Vascular ring and sling in a fetus who developed esophageal and airway compression after birth

2020 ◽  
Vol 37 (12) ◽  
pp. 2152-2154
Author(s):  
Shui‐hua Yang ◽  
Gui‐dan He ◽  
Meng‐feng Liang ◽  
Gui‐chan Qin ◽  
Yu‐lan Pang ◽  
...  
Keyword(s):  
Vascular Ring ◽  
Airway Compression

scholarly journals Bilateral Arterial Ducts Causing Airway Compression by a Vascular Ring

2018 ◽  
Vol 105 (2) ◽  
pp. e89
Author(s):  
Julia Langenbach ◽  
Brigitte Stiller ◽  
Johannes Kroll ◽  
Jochen Grohmann
Keyword(s):  
Vascular Ring ◽  
Airway Compression

Cardiac evaluation of a child with stridor

2020 ◽  
pp. 237-246
Author(s):  
Louise Morrison ◽  
Brian A McCrossan
Keyword(s):  
Aortic Arch ◽  
Subclavian Artery ◽  
Vascular Malformations ◽  
Vascular Ring ◽  
Diagnostic Challenge ◽  
Cross Sectional ◽  
Airway Compression ◽  
Delay In Diagnosis ◽  
Atrioventricular Valve Regurgitation ◽  
Cardiac Evaluation

This is the case of a 6-month-old boy who is diagnosed with, and treated for, a vascular ring, following several admissions to paediatric intensive care with difficult respiratory symptoms and ongoing failure to thrive. This case highlights the diagnostic challenge presented by these patients. Cardiovascular causes of paediatric airway compression are often under-recognized, with consequent delay in diagnosis. Although they are much less common than other causes of stridor, such as laryngomalacia or other tracheo-bronchial anomalies, chronic airway compression in childhood from vascular malformations carries significant morbidity and mortality. It is readily treatable and should not be overlooked. A high index of suspicion for mechanical compression should be maintained in small children with recurrent obstructive respiratory signs and symptoms or the older child presenting with dysphagia. The most prevalent vascular anomalies resulting in airway compression are a double aortic arch, right aortic arch with an aberrant left subclavian artery, innominate artery compression, left aortic arch with an aberrant right subclavian artery (rarely), and pulmonary artery sling. Rarely, complex congenital heart disease, itself leading to dilatation of the cardiac structures, may precipitate airway compromise, as in tetralogy of Fallot with an absent pulmonary valve syndrome or conditions with significant atrioventricular valve regurgitation causing left atrial enlargement. A dilated ascending aorta may compress the trachea, producing similar symptoms likewise with a cervical aortic arch with an aberrant sublclavian artery and ipsilateral ligamentum arteriosus. Such cases require a comprehensive diagnostic workup. Investigations include plain chest X-ray, echocardiogram, direct microlaryngoscopy and bronchoscopy, and CT angiography or cardiac MRI. A normal laryngoscopic examination should warrant further investigation in the presence of ongoing symptoms. An appreciation of aortic arch embryology is important in interpreting echocardiography and cross-sectional imaging in relation to the role of airway compression. Management often necessitates multidisciplinary collaboration among specialties, including ear, nose, and throat (ENT) specialists, paediatric cardiologists, respiratory physicians, intensivists, and cardiothoracic surgeons. Definitive treatment depends on the underlying pathology but usually involves surgical decompression or aortopexy. A proportion of patients will continue to exhibit symptoms following surgical release, due to ongoing weakness of the airway, and in severe cases may require ongoing respiratory support.

Airway Compression by a Right Aortic Arch in the Absence of a Vascular Ring

CHEST Journal ◽  
1984 ◽  
Vol 85 (5) ◽  
pp. 703-705 ◽  
Author(s):  
Samuel S. Gidding ◽  
Robert H. Beekman ◽  
Edward Lebowitz ◽  
John Wesley ◽  
Arnold Coran ◽  
...  
Keyword(s):  
Aortic Arch ◽  
Vascular Ring ◽  
Right Aortic Arch ◽  
Airway Compression

scholarly journals Airway Compression by a Right Aortic Arch in the Absence of a Vascular Ring

2019 ◽  
Vol 10 (1) ◽  
pp. 103-104 ◽  
Author(s):  
Salvatore Agati ◽  
Carlos Guerra Sousa ◽  
Felice Davide Calvaruso ◽  
Giuseppe Ferro ◽  
Rosanna Zanai ◽  
...  
Keyword(s):  
Aortic Arch ◽  
Vascular Ring ◽  
Right Aortic Arch ◽  
Airway Compression

Vascular ring surgery – can we do better?

2020 ◽  
Vol 41 (Supplement_2) ◽  
Author(s):  
G Amir ◽  
N Soffair ◽  
G Frenkel ◽  
E Bruckheimer ◽  
E Nachum ◽  
...  
Keyword(s):  
Aortic Arch ◽  
Respiratory Symptoms ◽  
Ductus Arteriosus ◽  
Vascular Ring ◽  
Symptomatic Relief ◽  
Mirror Image ◽  
Vascular Rings ◽  
Number Of Patients ◽  
Age At Surgery

Abstract Background Vascular anomalies of the Aortic arch can cause respiratory symptoms in children due to tracheal compression. Treatment consists of division of the vascular rings, nevertheless data regarding mid- term results is scarce. The purpose of this study was to evaluate clinical results of vascular ring surgery. Methods Between2007–2014, 85 children underwent vascular ring surgery. 51 had Double Aortic Arch (DAA, 60%), 31 Right Arch with Aberrant Subclavian Artery (RAA & ALSA, 36.5%) and 3 had RAA, mirror image branching & left ductus arteriosus (3.5%). Mean age and weight at operation were 12.4±13months and 8.6±4.1 kg respectively. Mid-term follow-up included clinical follow up by a pulmonologist (38 patients, 44.7%) and a telephone questionnaire (71 patients, 83%) performed 57±25.7 months after surgery. Results In most patients, symptomatic relief occurred in less than 6 months (table 1). Mid –term follow up revealed that although most parents described a significant improvement in their child's respiratory symptoms (95%), a significant number of patients described some residual respiratory symptoms (table 2). We did not find any significant association between age at surgery (under 6 month), or vascular ring anatomy (DAA vs. RAA&ASA) and the presence of residual symptoms at follow up Conclusions Surgical division of vascular rings results in a significant clinical improvement within one year, nevertheless many patients remain symptomatic to some degree. We found no association between the age at surgery or anatomic variant to the presence of symptoms in mid- term follow up. Further evaluation whether a more aggressive surgical approach is warranted in order to decrease the incidence long-term symptoms. Funding Acknowledgement Type of funding source: None

VASCULAR RING ANOMALIES ASSOCIATED WITH PERSISTENT RIGHT ARCH

1970 ◽  
Vol 46 (10) ◽  
pp. 513-514
Author(s):  
M. M. BRYDEN
Keyword(s):  
Vascular Ring

Situs Inversus Totalis and Corrected Transposition of the Great Arteries {I,D,D} in Association with a Previously Unreported Vascular Ring

2001 ◽  
Vol 22 (4) ◽  
pp. 338-342 ◽  
Author(s):  
B. Feingold ◽  
B. O'Sullivan ◽  
P. del Nido ◽  
P. Pollack
Keyword(s):  
Situs Inversus ◽  
Vascular Ring ◽  
Situs Inversus Totalis ◽  
Corrected Transposition

A vascular ring variant: an unusual case of vocal cord palsy due to an anomalous left carotid artery arising from a retrotracheal arch of the aorta

2006 ◽  
Vol 79 (945) ◽  
pp. e81-e83 ◽  
Author(s):  
A R Joshi ◽  
A Garg ◽  
B Vhanmane ◽  
S Merchant ◽  
N Nerurkar
Keyword(s):  
Carotid Artery ◽  
Vocal Cord ◽  
Unusual Case ◽  
Vascular Ring ◽  
Vocal Cord Palsy ◽  
Left Carotid Artery ◽  
Arch Of The Aorta
Sign in / Sign up

Export Citation Format

Share Document