A Skeletalized Representation of the Total Cavopulmonary Connection

2007 ◽  
Author(s):  
Resmi Krishnankuttyrema ◽  
Lakshmi Prasad Dasi ◽  
Kerem Pekkan ◽  
Kartik Sundareswaran ◽  
Hiroumi D. Kitajima ◽  
...  
Keyword(s):  
Congenital Heart ◽  
Single Ventricle ◽  
Venous Return ◽  
Right Heart ◽  
Live Births ◽  
Correction Technique ◽  
The Usa ◽  
Systemic Venous Return ◽  
The Right ◽  
Cavopulmonary Connection

Single ventricle congenital heart problems are reported for 2 out of every 1000 live births in the USA. In these cases, mixing of oxygenated and deoxygenated blood occurs in the heart causing severe cyanosis. The Fontan repair is a 3-stage palliative surgical correction technique performed during infancy. Its aim is to restore normal oxygen saturation by directly connecting the systemic venous return to the lungs and bypassing the right heart [1].

a study of the fontan circulation and ventricular energetics based on a model

2004 ◽  
Vol 14 (S3) ◽  
pp. 11-19 ◽  
Author(s):  
andrea ripoli ◽  
sergio berti ◽  
mattia glauber ◽  
vittorio vanini ◽  
vincenzo stefano luisi ◽  
...  
Keyword(s):  
Single Ventricle ◽  
Volume Overload ◽  
Systemic Circulation ◽  
Fontan Circulation ◽  
Total Cavopulmonary Connection ◽  
Right Heart ◽  
Cavopulmonary Anastomosis ◽  
Bidirectional Cavopulmonary Anastomosis ◽  
The Right ◽  
Cavopulmonary Connection

patients with congenitally malformed hearts characterised by a functionally single ventricle are currently treated using several procedures that bypass the right heart, such as the fontan and hemi-fontan operations, the bidirectional cavopulmonary anastomosis, and the total cavopulmonary connection. all these options are based on the procedures introduced for palliative correction of tricuspid atresia by fontan and baudet in 1971. introduced with the purpose of reducing the pre-operative volume overload, the surgical task mainly consists of separating the pulmonary from the systemic circulation. irrespective of the specific operation performed, we can call the resulting circulation the fontan circulation.

scholarly journals Cor triatriatum dextrum: A rare congenital cardiac abnormality

2016 ◽  
Vol 31 (1) ◽  
pp. 37-40
Author(s):  
MS Haque ◽  
MA Saleh ◽  
SR Kabir ◽  
A Muhammad ◽  
ANMM Islam ◽  
...  
Keyword(s):  
Rare Case ◽  
Congenital Heart ◽  
Septal Defect ◽  
Incidental Finding ◽  
Right Heart Failure ◽  
Accurate Diagnosis ◽  
Cor Triatriatum ◽  
Right Heart ◽  
2D Echocardiography ◽  
The Right

Cor triatriatum dextrum is an exceptionally rare congenital heart disease, in which the right atrium is partitioned into two chambers by a membrane to form a triatrial heart. It is caused by persistence of the right valve of sinus venosus. The aim of presenting this case is to develop awareness regarding cor triatriatum dextrum , though a rare case, can be present and may contribute to right heart failure and 2D-echocardiography is an important tool in making early and accurate diagnosis. We are reporting a case of an elderly Bangladeshi male presented with the features of mitral stenosis with pulmonary hypertension with CCF with respiratory tract infection, where cor triatriatum dextrum with an atrial septal defect was an incidental finding on routine echocardiographic assessment.Bangladesh Heart Journal 2016; 31(1) : 37-40

Transposition of the great arteries and sinus venosus defect with partially anomalous pulmonary venous return: physiological and anatomic considerations

2014 ◽  
Vol 25 (4) ◽  
pp. 787-789
Author(s):  
Vijayakumar Raju ◽  
Rahul Rathod ◽  
Luis G. Quinonez ◽  
Christopher W. Baird
Keyword(s):  
Congenital Heart Defect ◽  
Congenital Heart ◽  
Venous Return ◽  
Sinus Venosus ◽  
Live Births ◽  
Heart Defect ◽  
Anomalous Pulmonary Venous Return ◽  
Sinus Venosus Defect ◽  
Heart Lesions

AbstractTransposition of the great arteries is a common congenital heart defect causing cyanosis in neonates, occurring in 0.2 per 1000 live births. It has been reported to occur with other associated congenital heart lesions. However, its association with a superior sinus venosus defect and partially anomalous pulmonary venous return has not been reported. We present a neonate with transposition of the great arteries, superior sinus venosus defect with partially anomalous pulmonary venous return that underwent successful complete neonatal repair, and discuss important physiological and anatomic considerations.

The Right Heart in Adults With Congenital Heart Disease

2010 ◽  
Vol 63 (9) ◽  
pp. 1070-1086 ◽  
Author(s):  
Rafael Alonso-González ◽  
Konstantinos Dimopoulos ◽  
SiewYen Ho ◽  
José M. Oliver ◽  
Michael A. Gatzoulis
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Right Heart ◽  
The Right

Superior Vena Cava Banding to Facilitate Unilateral Bidirectional Glenn Operation in Patients With Single Ventricle Heart Disease and Bilateral Superior Caval Veins

2016 ◽  
Vol 8 (2) ◽  
pp. 215-219 ◽  
Author(s):  
Matthew C. Schwartz ◽  
David Nykanen ◽  
William DeCampli ◽  
Kamal Pourmoghadam
Keyword(s):  
Heart Disease ◽  
Congenital Heart ◽  
Single Ventricle ◽  
Superior Vena ◽  
Vena Cava ◽  
Novel Technique ◽  
Bidirectional Glenn ◽  
Increased Risk ◽  
Bridging Vein ◽  
Cavopulmonary Connection

Staged palliation to achieve a total cavopulmonary connection is a common treatment strategy in patients with single ventricle congenital heart disease. Patients with bilateral superior caval veins (bilateral SVC) often require the creation of bilateral superior cavopulmonary connections as part of the staged palliation, and these patients are at increased risk of morbidity. We describe a novel technique used in two patients with bilateral SVC and very small (1-2 mm) bridging vein that encouraged bridging vein growth and facilitated creation of a unilateral superior cavopulmonary connection.

scholarly journals Genetic Analysis of Right Heart Structure and Function in 40,000 People

2021 ◽  
Author(s):  
James P. Pirruccello ◽  
Paolo Di Achille ◽  
Victor Nauffal ◽  
Mahan Nekoui ◽  
Samuel N. Friedman ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Deep Learning ◽  
Right Ventricular ◽  
Congenital Heart ◽  
Left Ventricular ◽  
Structure And Function ◽  
Right Heart ◽  
Heart Chamber ◽  
The Right ◽  
And Function

The heart evolved hundreds of millions of years ago. During mammalian evolution, the cardiovascular system developed with complete separation between pulmonary and systemic circulations incorporated into a single pump with chambers dedicated to each circulation. A lower pressure right heart chamber supplies deoxygenated blood to the lungs, while a high pressure left heart chamber supplies oxygenated blood to the rest of the body. Due to the complexity of morphogenic cardiac looping and septation required to form these two chambers, congenital heart diseases often involve maldevelopment of the evolutionarily recent right heart chamber. Additionally, some diseases predominantly affect structures of the right heart, including arrhythmogenic right ventricular cardiomyopathy (ARVC) and pulmonary hypertension. To gain insight into right heart structure and function, we fine-tuned deep learning models to recognize the right atrium, the right ventricle, and the pulmonary artery, and then used those models to measure right heart structures in over 40,000 individuals from the UK Biobank with magnetic resonance imaging. We found associations between these measurements and clinical disease including pulmonary hypertension and dilated cardiomyopathy. We then conducted genome-wide association studies, identifying 104 distinct loci associated with at least one right heart measurement. Several of these loci were found near genes previously linked with congenital heart disease, such as NKX2-5, TBX3, WNT9B, and GATA4. We also observed interesting commonalities and differences in association patterns at genetic loci linked with both right and left ventricular measurements. Finally, we found that a polygenic predictor of right ventricular end systolic volume was associated with incident dilated cardiomyopathy (HR 1.28 per standard deviation; P = 2.4E-10), and remained a significant predictor of disease even after accounting for a left ventricular polygenic score. Harnessing deep learning to perform large-scale cardiac phenotyping, our results yield insights into the genetic and clinical determinants of right heart structure and function.

Quantitation of right-to-left shunting by double indicator and oxygen techniques

1976 ◽  
Vol 41 (3) ◽  
pp. 409-415 ◽  
Author(s):  
D. P. Copley ◽  
R. A. Klocke ◽  
F. J. Klocke
Keyword(s):  
Cardiac Output ◽  
Sulfur Hexafluoride ◽  
Venous Return ◽  
Right Heart ◽  
Indocyanine Green Dye ◽  
Arterial Blood ◽  
Vascular Space ◽  
Systemic Venous Return ◽  
Low Solubility ◽  
Right Heart Bypass

An improved double indicator technique for quantitating right-to-left shunting has been validated in a canine right-heart bypass shunt model and compared to standard O2 shunt measurements in the same preparation. A bolus of dissolved sulfur hexafluoride (SF6) and indocyanine green dye (ICG) is injected into systemic venous return and a single, time-averaged arterial blood sample is collected during the initial circulation of indicators. Because of its low solubility, SF6 is eliminated essentially quantitatively from blood traversing gas-filled alveoli; correction for volatile tracer in arterial blood derived from nonshunt pathways in therefore unnecessary. ICG remains confined to the vascular space and SF6 is not lost in shunt pathways. Ratios of SF6-ICG shunt to directly measured shunt averaged 0.99 +/- 0.27 (SD) in 55 comparisons of shunts ranging from 2 to 25% of cardiac output; differences between actual and measured shunt averaged 0.5 +/- 2.9% of cardiac output. Simultaneously determined ratios of O2 shunt to directly measured shunt averaged 0.98 +/- 0.48 in 34 comparisons; differences between actual and measured shunt were 0.7 +/- 3.4% of cardiac output.

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