SERUM ALPHA-FETOPROTEIN LEVELS IN EXTRAHEPATIC BILIARY ATRESIA, IDIOPATHIC NEONATAL HEPATITIS AND ALPHA-1-ANTITRYPSIN DEFICIENCY (PiZ)

1976 ◽  
Vol 65 (4) ◽  
pp. 623-629 ◽  
Author(s):  
D. I. JOHNSTON ◽  
A. P. MOWAT ◽  
HILARY ORR ◽  
J. KOHN
Keyword(s):  
Biliary Atresia ◽  
Alpha Fetoprotein ◽  
Neonatal Hepatitis ◽  
Extrahepatic Biliary Atresia ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Serum Alpha Fetoprotein ◽  
Alpha 1 Antitrypsin ◽  
Idiopathic Neonatal Hepatitis

Idiopathic Neonatal Hepatitis in One DNA Fingerprint Identical Twin

PEDIATRICS ◽  
1992 ◽  
Vol 89 (2) ◽  
pp. 329-330
Author(s):  
PIETRO VAJRO ◽  
ANGIOLA FONTANELLA ◽  
EMILIA VUTTARIELLO ◽  
ANNA DE VINCENZO ◽  
GIULIANA FORTUNATO
Keyword(s):  
Biliary Atresia ◽  
Hepatobiliary Disease ◽  
Identical Twin ◽  
Dna Fingerprint ◽  
Neonatal Hepatitis ◽  
Neonatal Cholestasis ◽  
Injury Site ◽  
Extrahepatic Biliary Atresia ◽  
Dizygotic Twins ◽  
Idiopathic Neonatal Hepatitis

For the practicing pediatrician, the most commonly encountered causes of neonatal cholestasis are idiopathic neonatal hepatitis (INH) and extrahepatic biliary atresia (EHBA). However, despite extensive research, little improvement in our understanding of the etiology of INH and EHBA has occurred.1 It has been proposed that both of them may be part of a continuum of hepatobiliary disease caused by a common insult with a different predominant injury site.2 In this respect, it is interesting that, up to the present, several cases of discordance for EHBA in twins of various zygosity have been reported,3-8 whereas no data are available about either concordance or discordance for INH both in monozygotic and dizygotic twins.

DIFFERENTIATION BETWEEN NEONATAL HEPATITIS AND BILIARY ATRESIA BY MEASURING SERUM-ALPHA-FETOPROTEIN

The Lancet ◽  
1974 ◽  
Vol 303 (7854) ◽  
pp. 373-375 ◽  
Author(s):  
PaulM. Zeltzer ◽  
EricW. Fonkalsrud ◽  
RobertC. Neerhout ◽  
E.Richard Stiehm
Keyword(s):  
Biliary Atresia ◽  
Alpha Fetoprotein ◽  
Neonatal Hepatitis ◽  
Serum Alpha Fetoprotein

DIFFERENTIATION BETWEEN NEONATAL HEPATITIS AND BILIARY ATRESIA BY MEASURING SERUM-ALPHA-FETOPROTEIN

The Lancet ◽  
1974 ◽  
Vol 304 (7881) ◽  
pp. 650-651 ◽  
Author(s):  
C.A. Kattamis ◽  
Sophia Laskari ◽  
N.S. Matsaniotis
Keyword(s):  
Biliary Atresia ◽  
Alpha Fetoprotein ◽  
Neonatal Hepatitis ◽  
Serum Alpha Fetoprotein

scholarly journals Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia

2017 ◽  
Vol 2017 ◽  
pp. 1-5
Author(s):  
Andrew W. Wang ◽  
Kimberly Newton ◽  
Karen Kling
Keyword(s):  
Liver Function ◽  
Biliary Atresia ◽  
Successful Outcome ◽  
Dual Pathology ◽  
Native Liver ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin ◽  
Prompt Diagnosis ◽  
Rare Instance

We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function.

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