A case of variant parachute mitral valve associated with mitral annular disjunction arrhythmic syndrome

2021 ◽  
Author(s):  
Ishita Datta ◽  
John Dawdy ◽  
Luis Afonso
1969 ◽  
Vol 77 (6) ◽  
pp. 809-813 ◽  
Author(s):  
Allan L. Simon ◽  
William F. Friedman ◽  
William C. Roberts

Circulation ◽  
2020 ◽  
Vol 142 (Suppl_3) ◽  
Author(s):  
uzoma obiaka ◽  
Anna Chow ◽  
Jen Lie Yau ◽  
Valeria Matto Morina ◽  
Shubhika Srivastava

Background: The incidence of congenital mitral valve disease is 0.4%; Double Orifice Mitral Valve (DOMV) and Parachute Mitral Valve (PMV) are two morphologic pathologies that may result in mitral valve dysfunction. The objectives of this study are 1) To describe valve function and progression and 2) To define factors contributing to disease progression. Methods: Retrospective database review. Fyler codes for DOMV, PMV and text search was performed. Echocardiographic images, echo reports, and chart review were used to identify mitral regurgitation (MR), mitral stenosis (MS), morphology, and associated lesions. Results: 39 patients with DOMV and 76 patients with PMV were identified. In the DOMV cohort, 51% were male, median age at diagnosis was 0.17 years (IQR 0.01, 3.88); median follow-up of 5.92 years (IQR 0.46, 10.22). In the PMV cohort, 44% were male, median age at diagnosis at was 0.01 years (IQR 0, 0.34); median follow-up of 2.56 years (IQR 0.25, 9.55). 41% of DOMV and 23% of patients with PMV had normal valve function at initial visit. DOMV was associated with MR (p=0.04), and PMV with MS (p<0.0001). 23% of patients in the PMV cohort had progressive MS compared to 5% of patients in the DOMV cohort (p<0.0001). There was no significant difference in MR progression between both groups (p=0.02). Papillary muscle (PM) morphology was evaluated in 37 (excluding canals) of 76 patients in the PMV cohort. 5 had true PMV (single PM), 32 had variant PMV with two PM groups of which 62.5% had dominant posterior medial PM. 67% of those with posterior medial PM dominance had progressive MS irrespective of association with Shone’s complex. The anterolateral PM muscle group dominant PMV were not associated with Shone’s complex and progressive MS. Conclusion: DOMV are more likely to have MR while PMV are more likely to have MS. DOMV has non progressive MR and MS. Posterior medial PM dominance in PMV is more likely to have progressive MS.


2010 ◽  
Vol 8 (4) ◽  
pp. 131-132
Author(s):  
Tetsushi Yamamoto ◽  
Tetsuari Onishi ◽  
Alaa Marbrouk Salem Omar ◽  
Kazuko Norisada ◽  
Kazuhiro Tatsumi ◽  
...  

Author(s):  
Hakimeh Sadeghian ◽  
Zahra Savand-Roomi

1997 ◽  
Vol 5 (4) ◽  
pp. 247-249
Author(s):  
Fatih İslamoğlu ◽  
Yüksel Atay ◽  
İlker Alat ◽  
Osman Saribülbül ◽  
E Alp Alayunt

A 3-year-old female presented with double-outlet right ventricle associated with supravalvular mitral ring, parachute mitral valve, left persistent superior vena cava, and atrial septal defect. The supra-annular mitral valve ring was resected. Only one papillary muscle of the mitral valve could be detected and this was minimally divided to achieve adequate valve opening. An intraventricular tunnel repair technique using a polytetrafluoroethylene patch was carried out to repair the double-outlet right ventricle, which had a subaortic ventricular septal defect. The follow-up results at 2 years are excellent.


2004 ◽  
Vol 13 (8) ◽  
pp. 50-51
Author(s):  
M.V. Schaverien ◽  
R.M. Freedom ◽  
B.W. McCrindle

2016 ◽  
Vol 68 ◽  
pp. S126-S130 ◽  
Author(s):  
Jagdish C. Mohan ◽  
Madhu Shukla ◽  
Vishwas Mohan ◽  
Arvind Sethi

2016 ◽  
Vol 25 ◽  
pp. S218
Author(s):  
G. Gan ◽  
A. Bhat ◽  
F. Fernandez ◽  
S. Liang ◽  
B. Changsiri ◽  
...  

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