Bilateral Partial Anomalous Pulmonary Venous Connection with Intact Atrial Septum

1996 ◽  
Vol 4 (3) ◽  
pp. 181-183 ◽  
Author(s):  
Antonio F Corno
Keyword(s):  
Surgical Repair ◽  
Atrial Septum ◽  
Intact Atrial Septum ◽  
Rare Malformation ◽  
Anomalous Pulmonary Venous Connection

Bilateral partial anomalous pulmonary venous connection is a very rare malformation; its association with intact atrial septum is even more unusual. This report concerns a 5-year-old girl with this condition who underwent successful surgical repair.

The impact, and surgical implications, of isolated anomalous connection of one pulmonary vein

2007 ◽  
Vol 17 (5) ◽  
pp. 554-556
Author(s):  
Masahiro Koh ◽  
Hideki Uemura ◽  
Koji Kagisaki
Keyword(s):  
Left Atrium ◽  
Pulmonary Vein ◽  
Surgical Repair ◽  
Atrial Septum ◽  
Intact Atrial Septum ◽  
Flow Through ◽  
The Difference ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection ◽  
The Impact

AbstractPartially anomalous pulmonary venous connection of a solitary pulmonary vein in the setting of an intact atrial septum is often subclinical, and the indications for surgical repair are controversial. Here we describe a patient who developed a significant shunt over a period of 10-years. Flow through the anomalously connected pulmonary segment depends on the difference of pressure between the right and left atrium, and may increase with age.

scholarly journals Novel technique of repairing right partial anomalous pulmonary venous connection with intact atrial septum using in situ interatrial septum as a flap in a 68-year-old-woman: a case report

2020 ◽  
Vol 15 (1) ◽  
Author(s):  
Atsushi Morishita ◽  
Ikuo Hagino ◽  
Hideyuki Tomioka ◽  
Seiichiro Katahira ◽  
Takeshi Hoshino ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Right Atrium ◽  
Septal Defect ◽  
Surgical Repair ◽  
Interatrial Septum ◽  
Pulmonary Artery Hypertension ◽  
Right Heart ◽  
Intact Atrial Septum ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection

Abstract Background Partial anomalous pulmonary venous connection draining into the right atrium with an intact atrial septum is a very rare clinical entity in the adult population. Partial anomalous pulmonary venous connection must be suspected as a differential diagnosis when the cause of right heart enlargement and pulmonary artery hypertension is unknown. Case presentation This study describes the surgical case of an isolated right partial anomalous pulmonary venous connection to the right atrium in a 68-year-old woman, who underwent tricuspid ring annuloplasty and right-sided maze procedure simultaneously. She had complaints of gradually progressing dyspnea on exertion. However, a diagnosis could not be established despite consultations at multiple hospitals for over a year. Right heart catheterization revealed severe pulmonary artery hypertension with a mean pulmonary artery pressure of 46 mmHg, step-up phenomenon of oxygen saturation at the mid-level of the right atrium with a pulmonary-to-systemic blood flow ratio of 2.4, and a pulmonary vascular resistance of 3.1 Wood Units. As medical treatment with pulmonary artery vasodilator therapy did not improve her symptoms, she underwent surgical repair. An atrial septal defect was created surgically with a curvilinear tongue-shaped cut. The right anomalous pulmonary veins were rerouted through the surgically created atrial septal defect into the left atrium with a baffle comprised of the interatrial septum flap, kept in continuity with the anterior margin and sutured while mobilizing the enlarged right atrium. The patient had an uneventful postoperative course and remains asymptomatic. Conclusions The described surgical technique could be considered an effective alternative for patients undergoing surgical repair for a partial anomalous pulmonary venous connection isolated to the right atrium. The indication for surgery must be judged on a case-by-case basis in these patients with prevalent systemic-to-pulmonary shunting.

Partial anomalous pulmonary venous connection with intact atrial septum

1967 ◽  
Vol 19 (1) ◽  
pp. 129
Author(s):  
Robert L. Frye ◽  
Mathilde M. Krebs ◽  
Shahbudin H. Rahimtoola ◽  
Franz J. Hallermann ◽  
Robert B. Wallace ◽  
...  
Keyword(s):  
Atrial Septum ◽  
Intact Atrial Septum ◽  
Anomalous Pulmonary Venous Connection

scholarly journals Novel technique of repairing right partial anomalous pulmonary venous connection with intact atrial septum using in situ interatrial septum as a flap in a 68-year-old-woman: a case report

2020 ◽  
Author(s):  
Atsushi Morishita ◽  
Ikuo Hagino ◽  
Hideyuki Tomioka ◽  
Seiichiro Katahira ◽  
Takeshi Hoshino ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Right Atrium ◽  
Septal Defect ◽  
Surgical Repair ◽  
Interatrial Septum ◽  
Pulmonary Artery Hypertension ◽  
Right Heart ◽  
Intact Atrial Septum ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection

Abstract Background: Partial anomalous pulmonary venous connection draining into the right atrium with an intact atrial septum is a very rare clinical entity in the adult population. Partial anomalous pulmonary venous connection must be suspected as a differential diagnosis when the cause of right heart enlargement and pulmonary artery hypertension is unknown.Case presentation: This study describes the surgical case of an isolated right partial anomalous pulmonary venous connection to the right atrium in a 68-year-old woman, who underwent tricuspid ring annuloplasty and right-sided maze procedure simultaneously. She had complaints of gradually progressing dyspnea on exertion. However, a diagnosis could not be established despite consultations at multiple hospitals for over a year. Right heart catheterization revealed severe pulmonary artery hypertension with a mean pulmonary artery pressure of 46 mmHg, step-up phenomenon of oxygen saturation at the mid-level of the right atrium with a pulmonary-to-systemic blood flow ratio of 2.4, and a pulmonary vascular resistance of 3.1 Wood Units. As medical treatment with pulmonary artery vasodilator therapy did not improve her symptoms, she underwent surgical repair. An atrial septal defect was created surgically with a curvilinear tongue-shaped cut. The right anomalous pulmonary veins were rerouted through the surgically created atrial septal defect into the left atrium with a baffle comprised of the interatrial septum flap, kept in continuity with the anterior margin and sutured while mobilizing the enlarged right atrium. The patient had an uneventful postoperative course and remains asymptomatic.Conclusions: The described surgical technique could be considered an effective alternative for patients undergoing surgical repair for a partial anomalous pulmonary venous connection isolated to the right atrium. The indication for surgery must be judged on a case-by-case basis in these patients with prevalent systemic-to-pulmonary shunting.

scholarly journals Recurrent Pneumonia and a Normal Heart: Late Complication after Repair of Hemianomalous Pulmonary Venous Drainage—A Cautionary Tale

2010 ◽  
Vol 2010 ◽  
pp. 1-3
Author(s):  
Maryanne Caruana ◽  
Victor Grech ◽  
Jane Somerville
Keyword(s):  
Surgical Repair ◽  
Correct Diagnosis ◽  
Late Complication ◽  
Venous Drainage ◽  
Atrial Septum ◽  
Specialist Care ◽  
Recurrent Pneumonia ◽  
Intact Atrial Septum ◽  
Respiratory Physician

Hemianomalous pulmonary venous drainage with intact atrial septum is a rare congenital anomaly and reports of its surgical repair and the long-term complications related to the correction are only infrequently encountered in the literature. We report the case of a patient with hemianomalous pulmonary venous drainage and intact atrial septum who underwent surgical repair using a pericardial baffle and creation of an “atrial septal defect” aged 15 years. Dyspnoea and recurrent chest infections started 7 months after surgery when he was seen by a respiratory physician without cardiac followup. He presented again aged 28 years with a recurrent pneumonia investigated over 6 weeks and heart pronounced normal from examination and echocardiography. Correct diagnosis was made in Grown Up Congenital Heart (GUCH) clinic stimulating review of data and catheterisation with pulmonary artery angiography which confirmed it. We feel that this case highlights the importance of specialist care and followup for GUCH patients.

Anomalous Pulmonary Venous Connection of Entire Left Lung with Intact Atrial Septum

Radiology ◽  
1977 ◽  
Vol 122 (3) ◽  
pp. 591-595 ◽  
Author(s):  
Stephen W. Miller ◽  
Robert E. Dinsmore ◽  
Richard R. Liberthson ◽  
Allan Goldblatt ◽  
Willard M. Daggett ◽  
...  
Keyword(s):  
Left Lung ◽  
Atrial Septum ◽  
Intact Atrial Septum ◽  
Anomalous Pulmonary Venous Connection
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