Massive Hematuria in Adults with Klippel-Trenaunay Syndrome Associated with Vascular Malformation of the Bladder

2000 ◽  
Vol 64 (4) ◽  
pp. 226-228 ◽  
Author(s):  
Bijan Shekarriz ◽  
Jyoti Upadhyay ◽  
Craig Smith ◽  
Andris Kazmers ◽  
Rene Frontera
Keyword(s):  
Vascular Malformation ◽  
Klippel Trenaunay Syndrome

scholarly journals Klippel–Trénaunay Syndrome – A Very Rare and Interesting Syndrome

2015 ◽  
Vol 9 ◽  
pp. CCRPM.S21645 ◽  
Author(s):  
Deepak Sharma ◽  
Sachin Lamba ◽  
Aakash Pandita ◽  
Sweta Shastri
Keyword(s):  
Soft Tissue ◽  
Vascular Malformation ◽  
Chronic Venous Insufficiency ◽  
Venous Insufficiency ◽  
Varicose Veins ◽  
Lower Limbs ◽  
Port Wine ◽  
Bone Deformity ◽  
Klippel Trenaunay Syndrome

Klippel–Trénaunay syndrome (KTS or KT) is an infrequently seen dermatological syndrome, which is often viewed as a triad of vascular malformation (capillary malformations or port-wine brands), venous varicosity, and soft tissue and/or bony hypertrophy. We report a case of a 12-year-old male who presented to us with the symptoms of varicose plaques over both lower limbs and was diagnosed as a case of KTS. Management is normally conservative and includes stockings for compression of the branches to reduce edema because of chronic venous insufficiency; modern devices that cause on and off pneumatic compression; and rarely, surgical correction of varicose veins with lifelong follow-up. The orthopedic abnormalities are treated with epiphysiodesis in order to prevent (stop) overgrowing of limb and correction of bone deformity.

scholarly journals Klippel Trenaunay Syndrome: a rare case report in a neonate

2016 ◽  
Vol 4 (1) ◽  
pp. 294
Author(s):  
Krishnappa Santosh Kumar ◽  
Nanjappa Mohan Kumar
Keyword(s):  
Case Report ◽  
Soft Tissue ◽  
Vascular Malformation ◽  
Conservative Management ◽  
Rare Case ◽  
Lymphatic Malformation ◽  
Rare Case Report ◽  
Klippel Trenaunay Syndrome ◽  
Prompt Diagnosis

Klippel Trenaunay Syndrome (KTS) is a cutaneous vascular malformation in combination with bone and soft tissue overgrowth, with or without lymphatic malformation. Symptoms appear by birth and approximately 90% of the cases are diagnosed by the age of 12 years. Prompt diagnosis at the earliest and conservative management with regular follow up is crucial in prognosis of KTS.

scholarly journals Conservative management of knee arthropathy in a patient with Klippel Trenaunay syndrome

2020 ◽  
Vol 19 ◽  
Author(s):  
Fanny Rodríguez Santos ◽  
Victoria Loson ◽  
Agustín Coria ◽  
Hugo Martínez
Keyword(s):  
Quality Of Life ◽  
Soft Tissue ◽  
Vascular Malformation ◽  
Multidisciplinary Approach ◽  
Venous Malformations ◽  
Physiotherapy Program ◽  
Associated Conditions ◽  
Klippel Trenaunay Syndrome

Abstract Klippel-Trenaunay syndrome (KTS) is a rare vascular malformation characterized by capillary malformation, venous malformations, and soft tissue or bone hypertrophy that affect the extremities in most cases. Knee or hip arthropathy are common associated conditions and cause serious disability. We present the case of a patient with a diagnosis of KTS and severe knee arthropathy. A 34-year-old man with KTS was referred to our hospital with severe knee arthropathy, with the joint fixed in a 90° position. CT Angiography and MRI of the left leg showed important varicose development of the superficial venous system with intraarticular vessels. After discussion of the case by a multidisciplinary committee, the patient was enrolled on a physiotherapy program and had achieved significant improvements in movement and quality of life at 12-month follow-up. Treatment of KTS is primarily conservative and a multidisciplinary approach is necessary.

How Do the Type and Location of a Vascular Malformation Influence Growth in Klippel-Trénaunay Syndrome?

2011 ◽  
Vol 127 (1) ◽  
pp. 340-346 ◽  
Author(s):  
Emi Funayama ◽  
Satoru Sasaki ◽  
Akihiko Oyama ◽  
Hiroshi Furukawa ◽  
Toshihiko Hayashi ◽  
...  
Keyword(s):  
Vascular Malformation ◽  
Klippel Trenaunay Syndrome

scholarly journals INVERSE KLIPPEL-TRENAUNAY SYNDROME

2020 ◽  
Vol 38 ◽  
Author(s):  
Mariana Franco Ferraz Santino ◽  
Maria João Paiva Lopes
Keyword(s):  
Vascular Malformation ◽  
Rare Case ◽  
Subcutaneous Tissue ◽  
Left Thigh ◽  
Case Description ◽  
Venous Malformations ◽  
Proper Understanding ◽  
Molecular Studies ◽  
Subcutaneous Tissues ◽  
Klippel Trenaunay Syndrome

ABSTRACT Objective: To report a rare case of inverse Kipplel-Trenaunay. Case description: A 16-year-old girl with a grayish-depressed plaque on her left thigh. Angioresonance showed a vascular malformation affecting the skin and subcutaneous tissue. Comments: Inverse Klippel-Trenaunay is a Klippel-Trenaunay syndrome variation in which there are capillary and venous malformations associated to hypotrophy or shortening of the affected limb. Modifications on the limb’s length or width result from alterations in bones, muscles, or subcutaneous tissues. It has few described cases. Further clinical and molecular studies must be performed for a proper understanding.

Case report: Jejunal vascular malformation in klippel-trenaunay syndrome

1991 ◽  
Vol 44 (2) ◽  
pp. 134-136 ◽  
Author(s):  
R. Brown ◽  
S.K. Ohri ◽  
P. Ghosh ◽  
J. Jackson ◽  
J. Spencer ◽  
...  
Keyword(s):  
Case Report ◽  
Vascular Malformation ◽  
Klippel Trenaunay Syndrome
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