scholarly journals Patient with Crouzon Syndrome Treated with Modified Le Fort III Osteotomy without Previous Orthodontic Treatment: Case Report and a Review of the Literature

2020 ◽  
Vol 2020 ◽  
pp. 1-9
Author(s):  
Farnoosh Mohammadi ◽  
Afrooz Javanmard ◽  
Hamid Mojtahedi

Crouzon syndrome is the most common type of craniofacial dysostosis anomaly which presents a great challenge for clinicians since birth. Multiple synostoses in the sutures of the cranial base in this syndrome result in the hypoplasia of the midface, shallow orbits, a short nasal dorsum, maxillary hypoplasia, and, in severe cases, obstruction of the upper airways. Apart from esthetic and functional problems, these patients suffer from various psychological problems which mandate correction of midface deformities at younger ages. The aim of this report is to describe the case of a 26-year-old female patient with Crouzon syndrome displaying severe midface hypoplasia and proptosis with no history of orthodontic treatment, who was treated with modified Le Fort III osteotomy with a coronal and intraoral approach without periocular incisions.

2016 ◽  
Vol 53 (1) ◽  
pp. 118-125 ◽  
Author(s):  
Firdaus Hariri ◽  
Lim Kwong Cheung ◽  
Zainal Ariff Abdul Rahman ◽  
Vickneswaran Mathaneswaran ◽  
Dharmendra Ganesan

2015 ◽  
Vol 129 (10) ◽  
pp. 1036-1039 ◽  
Author(s):  
E Kyriakidou ◽  
T Howe ◽  
B Veale ◽  
S Atkins

AbstractBackground:Dermoid cysts in the floor of the mouth are relatively uncommon developmental lesions. They are thought to arise in the midline and along the lines of embryonic fusion of the facial processes containing ectodermal tissue.Case report:A 17-year-old female presented with a 3-month history of a growing, progressive swelling in the mouth floor. Clinical examination revealed a rather large symmetrical, soft swelling in the mouth floor, displacing the tongue superiorly. The fast growing nature and size of the lesion raised suspicion of potential compromise to the airway. Surgical excision was therefore performed.Conclusion:Differential diagnosis of cystic lesions in the floor of the mouth is of paramount importance, as the recommended surgical techniques vary depending on the anatomical position of the lesions. The intraoral approach is preferred for those lesions that do not extend beyond the mylohyoid muscle boundaries; this leads to a satisfactory cosmetic and functional outcome.


2013 ◽  
Vol 132 (4) ◽  
pp. 592e-601e ◽  
Author(s):  
E. J. Caterson ◽  
Pradip R. Shetye ◽  
Barry H. Grayson ◽  
Joseph G. McCarthy

2008 ◽  
Vol 37 (9) ◽  
pp. 781-789 ◽  
Author(s):  
E. Nout ◽  
L.L.M. Cesteleyn ◽  
K.G.H. van der Wal ◽  
L.N.A. van Adrichem ◽  
I.M.J. Mathijssen ◽  
...  

2008 ◽  
Vol 45 (3) ◽  
pp. 332-336 ◽  
Author(s):  
Corstiaan C. Breugem ◽  
Kevin Bush ◽  
Donald F. Fitzpatrick

Midface hypoplasia in a 5-year-old boy with Crouzon syndrome was treated using a rigid external distraction device. Seven months prior to this surgery, a bone allograft was used during frontal-orbital bar advancement. Three weeks after the Le Fort III distraction a depression fracture was diagnosed, associated with an intracerebral screw penetration of 3.5 cm. This case report cautions against the use of distraction osteogenesis in patients when previous allografts were used for calvarial reconstruction. We suggest that a preoperative computed tomography scan is mandatory to accurately delineate the location for placement of the pins.


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