Comparison of utility scores from the Visual Analog Scale and Health Utilities Index 3 in children following pediatric intensive care unit admission

2013 ◽  
Vol 19 (1) ◽  
pp. 53-62 ◽  
Author(s):  
Shanil Ebrahim ◽  
Christopher Parshuram
Keyword(s):  
Intensive Care Unit ◽  
Intensive Care ◽  
Intensive Care Unit Admission ◽  
Pediatric Intensive Care Unit ◽  
Visual Analog Scale ◽  
Pediatric Intensive Care ◽  
Health Utilities Index ◽  
Analog Scale ◽  
Health Utilities ◽  
Utility Scores

GNAO1 Mutation–Induced Pediatric Dystonic Storm Rescue With Pallidal Deep Brain Stimulation

2018 ◽  
Vol 33 (6) ◽  
pp. 413-416 ◽  
Author(s):  
C. Michael Honey ◽  
Armaan K. Malhotra ◽  
Maja Tarailo-Graovac ◽  
Clara D. M. van Karnebeek ◽  
Gabriella Horvath ◽  
...  
Keyword(s):  
Intensive Care Unit ◽  
Intensive Care ◽  
Deep Brain Stimulation ◽  
Intensive Care Unit Admission ◽  
Pediatric Intensive Care Unit ◽  
Brain Stimulation ◽  
De Novo ◽  
Pediatric Intensive Care ◽  
Status Dystonicus ◽  
Deep Brain

Dystonic storm or status dystonicus is a life-threatening hyperkinetic movement disorder with biochemical alterations due to the excessive muscle contractions. The medical management can require pediatric intensive care unit admission and a combination of medications while the underlying trigger is managed. Severe cases may require general anesthesia and paralytic agents with intubation and may relapse when these drugs are weaned. Deep brain stimulation of the globus pallidum has been reported to terminate dystonic storm in several pediatric cases. We present a 10-year-old boy with a de novo GNAO1 mutation–induced dystonic storm who required a 2-month pediatric intensive care unit admission and remained refractory to all medical treatments. Deep brain stimulation was performed under general anesthetic without complication. His dyskinetic movements stopped with initiation of stimulation. He was discharged from the pediatric intensive care unit after 4 days. We present prospectively evaluated changes in dystonia symptoms and quality of life for a patient with GNAO1 mutation treated with deep brain stimulation.

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