Port-Wine-Stain (Nevus Flammeus), Congenital Becker's Nevus, Café-au-lait-Macule and Lentigines: Phakomatosis Pigmentovascularis Type Ia-A New Combination

1999 ◽  
Vol 26 (12) ◽  
pp. 834-836 ◽  
Author(s):  
Arun Joshi ◽  
Vijay Kumar Garg ◽  
Sudha Agrawal ◽  
Arun Agarwalla ◽  
Amarnath Thakur
2018 ◽  
pp. 1406-1408
Author(s):  
Jason E. Hale ◽  
Sumayya J. Almarzouqi ◽  
Michael L. Morgan ◽  
Andrew G. Lee

Author(s):  
Nayak V ◽  
Kini R ◽  
Rao PK ◽  
Bhandarkar G ◽  
Kashyap RR

PEDIATRICS ◽  
1991 ◽  
Vol 87 (6) ◽  
pp. 956-957
Author(s):  
ARYEH METZKER ◽  
RAANAN SHAMIR

In Reply.— We were delighted to encounter interest in our "Butterfly-Shaped Mark" (BSM), and read Dr Oakes' remarks with interest. Alas, his critical attitude derives mainly from confusion of terminology. A call for an accepted agreement on common terminology is long due.1 When using the term nevus flammeus (a port wine stain), we clearly differentiate it from capillary hemangioma (strawberry hemangioma). We are quite aware of, and quoted accordingly, the occurrence of several capillary hemangiomas with spinal lesions.2


2014 ◽  
Vol 18 (2) ◽  
pp. 109-112
Author(s):  
Ayse Kocak-Buyukdere ◽  
Esra Guzeldemir

SUMMARYNevus flammeus, which is also known as port-wine stain (PWS), is one of the vascular birthmarks. PWS occurs in 0.3% of the newborns in both genders. It is a capillary vascular malformation, characterized by a pink or red stain and may involve skin, soft tissue and/or bone. There are a very limited number of reports regarding intraoral involvement of PWS. We report 2 female patients with PWS from date of birth. The first patient was an 11-year-old female who applied to our clinics for the treatment of her non-aesthetic and deviated intraoral view and discoloration of her gingiva, and the second patient was a 56-year-old female who applied for the extraction of her wisdom tooth. Extraoral examination in both patients revealed a diffuse PWS on the right side of their face over the cheek, extending from the midline. While the first patient had reddish skin, gingiva on right site her both jaws and lips, the second patient had only her upper jaw and lip. Because of the first patient’ age, the treatment postponed to her 20’, and the second patient did not accept any treatment. PWS is a rare and non-fatal condition; however, the unique appearance of these patients can lead to psychological problems especially in early ages.


Author(s):  
Jason E. Hale ◽  
Sumayya J. Almarzouqi ◽  
Michael L. Morgan ◽  
Andrew G. Lee

2016 ◽  
Vol 8 (1) ◽  
pp. 68
Author(s):  
Kazi Nilufar Moly ◽  
S.M. Abu Ahsan ◽  
Md. Shafiqul Lslam

<p>Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face (purple colored flat cutaneous haemangiomas ), typically in the ophthalmic (V1) and maxillary (V2) distributions of the trigeminal nerve. The hallmark of sturge weber syndrome is a facial cutaneous venous dilation, also referred to as a nevus flammeus or port wine stain (PWS). Because of the rarity, we report here a one &amp; half year old male child who presented with features of the Sturge Weber Syndrome on both side of face.</p>


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