Isolated Single Right Coronary Artery in a Pediatric Patient

2019 ◽  
Vol 10 (4) ◽  
pp. 515-517
Author(s):  
Justin H. Berger ◽  
Jonathan J. Rome ◽  
Julie A. Brothers
Keyword(s):  
Coronary Artery ◽  
Sudden Cardiac Death ◽  
Pediatric Patient ◽  
Coronary Arteries ◽  
Right Coronary Artery ◽  
Cardiac Disease ◽  
Cardiac Death ◽  
Adult Onset ◽  
First Case ◽  
Single Right Coronary Artery

Anatomic single coronary arteries are quite rare but can be a potential cause of sudden cardiac death. We present the first case of a pediatric patient with an anatomic single right coronary artery (Lipton type R1 or Shirani-Roberts type IIA), of a type which has been associated with adult-onset ischemic cardiac disease. We review the evaluation and management of this young patient.

scholarly journals A Single Coronary Artery Originating from the Right Coronary Sinus with a Typical Course of the Right Coronary Artery and the Interarterial Course of the Left Main, Left Anterior Descending, and Left Circumflex as an Example of a Rare Case of High-Risk Coronary Anomaly

Diagnostics ◽  
2022 ◽  
Vol 12 (1) ◽  
pp. 167
Author(s):  
Paweł Gać ◽  
Aleksandra Żórawik ◽  
Rafał Poręba
Keyword(s):  
Coronary Artery ◽  
Sudden Cardiac Death ◽  
Coronary Arteries ◽  
Right Coronary Artery ◽  
Coronary Sinus ◽  
Cardiac Death ◽  
Rare Case ◽  
Pulmonary Trunk ◽  
Increased Risk ◽  
The Right

In the typical course of the coronary arteries, the right coronary artery comes from the right coronary sinus and descends in the right atrioventricular groove. The left coronary artery trunk begins from the left coronary sinus. It crosses the pulmonary trunk and divides into left anterior descending and left circumflex arteries. Anatomical differences of the coronary arteries can be observed in 0.3–5.6% of the population. The interarterial course of coronary branches between the aorta and the pulmonary trunk is a malignant anomaly of the coronary arteries. Such abnormalities have been associated with an increased risk of sudden cardiac death. We present a rare case of coronary arteries anomaly involving the presence of a single right coronary artery and the interarterial course of its atypical branches documented by computed tomography angiography (CTA). In summary, the accurate assessment of the anatomical topography of coronary anomalies, possible in CTA, is necessary in the analysis of the risk of sudden cardiac death and its prevention.

scholarly journals Anomalous Right Coronary Artery and Sudden Cardiac Death

2012 ◽  
Vol 5 (6) ◽  
Author(s):  
Brian Greet ◽  
Adriana Quinones ◽  
Monvadi Srichai ◽  
Sripal Bangalore ◽  
Robert O. Roswell
Keyword(s):  
Coronary Artery ◽  
Sudden Cardiac Death ◽  
Right Coronary Artery ◽  
Cardiac Death

Evidence of spasm in the distal right coronary artery at autopsy in cases of sudden cardiac death

1994 ◽  
Vol 109 (1-2) ◽  
pp. 300
Author(s):  
L. Jørgensen ◽  
J. Olving ◽  
T.O. Rognum ◽  
S. Rogde ◽  
B. Olaisen
Keyword(s):  
Coronary Artery ◽  
Sudden Cardiac Death ◽  
Right Coronary Artery ◽  
Cardiac Death

scholarly journals Sudden Cardiac Death due to Coronary Artery Vasculitis in a Patient with Relapsing Polychondritis

2020 ◽  
Vol 2020 ◽  
pp. 1-6
Author(s):  
Heather Bukiri ◽  
Steven M. Ruhoy ◽  
Jane H. Buckner
Keyword(s):  
Coronary Artery ◽  
Sudden Cardiac Death ◽  
Cardiac Disease ◽  
Cardiac Death ◽  
Plasma Cells ◽  
Clinical Manifestations ◽  
Relapsing Polychondritis ◽  
Tracheobronchial Tree ◽  
Systemic Autoimmune Disease ◽  
Igg4 Related Disease

Relapsing polychondritis (RP) is a systemic autoimmune disease characterized by relapsing and remitting inflammation of the cartilaginous structures of the ears, nose, tracheobronchial tree, and joints. Diagnosis is challenging due to the heterogeneity of clinical manifestations, the relapsing and remitting nature of the disease, the presence of coexistent diseases in at least one-third of patients, and the lack of a diagnostic blood test. Although RP-associated cardiac disease is the second most common cause of death behind tracheobronchial complications, coronary artery vasculitis is rare. This report describes a case of sudden cardiac death due to vasculitis affecting the coronary arteries in a patient with RP. The pathologic findings included obliterative coronary arteritis with plasma cells and storiform fibrosis, features suggesting that IgG4-related disease (IgG4-RD) may have contributed to the patient’s cardiac disease. The literature on vasculitis and cardiac disease in RP and the possible role of IgG4-RD in this setting is also reviewed. The primary take-home message from this case report is the importance of frequent screening for cardiac disease, regardless of symptoms, in patients with RP. In addition, considering the diagnosis of IgG4-RD in some cases thought to be RP may also be warranted.

scholarly journals Hypoplastic coronary artery disease and hypertension in a child: a case report

2021 ◽  
Author(s):  
Yuji Doi ◽  
Kenji Waki ◽  
Kayo Ogino ◽  
Tomohiro Hayashi
Keyword(s):  
Heart Failure ◽  
Coronary Artery Disease ◽  
Coronary Artery ◽  
Sudden Cardiac Death ◽  
Rare Disease ◽  
Pediatric Patient ◽  
Cardiac Death ◽  
Acute Myocarditis ◽  
Close Observation ◽  
Artery Disease

Abstract Background Hypoplastic coronary artery disease (HCAD) is an extremely rare disease associated with a risk of sudden cardiac death. It is rarely recognized in a live pediatric patient. Case summary We report a case of HCAD in a patient who first presented with vomiting and poor feeding, suggestive of acute heart failure due to cardiomyopathy or acute myocarditis in infancy. Hypertension and signs of ischemia became evident on electrocardiography and scintigraphy after his cardiac function fully recovered, and he was diagnosed with HCAD by angiography performed at the age of eight years. He has remained under close observation with anti-hypertensives, aspirin, and exercise restriction. Discussion Although HCAD is a rare disease, it may not only cause ischemia but may also result in heart failure and sudden cardiac death. It should be considered in any pediatric patient with heart failure. Mid-term follow-up visits might be necessary to detect signs of ischemia in pediatric patients presenting with features of heart failure.

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