomography (HRCT) assessment of congenital ear anomalies before cochlear implantation.</p><p class="abstract"><strong>Methods:</strong> This prospective study was conducted in the Department of Radio diagnosis and Imaging, GMC, Srinagar. 24 children in the age group of 1 to 12 years with unidentified causes of bilateral SNHL were subjected to HRCT over a period of 7 months from January to July 2019.  </p><p class="abstract"><strong>Results:</strong> Eighteen patients had normal radiological scans and 6 had congenital anomalies. We had one each case of common cavity, bilateral labrynthine aplasia, incomplete partition type 1, Mondini’s deformity with dilated vestibular duct, Internal auditory canal stenosis and bilateral large vestibular aqueduct. Out of 18 patients without congenital anomaly, two had Korner’s septum and giant jugular bulb which were important for operating surgeon.</p><p><strong>Conclusions:</strong> HRCT temporal bone is superior at identifying the bony labyrinth, including enlarged vestibular aqueduct and caliber of internal auditory canal. HRCT temporal bone should be supplemented by magnetic resonance imaging especially for cochlear nerve assessment. It is the initial imaging modality of choice for assessment of congenital SNHL. </p>

scholarly journals A variant of Goldenhar syndrome

2017 ◽  
Vol 4 (3) ◽  
pp. 1115
Author(s):  
Akanksha Jaiswal ◽  
Thumjaa Annamalai ◽  
Nirupama M ◽  
Shafath Ahmed M ◽  
Ramya V
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Sensorineural Hearing Loss ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Cardiac Anomaly ◽  
Goldenhar Syndrome ◽  
Renal Anomaly ◽  
Side Face ◽  
The Right

We report a case of 10 months old child with a variant of Goldenhar syndrome in the form of microtia of right ear, microsomia of the right-side face, right facial nerve palsy with cardiac anomaly, renal anomaly and sensorineural hearing loss on the right side which were rare associations prompted to report this case.

scholarly journals Facial nerve palsy as the presenting feature of metastatic prostatic cancer in the temporal bone

2020 ◽  
Vol 6 (1) ◽  
pp. 1-5
Author(s):  
Daichi Fujii ◽  
Hikari Shimoda ◽  
Natsumi Uehara ◽  
Takeshi Fujita ◽  
Masanori Teshima ◽  
...  
Keyword(s):  
Facial Nerve ◽  
Temporal Bone ◽  
Prostatic Cancer ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Metastatic Prostatic Cancer

scholarly journals Bilateral Temporal Bone Fractures with Bilateral Facial Nerve Palsy

2016 ◽  
Vol 13 (03) ◽  
pp. 168-170
Author(s):  
Kanjully Sabarigirish ◽  
Sanjeev Saxena ◽  
Himanshu Swami ◽  
Angshuman Dutta ◽  
Lohith BR
Keyword(s):  
Facial Nerve ◽  
Temporal Bone ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Bone Fractures
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