Ascending aortic aneurysm and diaphragmatic hernia in a case of Marfan syndrome

2017 ◽  
Vol 25 (5) ◽  
pp. 378-380 ◽  
Author(s):  
Jignesh Kothari ◽  
Manish Hinduja ◽  
Kinnaresh Baria ◽  
Himani Pandya
Keyword(s):  
Aortic Aneurysm ◽  
Hiatal Hernia ◽  
Marfan Syndrome ◽  
Diaphragmatic Hernia ◽  
Rare Case ◽  
Surgical Repair ◽  
Gastrointestinal Involvement ◽  
Ascending Aortic Aneurysm ◽  
Diagnosis And Management ◽  
Type Iv

Marfan syndrome commonly affects the skeletal, ocular, and cardiovascular systems. Involvement of the gastrointestinal system is known but uncommon. Intervention depends upon the system involved and the severity of symptoms. Special awareness is required for the diagnosis and management of gastrointestinal involvement in these patients. We report a rare case of simultaneous surgical repair of an ascending aortic aneurysm and a type IV hiatal hernia in a 35-year-old man with Marfan syndrome.

Unicommissural Unicuspid Aortic Valve, Ascending Aortic Aneurysm, and Bovine Arch: A Rare Case Report

2021 ◽  
pp. 215013512096520
Author(s):  
Zachary T. Wilson ◽  
Graham Stockdale ◽  
William B. Reichert ◽  
Modesto Colon ◽  
Michael Morris ◽  
...  
Keyword(s):  
Aortic Valve ◽  
Aortic Aneurysm ◽  
Rare Case ◽  
Mechanical Valve ◽  
Aortic Graft ◽  
Ascending Aortic Aneurysm ◽  
Graft Placement ◽  
Progressive Dyspnea ◽  
Rare Case Report ◽  
Bovine Arch

A 24-year-old man presented with rapidly progressive dyspnea due to mixed aortic stenosis and insufficiency. Unicommissural unicuspid aortic valve, ascending aortic aneurysm, and a bovine arch were identified on computed tomography angiography. Uncomplicated surgical mechanical valve replacement and ascending aortic graft placement improved his symptoms. Aortopathy is common in unicuspid valve patients.

scholarly journals A rare case of pseudoaneurysm at the site of untreated coarctation of the aorta in an adult patient

2020 ◽  
Author(s):  
Takuma Mikami ◽  
Takeshi Kamada ◽  
Hiroki Uchiyama ◽  
Yosuke Kuroda ◽  
Ryo Harada ◽  
...  
Keyword(s):  
High Risk ◽  
Aortic Aneurysm ◽  
Aortic Coarctation ◽  
Poor Prognosis ◽  
Rare Case ◽  
Surgical Repair ◽  
Coarctation Of The Aorta ◽  
Pathological Findings ◽  
Open Surgical Repair ◽  
Risk Of Rupture

Abstract Here we report a rare case of pseudoaneurysm at the site of aortic coarctation. Aortic coarctation and a saccular aortic aneurysm protruding from the site of this coarctation were detected in a 50-year-old woman. Owing to the shape of the aneurysm and high risk of rupture, an open surgical repair was performed. The pathological findings of the removed aneurysm revealed a pseudoaneurysm consisting of only a thin adventitial wall. Adult uncorrected aortic coarctation has a poor prognosis. One of its causes may be the formation of such a pseudoaneurysm.

scholarly journals Durability of open surgical repair of type IV thoracoabdominal aortic aneurysm

2019 ◽  
Vol 69 (3) ◽  
pp. 661-670 ◽  
Author(s):  
Christopher A. Latz ◽  
Virendra I. Patel ◽  
Richard P. Cambria ◽  
Emel A. Ergul ◽  
R. Todd Lancaster ◽  
...  
Keyword(s):  
Aortic Aneurysm ◽  
Surgical Repair ◽  
Thoracoabdominal Aortic Aneurysm ◽  
Open Surgical Repair ◽  
Type Iv

scholarly journals A rare case of compression atelectasis due to spontaneous diaphragmatic hernia: a case report

2021 ◽  
Vol 9 (1) ◽  
Author(s):  
Fachreza Damara
Keyword(s):  
Diaphragmatic Hernia ◽  
Rare Case ◽  
Epigastric Pain ◽  
Clinical Manifestations ◽  
Gastrointestinal Symptoms ◽  
Intrathoracic Pressure ◽  
Acid Reflux ◽  
Type Iv ◽  
Rare Occasion ◽  
High Level

Type IV diaphragmatic hernia is a rare case which has various clinical manifestations. The clinical manifestations as a result of protruded organ towards thoracic cavity in diaphragmatic hernia are varied from gastrointestinal symptoms such as epigastric pain, dysphagia and acid reflux. However, in a rare occasion, dyspnea may present as a result of compression atelectasis due to excessive increased in intrathoracic pressure. Here, we report a 57-year-old male patient who had spontaneous diaphragmatic hernia admitted with dyspnea as a chief complaint. This report might add another perspective to the physicians in facing the patient with atelectasis as the result of a high level of lung compression secondary to type IV diaphragmatic hernia.

A Rare Case of Pancreatitis Due to Trans-Hiatal Herniation of the Pancreas Within a Type IV Hiatal Hernia

2018 ◽  
Vol 113 (Supplement) ◽  
pp. S730
Author(s):  
Patrick Chen ◽  
David Do ◽  
Steve Mudroch ◽  
Rajan Prakash ◽  
Padmini Krishnamurthy
Keyword(s):  
Hiatal Hernia ◽  
Rare Case ◽  
Type Iv

scholarly journals Case report: Type IV paraesophageal hernia

2015 ◽  
Vol 5 (1) ◽  
pp. 36-39
Author(s):  
Joshua Hefler
Keyword(s):  
Case Report ◽  
Small Bowel ◽  
Hiatal Hernia ◽  
Paraesophageal Hernia ◽  
Surgical Repair ◽  
Large Defect ◽  
Type Iv ◽  
Gastric Obstruction ◽  
Paraesophageal Hiatal Hernia ◽  
Over Time

This case report is about a 43 year old man, who presented with a large paraesophageal hiatal hernia. Hiatal hernias are common and often asymptomatic. However, this patient’s hernia was caused by a large defect in his diaphragm, into which his stomach, multiple loops of small bowel and even part of his colon had herniated, causing recurrent gastric obstruction. While this is a condition that develops slowly, over time in most patients, this case of hiatal hernia likely results from a congenital defect, given his relatively young age, the size of the defect and his associated anatomical abnormalities. This report details his presentation and surgical repair, complemented with corresponding images.

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