scholarly journals Gingival Tissue Alterations in 2 Patients with Port Wine Stain

2014 ◽  
Vol 18 (2) ◽  
pp. 109-112
Author(s):  
Ayse Kocak-Buyukdere ◽  
Esra Guzeldemir
Keyword(s):  
Soft Tissue ◽  
Gingival Tissue ◽  
Port Wine Stain ◽  
Port Wine ◽  
Wisdom Tooth ◽  
Upper Jaw ◽  
Vascular Birthmarks ◽  
The Right ◽  
Tissue Alterations ◽  
Nevus Flammeus

SUMMARYNevus flammeus, which is also known as port-wine stain (PWS), is one of the vascular birthmarks. PWS occurs in 0.3% of the newborns in both genders. It is a capillary vascular malformation, characterized by a pink or red stain and may involve skin, soft tissue and/or bone. There are a very limited number of reports regarding intraoral involvement of PWS. We report 2 female patients with PWS from date of birth. The first patient was an 11-year-old female who applied to our clinics for the treatment of her non-aesthetic and deviated intraoral view and discoloration of her gingiva, and the second patient was a 56-year-old female who applied for the extraction of her wisdom tooth. Extraoral examination in both patients revealed a diffuse PWS on the right side of their face over the cheek, extending from the midline. While the first patient had reddish skin, gingiva on right site her both jaws and lips, the second patient had only her upper jaw and lip. Because of the first patient’ age, the treatment postponed to her 20’, and the second patient did not accept any treatment. PWS is a rare and non-fatal condition; however, the unique appearance of these patients can lead to psychological problems especially in early ages.

Port-Wine Stain (Nevus Flammeus) in Sturge-Weber Syndrome

2018 ◽  
pp. 1406-1408
Author(s):  
Jason E. Hale ◽  
Sumayya J. Almarzouqi ◽  
Michael L. Morgan ◽  
Andrew G. Lee
Keyword(s):  
Port Wine Stain ◽  
Port Wine ◽  
Weber Syndrome ◽  
Sturge Weber Syndrome ◽  
Nevus Flammeus

scholarly journals A Final Diagnosis of Port Wine Stain or Nevus Flammeus

2017 ◽  
Vol 04 (8) ◽  
Author(s):  
Nayak V ◽  
Kini R ◽  
Rao PK ◽  
Bhandarkar G ◽  
Kashyap RR
Keyword(s):  
Final Diagnosis ◽  
Port Wine Stain ◽  
Port Wine ◽  
Nevus Flammeus

Butterfly-Shaped Mark

PEDIATRICS ◽  
1991 ◽  
Vol 87 (6) ◽  
pp. 956-957
Author(s):  
ARYEH METZKER ◽  
RAANAN SHAMIR
Keyword(s):  
Capillary Hemangioma ◽  
Port Wine Stain ◽  
Port Wine ◽  
Critical Attitude ◽  
Spinal Lesions ◽  
Nevus Flammeus

In Reply.— We were delighted to encounter interest in our "Butterfly-Shaped Mark" (BSM), and read Dr Oakes' remarks with interest. Alas, his critical attitude derives mainly from confusion of terminology. A call for an accepted agreement on common terminology is long due.1 When using the term nevus flammeus (a port wine stain), we clearly differentiate it from capillary hemangioma (strawberry hemangioma). We are quite aware of, and quoted accordingly, the occurrence of several capillary hemangiomas with spinal lesions.2

scholarly journals Combined lymphangioma and hemangioma of the spleen in a patient with Klippel–Trénaunay syndrome

2012 ◽  
Vol 140 (11-12) ◽  
pp. 777-781 ◽  
Author(s):  
Marko Spasic ◽  
Dragce Radovanovic ◽  
Dragan Canovic ◽  
Goran Azanjac ◽  
Predrag Djurdjevic ◽  
...  
Keyword(s):  
Congenital Anomaly ◽  
Soft Tissue ◽  
Female Patient ◽  
Port Wine Stain ◽  
Port Wine ◽  
Rare Congenital Anomaly ◽  
Vascular Origin ◽  
Accompanying Symptoms ◽  
Clinical Triad ◽  
Klippel Trenaunay Syndrome

Introduction. Klippel?Tr?naunay syndrome (KTS) is a very rare congenital anomaly of blood vessels, characterized by the following clinical triad: varicose superficial veins, port-wine stain and usually bony and soft tissue hypertophy of extremities, most often located in the lower extremities. It is often accompanied by visceral manifestations, and rarely combined with splenomegaly. Case Outline. A 30-year-old female patient came to the Surgery Clinic because of occasional left hypochondrial pain. After she was diagnosed with KTS combined with splenomegaly, splenectomy was performed. Macroscopic and microscopic spleen examination indicated the presence of tumor of vascular origin, presenting a combination of lymphangioma and hemangioma. Conclusion. Diagnosed KTS demands a thorough clinical examination of the patient because of the potential presence of visceral manifestations. When splenomegaly is present, even though being often benign, splenectomy is usually performed to alleviate accompanying symptoms which occur as a result of organ enlargement and compression, to prevent rupture and consequential bleeding when the vascular spleen tumor is large, and finally to avoid a possibility of malignant transformation.

Port-Wine Stain (Nevus Flammeus) in Sturge-Weber Syndrome

2015 ◽  
pp. 1-2
Author(s):  
Jason E. Hale ◽  
Sumayya J. Almarzouqi ◽  
Michael L. Morgan ◽  
Andrew G. Lee
Keyword(s):  
Port Wine Stain ◽  
Port Wine ◽  
Weber Syndrome ◽  
Sturge Weber Syndrome ◽  
Nevus Flammeus

scholarly journals Klippel Trenaunay Syndrome: A Brief Overview

2021 ◽  
Vol 5 (2) ◽  
pp. 387-394
Author(s):  
Pande Ayu Naya Kasih Permatananda ◽  
I Gusti Agung Made Adnyana Putra
Keyword(s):  
Soft Tissue ◽  
Vascular Disease ◽  
Clinical Presentation ◽  
Invasive Procedure ◽  
Port Wine Stain ◽  
Port Wine ◽  
Vascular Disorders ◽  
Non Invasive ◽  
Vasculogenesis And Angiogenesis ◽  
Klippel Trenaunay Syndrome

A B S T R A C TKlippel-Trenaunay syndrome is a rare congenital vascular disease. The pathogenesisof this syndrome is unclear, but it is thought that most cases are the result of somaticmutations that affect genes that play a role in vasculogenesis and angiogenesis. Somepatients come with a triad of capillary malformation (hemangioma or port-wine stain),venous varicosities and bony or soft tissue hypertrophy. Clinical presentation of thissyndrome can lead to significant morbidities and mortalities due to severe bleedingand emboli. Although the number of cases is low, a doctor must be able to distinguishKlippel-Trenaunay Syndrome from other rare vascular disorders. Parkes Webersyndrome is usually similar to Klippel-Trenaunay syndrome, except in the arterialmalformations associated with capillary malformations and soft tissue to skeletal orbone hypertrophy. The diagnosis of Klippel-Trenaunay Syndrome is carried outclinically and is quite difficult to do even with experienced doctors because there is noprecise pathognomonic test. There are several options in relation to the managementof Klippel-Trenaunay Syndrome and non-invasive procedure is considered to be themost important of therapy modalities. Early diagnoses, progression monitoring, andproper intervention should be carried out for better prognosis and preventingcomplication.

scholarly journals Sturge Weber Syndrome

2016 ◽  
Vol 8 (1) ◽  
pp. 68
Author(s):  
Kazi Nilufar Moly ◽  
S.M. Abu Ahsan ◽  
Md. Shafiqul Lslam
Keyword(s):  
Trigeminal Nerve ◽  
Male Child ◽  
Port Wine Stain ◽  
Port Wine ◽  
Weber Syndrome ◽  
Neurocutaneous Disorder ◽  
The Face ◽  
Sturge Weber Syndrome ◽  
Nevus Flammeus

<p>Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face (purple colored flat cutaneous haemangiomas ), typically in the ophthalmic (V1) and maxillary (V2) distributions of the trigeminal nerve. The hallmark of sturge weber syndrome is a facial cutaneous venous dilation, also referred to as a nevus flammeus or port wine stain (PWS). Because of the rarity, we report here a one &amp; half year old male child who presented with features of the Sturge Weber Syndrome on both side of face.</p>

Endocrine Dysfunction in a Patient With Phace Syndrome, Including Port-Wine Stain of the Right Periorbital Area

2010 ◽  
Vol 16 (2) ◽  
pp. 255-259 ◽  
Author(s):  
Marie Merheb ◽  
Roula Hourani ◽  
Mira Zantout ◽  
Sami Azar
Keyword(s):  
Port Wine Stain ◽  
Port Wine ◽  
Endocrine Dysfunction ◽  
Phace Syndrome ◽  
The Right
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