Nevoid basal cell carcinoma syndrome is a hereditary condition associated with a wide range of developmental anomalies as well as increased risk of certain neoplasms. It is more commonly known as Gorlin–Goltz syndrome (GGS). We report a case of GGS with classic clinical and imaging findings of multiple odontogenic keratocysts (OKCs) in the jaw, calcification of falx cerebri, and bifid ribs. The findings of restricted diffusion within OKCs on diffusion-weighted imaging are also described.
Imaging findings of Gorlin-Goltz syndrome
