Severe deficiency of cystic fibrosis transmembrane conductance regulator messenger RNA carrying nonsense mutations R553X and W1316X in respiratory epithelial cells of patients with cystic fibrosis.

Nonsense Mutations ◽

Severe Deficiency ◽

Respiratory Epithelial ◽

Role of the cystic fibrosis transmembrane conductance regulator in internalization of Pseudomonas aeruginosa by polarized respiratory epithelial cells

Cellular Microbiology ◽

10.1111/j.1462-5822.2004.00380.x ◽

2004 ◽

Vol 6 (6) ◽

pp. 521-533 ◽

Cited By ~ 27

Author(s):

Katharine E. A. Darling ◽

Ann Dewar ◽

Thomas J. Evans

Keyword(s):

Cystic Fibrosis ◽

Pseudomonas Aeruginosa ◽

Epithelial Cells ◽

Respiratory Epithelial ◽

Human cystic fibrosis transmembrane conductance regulator directed to respiratory epithelial cells of transgenic mice

Nature Genetics ◽

10.1038/ng0992-13 ◽

1992 ◽

Vol 2 (1) ◽

pp. 13-20 ◽

Cited By ~ 61

Author(s):

Jeffrey A. Whitsett ◽

Chitta R. Dey ◽

Barry R. Stripp ◽

Kathryn A. Wikenheiser ◽

Jean C. Clark ◽

...

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Transgenic Mice ◽

Respiratory Epithelial ◽

Pseudomonas aeruginosa–Induced Apoptosis Is Defective in Respiratory Epithelial Cells Expressing Mutant Cystic Fibrosis Transmembrane Conductance Regulator

American Journal of Respiratory Cell and Molecular Biology ◽

10.1165/rcmb.4898 ◽

2003 ◽

Vol 29 (2) ◽

pp. 188-197 ◽

Cited By ~ 86

Author(s):

Carolyn L. Cannon ◽

Michael P. Kowalski ◽

Kimberly S. Stopak ◽

Gerald B. Pier

Keyword(s):

Cystic Fibrosis ◽

Pseudomonas Aeruginosa ◽

Epithelial Cells ◽

Induced Apoptosis ◽

Respiratory Epithelial ◽

Faculty Opinions recommendation of Cystic fibrosis transmembrane conductance regulator is expressed in mucin granules from Calu-3 and primary human airway epithelial cells.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.718017856.793479176 ◽

2013 ◽

Author(s):

Steven M Rowe ◽

Sammeta Vamsee Raju

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Airway Epithelial Cells ◽

Airway Epithelial ◽

Human Airway ◽

Cystic Fibrosis Transmembrane ◽

Human Airway Epithelial Cells

Cellular differentiation is required for cAMP but not Ca(2+)-dependent Cl- secretion in colonic epithelial cells expressing high levels of cystic fibrosis transmembrane conductance regulator.

Journal of Biological Chemistry ◽

10.1016/s0021-9258(18)42804-9 ◽

1992 ◽

Vol 267 (8) ◽

pp. 5575-5583

Author(s):

A.P. Morris ◽

S.A. Cunningham ◽

D.J. Benos ◽

R.A. Frizzell

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Cellular Differentiation ◽

Colonic Epithelial Cells ◽

Cl Secretion ◽

Dysregulation of proteoglycan production by intrahepatic biliary epithelial cells bearing defective (Delta-f508) cystic fibrosis transmembrane conductance regulator

Hepatology ◽

10.1002/hep.510270103 ◽

1998 ◽

Vol 27 (1) ◽

pp. 7-14 ◽

Cited By ~ 19

Author(s):

K. Ramakrishnan Bhaskar ◽

Bradley S. Turner ◽

Shelley A. Grubman ◽

Douglas M. Jefferson ◽

J.Thomas LaMont

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Biliary Epithelial Cells ◽

Functional Stability of Rescued ΔF508 Cystic Fibrosis Transmembrane Conductance Regulator in Airway Epithelial Cells

American Journal of Respiratory Cell and Molecular Biology ◽

10.1165/rcmb.2008-0434oc ◽

2010 ◽

Vol 42 (3) ◽

pp. 363-372 ◽

Cited By ~ 39

Author(s):

Asta Jurkuvenaite ◽

Lan Chen ◽

Rafal Bartoszewski ◽

Rebecca Goldstein ◽

Zsuzsa Bebok ◽

...

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Airway Epithelial Cells ◽

Functional Stability ◽

Airway Epithelial ◽

The cystic fibrosis transmembrane conductance regulator is not a base transporter in isolated duodenal epithelial cells

Acta Physiologica Scandinavica ◽

10.1046/j.1365-201x.2002.00957.x ◽

2002 ◽

Vol 174 (4) ◽

pp. 327-336 ◽

Cited By ~ 7

Author(s):

J. PRAETORIUS ◽

U. G. FRIIS ◽

M. A. AINSWORTH ◽

O. B. SCHAFFALITZKY DE MUCKADELL ◽

T. JOHANSEN

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Disruption of Interleukin-1β Autocrine Signaling Rescues Complex I Activity and Improves ROS Levels in Immortalized Epithelial Cells with Impaired Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Function

PLoS ONE ◽

10.1371/journal.pone.0099257 ◽

2014 ◽

Vol 9 (6) ◽

pp. e99257 ◽

Cited By ~ 25

Author(s):

Mariángeles Clauzure ◽

Angel G. Valdivieso ◽

María M. Massip Copiz ◽

Gustavo Schulman ◽

María Luz Teiber ◽

...

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Complex I ◽

Interleukin 1Β ◽

Autocrine Signaling ◽

Complex I Activity ◽

Spliceosome-Mediated RNATrans-Splicing with Recombinant Adeno-Associated Virus Partially Restores Cystic Fibrosis Transmembrane Conductance Regulator Function to Polarized Human Cystic Fibrosis Airway Epithelial Cells

Human Gene Therapy ◽

10.1089/hum.2005.16.1116 ◽

2005 ◽

Vol 16 (9) ◽

pp. 1116-1123 ◽

Cited By ~ 42

Author(s):

Xiaoming Liu ◽

Meihui Luo ◽

Liang N. Zhang ◽

Ziying Yan ◽

Roman Zak ◽

...

Keyword(s):

Cystic Fibrosis ◽

Epithelial Cells ◽

Airway Epithelial Cells ◽

Airway Epithelial ◽

Adeno Associated Virus ◽

Cystic Fibrosis Airway ◽