Perioperative and Anesthetic Considerations in Truncus Arteriosus

2018 ◽  
Vol 22 (3) ◽  
pp. 285-293 ◽  
Author(s):  
Rishi Parikh ◽  
Michael Eisses ◽  
Gregory J. Latham ◽  
Denise C. Joffe ◽  
Faith J. Ross
Keyword(s):  
Heart Failure ◽  
Congestive Heart Failure ◽  
Neonatal Period ◽  
Anesthetic Management ◽  
Truncus Arteriosus ◽  
Semilunar Valve ◽  
Cardiac Lesion ◽  
Complete Repair ◽  
Arterial Trunk ◽  
Anesthetic Considerations

Truncus arteriosus is a congenital cardiac lesion in which failure of embryonic truncal septation results in a single semilunar valve and single arterial trunk providing both pulmonary and systemic circulations. Most patients with this lesion are symptomatic in the neonatal period with cyanosis and/or congestive heart failure and undergo complete repair in the first weeks of life. This review will focus on the anatomy, physiology, and perioperative anesthetic management of patients with truncus arteriosus.

Successful Surgical and Anesthetic Management of Vein of Galen Aneurysm in a Neonate in Congestive Heart Failure

Neurosurgery ◽  
1988 ◽  
Vol 22 (5) ◽  
pp. 908-910 ◽  
Author(s):  
Jane Matjasko ◽  
Walker Robinson ◽  
Daniel Eudaily
Keyword(s):  
Heart Failure ◽  
Congestive Heart Failure ◽  
Cardiac Failure ◽  
Growth And Development ◽  
Anesthetic Management ◽  
Vascular Supply ◽  
Vein Of Galen ◽  
Vein Of Galen Malformation ◽  
Vein Of Galen Aneurysm

Abstract A 12-day-old infant in intractable cardiac failure due to a vein of Galen malformation was treated successfully with serial ligation of the majority of the vessels feeding the malformation. Despite some residual vascular supply to the malformation, the congestive heart failure has disappeared and growth and development have been normal over a 3-year follow-up period.

scholarly journals Vein of Galen malformation, a rare cause of epilepsy

2016 ◽  
Vol 03 (01) ◽  
pp. 024-025
Author(s):  
Mohammad Sayadnasiri
Keyword(s):  
Heart Failure ◽  
Congestive Heart Failure ◽  
Vascular Malformation ◽  
Neonatal Period ◽  
Severe Congestive Heart Failure ◽  
Low Flow ◽  
Vein Of Galen ◽  
Vein Of Galen Malformation ◽  
Venous Structure ◽  
Cerebral Vascular Malformation

AbstractVein of Galen malformation (VOGM) is a rare congenital cerebral vascular malformation characterized by an aneurysmally dilated midline deep venous structure, fed by abnormal arteriovenous communication. Most patients develop severe congestive heart failure at neonatal period that is fatal if left untreated. Rarely, patients with low-flow fistula present with headache, seizure, or focal neurological sign at adulthood. A 28-year-old female with VOGM-related epilepsy was introduced in this brief report.

Surgical ligation of a persistent arterial duct in one of conjoined thoracopagus twins prior to surgical separation

1999 ◽  
Vol 9 (2) ◽  
pp. 203-206 ◽  
Author(s):  
Roque A. Cordoba ◽  
Ernesto Juaneda ◽  
Luis E. Alday
Keyword(s):  
Heart Failure ◽  
Congestive Heart Failure ◽  
Respiratory Distress ◽  
Neonatal Period ◽  
Excellent Outcome ◽  
Surgical Ligation ◽  
Arterial Duct ◽  
Subsequent Separation ◽  
Persistent Arterial Duct ◽  
Surgical Separation

AbstractOne of conjoined thoracopagus twins, with separate hearts and a common pericardial sack, presented with respiratory distress because of a persistent arterial duct causing congestive heart failure in the neonatal period. Surgical ligation of the duct was performed prior to subsequent separation, with an excellent outcome.

scholarly journals Early Neonatal Cyanosis as a Presentation of a Rare Cardiac Anomaly: Truncus Arteriosus Type IV

2021 ◽  
pp. 1-4
Author(s):  
Amjad Mohamed Haider ◽  
Ammar M.H. Shehadeh ◽  
Rola Mohamed Alfarra
Keyword(s):  
Heart Failure ◽  
Congestive Heart Failure ◽  
Coming Out ◽  
Congenital Heart ◽  
Truncus Arteriosus ◽  
Cardiac Anomaly ◽  
Common Trunk ◽  
Type Iv ◽  
Congenital Heart Anomaly ◽  
Blalock Taussig Shunt

Truncus arteriosus (TA) is a rare congenital heart anomaly presenting with mild cyanosis and congestive heart failure. It occurs when the blood vessels coming out of the heart in the developing baby fail to separate completely during development, leaving a common trunk responsible for the pulmonary and systemic perfusion. There are several variants of TA, depending on the specific anatomy and arterial connection. We report a case of a full-term newborn who developed cyanosis and desaturation during the first day of life. Investigations and echocardiography were consistent with TA type IV. Prostaglandin infusion was immediately started, and then, a successful palliative right modified Blalock Taussig shunt was performed.

scholarly journals Anesthetic Management of a Patient with Harlequin Ichthyosis

2021 ◽  
Vol 2021 ◽  
pp. 1-3
Author(s):  
Klint J. Smart ◽  
Catherine A. Gruffi ◽  
Tara M. Doherty
Keyword(s):  
Neonatal Period ◽  
Anesthetic Management ◽  
Skin Barrier ◽  
Skin Infections ◽  
Congenital Ichthyosis ◽  
Harlequin Ichthyosis ◽  
Anesthetic Considerations ◽  
Vulnerable Patient ◽  
Fatal Form ◽  
The Right

Harlequin ichthyosis is a severe and often fatal form of congenital ichthyosis caused by defective lipid transport which results in a dysfunctional skin barrier. Patients who survive the neonatal period are predisposed to skin infections, sepsis, impaired thermoregulation, and dehydration. The unique skin characteristics can present significant anesthetic challenges. We highlight the relevant anesthetic considerations in a 3-year-old presenting for syndactyly release of the right second and fourth digits. We describe the steps to ensure protection of the fragile skin barrier during establishment of intravenous access and airway management, therefore providing guidance for care of this vulnerable patient population.

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