Primary Cardiac Synovial Sarcoma Originating from the Mitral Valve Causing Left Ventricular Outflow Tract Obstruction

2015 ◽  
Vol 18 (3) ◽  
pp. 112 ◽  
Author(s):  
Altin Veshti ◽  
Edvin Mihal Prifti ◽  
Majlinda Ikonomi

An 11-year-old boy was admitted due to different episodes of syncope and convulsion. Echocardiogram revealed a mass of 2 × 4 cm originating from the mitral subvalvular apparatus and more precisely from the antero-lateral papillary muscle, protruding in the left ventricle outflow tract causing intermittent obstruction. The patient underwent surgical excision of the left sided mass. Pathology confirmed the diagnosis of primary synovial sarcoma. At 6 months after the operation a small mass in the left ventricle of 1 × 1 cm was detected. The patient underwent reoperation consisting in radical resection of the subvalvular apparatus and mitral valve replacement. Histology confirmed that the mass was a cardiac synovial sarcoma. At 1 year after surgery the patient is doing well.

2017 ◽  
Vol 2017 ◽  
pp. 1-4 ◽  
Author(s):  
Kelechukwu U. Okoro ◽  
Matthew D. Roby ◽  
David C. Sane ◽  
Robert E. Budin

Primary cardiac sarcoma is a rare malignant myocardial neoplasm that does not exhibit gender predominance or age predilection. The classification of these tumors includes several subtypes, of which synovial sarcoma is a rare manifestation. When present, these tumors portend a poor prognosis with high morbidity and mortality that is attributable to their inherent infiltrative capacity, especially in the absence of treatment. The general consensus for treatment is surgical excision and neoadjuvant chemotherapy and radiotherapy. In this report, a case of synovial sarcoma involving the left ventricular outflow tract and aortic valve is presented.


2007 ◽  
Vol 5 (3) ◽  
pp. 0-0
Author(s):  
Daina Liekienė ◽  
Virgilijus Lebetkevičius ◽  
Virgilijus Tarutis ◽  
Rimantas Karalius ◽  
Rita Sudikienė ◽  
...  

Daina Liekienė1, Virgilijus Lebetkevičius1, Virgilijus Tarutis2, Rimantas Karalius1, Rita Sudikienė2, Kęstutis Lankutis2, Giedrė Nogienė1, Alicija Dranenkienė1, Vytautas Sirvydis11 Vilniaus universiteto Širdies chirurgijos centras, Santariškių g. 2, LT-08661 Vilnius2 Vilniaus universiteto ligoninės Santariškių klinikų Širdies chirurgijos centras,Santariškių g. 2, LT-08661 VilniusEl paštas: [email protected] Subaortinės stenozės diagnozė apima didelį spektrą anatominių pakitimų – nuo paprastos membranos iki fibroraumeninio tunelio. Straipsnyje aprašoma reta subaortinė stenozė, sukelta dviburio vožtuvo priekinės burės ir papilinio raumens anomalijos. Trys pacientai, operuoti dėl subaortinės stenozės, sukeltos dviburio vožtuvo anomalijos, dviem atlikta dviburio vožtuvo plastika ir kairiojo skilvelio infundibulinės dalies raumenų rezekcija. Vienam ligoniui atliktas mitralinio vožtuvo (MV) protezavimas ir kairiojo skilvelio infundibulinės dalies raumenų rezekcija.Dviburį vožtuvą išsaugančias operacijas dažniau pavyksta padaryti, kai dviburio vožtuvo yda yra antrinė liga. Dviburio vožtuvo plastika galima rečiau, jei anomalaus dviburio vožtuvo audiniai siaurina kairiojo skilvelio infundibulinę dalį. Pagrindiniai žodžiai: subaortinė stenozė, dviburio vožtuvo anomalija, kairiojo skilvelio išvarymo trakto obstrukcija Subaortic stenosis and mitral valve anomaly: surgical treatment aspects Daina Liekienė1, Virgilijus Lebetkevičius1, Virgilijus Tarutis2, Rimantas Karalius1, Rita Sudikienė2, Kęstutis Lankutis2, Giedrė Nogienė1, Alicija Dranenkienė1, Vytautas Sirvydis11 Vilnius University, Cardiac Surgery Centre, Santariškių str. 2, LT-08661 Vilnius, Lithuania2 Vilnius University Hospital „Santariškių klinikos“, Cardiac Surgery Centre,Santariškių str. 2, LT-08661 Vilnius, LithuaniaE-mail: [email protected] The diagnosis of subaortic stenosis contains a broad spectrum of anatomical changes varying from discrete membrane to fibromuscular tunnel. We review a rare subaortic stenosis caused by anomaly of mitral valve anterior leaflet and papillary muscle. We review three patients who underwent surgery because of subaortic stenosis caused by anomalous mitral valve. Two patients underwent mitral valve plastic and resection of the left ventricular outflow tract muscles. One patient underwent mitral valve replacement and resection of the left ventricular outflow tract muscles.Valve preserving operations are more easy to perform when mitral valve disease is a comorbidity. Mitral valvoplasty is more complicated to perform when the mass of anomalous mitral valve obstructs the outflow tract of the left ventricle. Key words: subaortic stenosis, anomalous mitral valve, left ventricle outflow tract obstruction


2005 ◽  
Vol 15 (S1) ◽  
pp. 27-36 ◽  
Author(s):  
Alfred Asante-Korang ◽  
Robert H. Anderson

The previous reviews in this section of our Supplement1,2 have summarized the anatomic components of the ventriculo-arterial junctions, and then assessed the echocardiographic approach to the ventriculo-arterial junction or junctions as seen in the morphologically right ventricle. In this complementary review, we discuss the echocardiographic assessment of the comparable components found in the morphologically left ventricle, specifically the outflow tract and the arterial root. We will address the echocardiographic anatomy of the aortic valvar complex, and we will review the causes of congenital arterial valvar stenosis, using the aortic valve as our example. We will also review the various lesions that, in the outflow of the morphologically left ventricle, can produce subvalvar and supravalvar stenosis. We will then consider the salient features of the left ventricular outflow tract in patients with discordant ventriculo-arterial connections, and double outlet ventricles. To conclude the review, we will briefly address some rarer anomalies that involve the left ventricular outflow tract, showing how the transesophageal echocardiogram is used to assist the surgeon preparing for repair. The essence of the approach will be to consider the malformations as seen at valvar, subvalvar, or supravalvar levels,1 but we should not lose sight of the fact that aortic coarctation or interruption, hypoplasia of the left heart, and malformations of the mitral valve are all part of the spectrum of lesions associated with obstruction to the left ventricular outflow tract. These additional malformations, however, are beyond the scope of this review.


2021 ◽  
Vol 14 (3) ◽  
pp. e240010
Author(s):  
Paulina M Conradi ◽  
Ramon B van Loon ◽  
M Louis Handoko

We report a case of a 73-year-old female patient, who was admitted to the coronary care unit due to chest pain, malaise and near syncope. During physical examination, the patient was hypotensive and there were signs of left-sided heart failure and a loud systolic murmur. Echocardiogram showed apical ballooning with dynamic left ventricular outflow tract obstruction, based on systolic anterior motion of the mitral valve with important mitral valve regurgitation. In the acute setting, the cardiogenic shock was treated cautiously with fluid resuscitation and intravenous metoprolol, resulting in direct stabilisation of her haemodynamic condition. As a codiagnosis, there was a significant stenosis of left anterior descending artery, which was treated successfully by percutaneous coronary intervention with drug eluting stents. During follow-up, left ventricular function normalised, and the left ventricular outflow tract obstruction, systolic anterior motion of mitral valve and related mitral regurgitation all resolved.


2000 ◽  
Vol 17 (2) ◽  
pp. 177-180 ◽  
Author(s):  
RAFFAELE CALABRO ◽  
GIUSEPPE SANTORO ◽  
CARLO PISACANE ◽  
BERARDO SARUBBI ◽  
GABRIELLA FARINA ◽  
...  

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