Performance with an Auditory Brainstem Implant and Contralateral Cochlear Implant in Pediatric Patients

2018 ◽  
Vol 23 (4) ◽  
pp. 216-221 ◽  
Author(s):  
David R. Friedmann ◽  
Leena Asfour ◽  
William H. Shapiro ◽  
J. Thomas Roland Jr. ◽  
Susan B. Waltzman

Objective: To assess bimodal auditory performance in children with a cochlear implant (CI) and contralateral auditory brainstem implant (ABI). Methods: This is a retrospective case review performed at a tertiary referral center. Four patients with cochlear nerve deficiency initially underwent cochlear implantation but were not benefiting from their devices and underwent ABI in the contralateral ear. The main outcome measures included age-appropriate speech perception and production assessments. Results: Three subjects performed better on their auditory perception assessments using both of their devices than with either device alone. One subject had only preliminary outcomes, but subjectively performed best with both devices. Conclusions: We observed continued improvement in CI performance over time, even if no benefit was evident before the decision for ABI. This could suggest that ABI and CI have a synergistic effect, or it could simply be the adaptive ability of the developing brain to utilize the signals coming from these devices. There is preliminary evidence to support choosing the ear contralateral to the CI for an ABI in a pediatric patient with bilateral cochlear nerve deficiency.

2019 ◽  
Vol 80 (01) ◽  
pp. e1-e9 ◽  
Author(s):  
Anand Kasbekar ◽  
Yu Chuen Tam ◽  
Robert Carlyon ◽  
John Deeks ◽  
Neil Donnelly ◽  
...  

Objectives A decision on whether to insert a cochlear implant can be made in neurofibromatosis 2 (NF2) if there is objective evidence of cochlear nerve (CN) function post vestibular schwannoma (VS) excision. We aimed to develop intraoperative CN monitoring to help in this decision. Design We describe the intraoperative monitoring of a patient with NF2 and our stimulating and recording set up. A novel test electrode is used to stimulate the CN electrically. Setting This study was set at a tertiary referral center for skull base pathology. Main outcome measure Preserved auditory brainstem responses leading to cochlear implantation. Results Electrical auditory brainstem response (EABR) waveforms will be displayed from different stages of the operation. A cochlear implant was inserted at the same sitting based on the EABR. Conclusion Electrically evoked CN monitoring can provide objective evidence of CN function after VS excision and aid in the decision-making process of hearing rehabilitation in patients who will be rendered deaf.


Skull Base ◽  
2008 ◽  
Vol 18 (4) ◽  
pp. 281-287 ◽  
Author(s):  
Enrico Piccirillo ◽  
Maurizio Guida ◽  
Sean Flanagan ◽  
Lorenzo Lauda ◽  
Paolo Fois ◽  
...  

2015 ◽  
Vol 154 (2) ◽  
pp. 335-342
Author(s):  
Giacomo Colletti ◽  
Marco Mandalà ◽  
Liliana Colletti ◽  
Vittorio Colletti

2012 ◽  
Vol 13 (1) ◽  
pp. 16-25 ◽  
Author(s):  
Peter Roland ◽  
Kathryn Henion ◽  
Timothy Booth ◽  
Julia Dee Campbell ◽  
Anu Sharma

2021 ◽  
pp. 019459982110574
Author(s):  
Kaitian Chen ◽  
Bixue Huang ◽  
Jincangjian Sun ◽  
Yue Liang ◽  
Guanxia Xiong

Objective Mutations in the cadherin 23 gene ( CDH23) have been reported to cause cochlear damage, but few studies have investigated the auditory and speech outcome of patients after cochlear implantation. Here, we describe the genetic, auditory, and postoperative outcomes of patients with CDH23 mutations who received cochlear implants. Study Design Retrospective case review. Setting Tertiary referral center. Methods Targeted deafness-related gene panels were sequenced in Chinese families with profound sensorineural hearing loss. The clinical features of subjects carrying potentially pathogenic CDH23 mutations were analyzed. Results Between 2017 and 2019, we identified 5 children with prelinguistically profound hearing loss at our center who harbored 6 variants of CDH23 that segregated with the disease. Of these, 4 variants were novel (c.2591G>T, c.4785G>C, c.5765A>G, and c.9280_9281insTT). All affected individuals had a loss of outer hair cell function, with an average residual hearing level of 3 to 10 dB SPL. Cochlear implantations were arranged for the patients at 11 to 36 months of age. All children made gains in their hearing, language, and speech performances 14 to 120 months after surgery. Their auditory outcomes improved during follow-up intervals. Conclusion This study revealed that children with congenital cochlear defects caused by CDH23 variants can acquire an acceptable auditory and speech outcome after cochlear implantation. Early genetic detection and prenatal counseling for rare deafness genes such as CDH23 remain a priority for the future.


2014 ◽  
Vol 151 (1_suppl) ◽  
pp. P93-P93
Author(s):  
Giacomo Colletti ◽  
Marco Mandala ◽  
Liliana Colletti ◽  
Vittorio Colletti

2004 ◽  
Vol 9 (4) ◽  
pp. 247-255 ◽  
Author(s):  
V. Colletti ◽  
M. Carner ◽  
V. Miorelli ◽  
L. Colletti ◽  
M. Guida ◽  
...  

2011 ◽  
Vol 121 (9) ◽  
pp. 1979-1988 ◽  
Author(s):  
Craig A. Buchman ◽  
Holly F. B. Teagle ◽  
Patricia A. Roush ◽  
Lisa R. Park ◽  
Debora Hatch ◽  
...  

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