Transposition of the Great Arteries Associated With Non-Kommerell Diverticulum: Lessons From Two Cases

2020 ◽  
Vol 11 (3) ◽  
pp. 377-379
Author(s):  
Truong Ly Thinh Nguyen ◽  
Vinh Quang Tran
Keyword(s):  
Surgical Management ◽  
Congenital Heart ◽  
Vascular Ring ◽  
Unusual Combination ◽  
Heart Lesions ◽  
Kommerell Diverticulum

Vascular ring malformations usually occur as an isolated lesion. d-Transposition of the great arteries (d-TGA) associated with vascular ring malformations has seldom been reported in the literature. In this report, we describe two unusual cases of d-TGA associated with non-Kommerell diverticulum resulting in vascular ring. Our approach for the diagnosis and surgical management of this unusual combination of congenital heart lesions is described.

Unusual combination of congenital heart lesions in a child with Noonan's syndrome

1982 ◽  
Vol 3 (1) ◽  
pp. 23-26 ◽  
Author(s):  
Jan Lam ◽  
Antonio Corno ◽  
Hanna W. E. Oorthuys ◽  
Carlo Marcelletti
Keyword(s):  
Congenital Heart ◽  
Noonan's Syndrome ◽  
Unusual Combination ◽  
Heart Lesions ◽  
Noonan’S Syndrome

scholarly journals Incidence of Postoperative Chylothorax Following Congenital Heart Surgery in Pediatric Patients: A Single-Center Experience

2020 ◽  
Vol 23 (4) ◽  
pp. E430-E434
Author(s):  
Sung Kwang Lee ◽  
Kwang Ho Choi
Keyword(s):  
Surgical Management ◽  
Medical Records ◽  
Congenital Heart ◽  
Heart Surgery ◽  
Vascular Ring ◽  
Congenital Heart Surgery ◽  
Single Center Experience ◽  
Management Group ◽  
Heart Repair ◽  
Substantial Morbidity

Background: Although postoperative chylothorax following congenital heart surgery occurs rarely, it is associated with substantial morbidity and mortality. The incidence of postoperative chylothorax has been reported as 2% to 5%. Therefore, we aimed to evaluate the incidence of postoperative chylothorax at our center and compared our results with those of other studies. Methods: Between January 2009 and December 2018, there were 2,515 congenital heart repair surgeries performed at our center. Thirty-six patients with postoperative chylothorax were enrolled in this study, and their medical records retrospectively were reviewed. We calculated the overall and surgery-specific incidences. We compared the data of the medical management group with those of the surgical management group. Results: The overall incidence of postoperative chylothorax was 1.4%. The incidence was highest for patients who underwent vascular ring repair (3/32). Moreover, the incidence was higher for single ventricle-related procedure than bi-ventricle-related procedures (5.6% versus 1.0%, P < .0001). Chylothorax was predominantly found on the left side (20/36). Among these cases, six patients died; three of these six were in the surgical management group. Conclusions: The postoperative chylothorax incidence at our center was comparable to those of other centers. However, a reasonable protocol for postoperative chylothorax management to improve outcomes is necessary.

Surgical management of congenital heart defects in adolescent and adult patients, between years 2001–2008

2009 ◽  
Vol 150 (37) ◽  
pp. 1739-1743 ◽  
Author(s):  
István Hartyánszky ◽  
Andrea Székely ◽  
László Király ◽  
Zsolt Prodán ◽  
Sándor Mihályi ◽  
...  
Keyword(s):  
Surgical Management ◽  
Congenital Heart Defects ◽  
Congenital Heart ◽  
Heart Defects ◽  
Adult Patients

A felnőttkorban operált veleszületett szívhibák között vezetnek az I. rekonstrukciós beavatkozások: a) frissen felismert betegségek, b) megelőzően inoperábilisnak ítélt kórképek, c) pulmonalis hypertonia, jobbkamra-elégtelenség miatt „elkésett” műtétek. Növekszik a II. REDO műtétek száma: a) residuumok korrigálása, b) kinőtt, diszfunkciós homograftok cseréje, c) műtéti/intervenciós korrigálás utáni recoarctatio (aneurysma, dissectio) sebészete, d) aorta valvulotomia/valvuloplastica, illetve társvitiumok (TGA) korrigálásának következményeként Ross-műtét, műbillentyű-beültetés . Betegek, eredmények: A 2001–2008 között végzett 4496 műtét közül 166 volt fiatal-felnőtt korú (16–52, átlagéletkor: 28 év) (Ia: 77, Ib: 15, Ic: 4, IIa: 11, IIb: 22, IIc: 9, IId: 28). Műtéti mortalitás nem volt, 1 beteg pulmonalis hypertoniás krízisben, 1 jobbkamra-elégtelenség miatti malignus ritmuszavarban, 2 többszerv-elégtelenségben halt meg. Konklúzió: A rizikófaktorokat a pulmonalis hypertonia és a jobbkamra-elégtelenség jelenti. A bonyolult sebészi megoldások a „congenitalis szívsebész” számára nem jelentenek problémát, de koraibb diagnózisok, terápiában az extracorporalis membránoxigenátor használata az eredményeket javíthatja.

Prevalence and diagnostic accuracy of heart disease in children with asymptomatic murmurs

2015 ◽  
Vol 26 (3) ◽  
pp. 446-450 ◽  
Author(s):  
Adziri H. Sackey
Keyword(s):  
Heart Disease ◽  
Diagnostic Accuracy ◽  
Clinical Examination ◽  
Clinical Assessment ◽  
Congenital Heart ◽  
Heart Murmur ◽  
Paediatric Cardiologist ◽  
Heart Murmurs ◽  
Cardiology Clinic ◽  
Heart Lesions

AbstractThis study was performed to determine the prevalence of CHD among children referred with asymptomatic murmurs and to determine the diagnostic accuracy of the assessment of asymptomatic heart murmurs by general paediatricians. We reviewed the records of children who had been referred by general paediatricians to a cardiology clinic for further evaluation of a heart murmur. The referring paediatricians’ clinical assessment of the murmur was compared with the cardiologist’s echocardiographic diagnosis. A total of 150 children were referred by paediatricians to a paediatric cardiologist for further assessment of a heart murmur. Out of 150 children, 72 had a paediatrician’s diagnosis of innocent murmur; of these 72 patients, two (3%) had heart disease on echocardiography. In all, after echocardiography, a range of congenital heart lesions was found in 28 (19%) of the 150 children. CHD is not rare among children with asymptomatic heart murmurs. In this series of children with asymptomatic murmurs, 19% had heart lesions on echocardiography. Most, but not all, of the children with heart lesions were identified on clinical examination by general paediatricians.

scholarly journals Genetic syndromes and congenital heart defects: how is surgical management affected?

2009 ◽  
Vol 35 (4) ◽  
pp. 606-614 ◽  
Author(s):  
Roberto Formigari ◽  
Guido Michielon ◽  
Maria Cristina Digilio ◽  
Gerardo Piacentini ◽  
Adriano Carotti ◽  
...  
Keyword(s):  
Surgical Management ◽  
Congenital Heart Defects ◽  
Congenital Heart ◽  
Heart Defects ◽  
Genetic Syndromes
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