Percutaneous Lymphatic Embolization of Abnormal Pulmonary Lymphatic Flow as Treatment of Plastic Bronchitis in Patients With Congenital Heart Disease

Circulation ◽  
2016 ◽  
Vol 133 (12) ◽  
pp. 1160-1170 ◽  
Author(s):  
Yoav Dori ◽  
Marc S. Keller ◽  
Jonathan J. Rome ◽  
Matthew J. Gillespie ◽  
Andrew C. Glatz ◽  
...  
2018 ◽  
Vol 2018 ◽  
pp. 1-5
Author(s):  
Sheila A. Habib ◽  
Robert C. Vasko ◽  
Jack Badawy ◽  
Gregory M. Anstead

Plastic bronchitis is the expectoration of bronchial casts in the mold of the tracheobronchial tree. It is a rare occurrence of unknown etiology that has been primarily described in children with congenital heart disease. In this case report, we present the first reported case of plastic bronchitis in a patient with pulmonary Kaposi sarcoma and underlying HIV infection.


Author(s):  
Joshua Rezkalla ◽  
Majid Husain ◽  
Ginger Slack ◽  
Sanjay Sinha

Refractory post-operative chylothorax in congenital heart disease is difficult to treat. We present a case of intractable neonatal chylothorax after cardiac surgery due to central lymphatic flow disorder that was treated by creating a lymphovenous anastomosis of the thoracic duct to the left external jugular vein for definitive treatment


2021 ◽  
Vol 10 (19) ◽  
Author(s):  
Bethan A. Lemley ◽  
Dave M. Biko ◽  
Aaron G. Dewitt ◽  
Andrew C. Glatz ◽  
David J. Goldberg ◽  
...  

Background Protein‐losing enteropathy (PLE) is a significant cause of morbidity and mortality in congenital heart disease patients with single ventricle physiology. Intrahepatic dynamic contrast‐enhanced magnetic resonance lymphangiography (IH‐DCMRL) is a novel diagnostic technique that may be useful in characterizing pathologic abdominal lymphatic flow in the congenital heart disease population and in diagnosing PLE. The objective of this study was to characterize differences in IH‐DCMRL findings in patients with single ventricle congenital heart disease with and without PLE. Methods and Results This was a single‐center retrospective study of IH‐DCMRL findings and clinical data in 41 consecutive patients, 20 with PLE and 21 without PLE, with single ventricle physiology referred for lymphatic evaluation. There were 3 distinct duodenal imaging patterns by IH‐DCMRL: (1) enhancement of the duodenal wall with leakage into the lumen, (2) enhancement of the duodenal wall without leakage into the lumen, and (3) no duodenal involvement. Patients with PLE were more likely to have duodenal involvement on IH‐DCMRL than patients without PLE ( P <0.001). Conclusions IH‐DCMRL findings of lymphatic enhancement of the duodenal wall and leakage of lymph into the duodenal lumen are associated with PLE. IH‐DCMRL is a useful new modality for characterizing pathologic abdominal lymphatic flow in PLE and might be useful as a risk‐assessment tool for PLE in at‐risk patients.


Author(s):  
Ignacio Iglesias Serrano ◽  
Mercedes Pérez Lafuente ◽  
Antoni Segarra Medrano ◽  
Antonia Pijuan Domenech ◽  
Dimpna Albert Brotons ◽  
...  

2013 ◽  
Vol 2013 ◽  
pp. 1-8 ◽  
Author(s):  
Rebecca Kunder ◽  
Christian Kunder ◽  
Heather Y. Sun ◽  
Gerald Berry ◽  
Anna Messner ◽  
...  

Plastic bronchitis (PB) is a pathologic condition in which airway casts develop in the tracheobronchial tree causing airway obstruction. There is no standard treatment strategy for this uncommon condition. We report an index patient treated using an emerging multimodal strategy of directly instilled and inhaled tissue plasminogen activator (t-PA) as well as 13 other cases of PB at our institution between 2000 and 2012. The majority of cases (n=8) occurred in patients with congenital heart disease. Clinical presentations, treatments used, histopathology of the casts, and patient outcomes are reviewed. Further discussion is focused on the epidemiology of plastic bronchitis and a systematic approach to the histologic classification of casts. Comorbid conditions identified in this study included congenital heart disease (8), pneumonia (3), and asthma (2). Our institutional prevalence rate was 6.8 per 100,000 patients, and our case fatality rate was 7%.


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