A Rare Case of Proboscis Lateralis with Median Cleft Lip

2010 ◽  
Vol 47 (5) ◽  
pp. 553-556 ◽  
Author(s):  
Yoshiaki Sakamoto ◽  
Tatsuo Nakajima ◽  
Junpei Miyamoto
Keyword(s):  
Rare Case ◽  
Cleft Lip ◽  
Median Cleft ◽  
Proboscis Lateralis

New Classification Scheme of Proboscis Lateralis Based on a Review of 50 Cases

2012 ◽  
Vol 49 (2) ◽  
pp. 201-207 ◽  
Author(s):  
Yoshiaki Sakamoto ◽  
Junpei Miyamoto ◽  
Hideo Nakajima ◽  
Kazuo Kishi
Keyword(s):  
Cleft Lip ◽  
Classification Scheme ◽  
The Other ◽  
New Classification ◽  
Group Vi ◽  
Term Survival ◽  
Group V ◽  
Group I ◽  
Median Cleft ◽  
Proboscis Lateralis

Background Among congenital nasal deformities, proboscis lateralis is one of the rarest. Boo-Chai classified proboscis lateralis into four groups. Recently, we encountered a new case of proboscis lateralis with median cleft lip. We noticed that this classification had not been considered according to convalescence and embryologics, and further refinement seemed to be needed. Methods We reviewed all cases of proboscis lateralis reported in English through 2009 and classified them by intercanthal distance. Results A total of 34 studies involving 50 cases were reviewed. Six cases were identified as having normal intercanthal distance. Three of them presented nose abnormalities and fit Boo-Chai group II category. The other three were consistent with group I. Hypertelorism was observed in 27 cases and was further divided into two groups based on the occurrence of a frontal encephalocele. Seventeen cases without a frontal encephalocele were compatible with Boo-Chai groups III and IV. The other 10 cases associated with a visible encephalocele had encephalopathy; most died at an early age, and long-term survival cases suffered developmental delay and mental retardation. Seventeen cases were defined as hypotelorism, and all cases also presented as holoprosencephaly. Conclusions The redefined classification contains two new groups: group V as hypertelorism with encephalocele and group VI as hypotelorism. A new classification scheme is proposed as not only convenient for clinical application but also embryologically accurate.

Custom-Made Nasal Retainer Using Latex Nelaton Urine Catheter After the Cheiloplasty

2021 ◽  
pp. 105566562199267
Author(s):  
Joon Seok Oh ◽  
Jeehyeok Chung ◽  
Jeong Hyun Ha ◽  
Hyo Kyung Yoo ◽  
Sukwha Kim
Keyword(s):  
Surgical Procedures ◽  
Cleft Lip ◽  
Custom Made ◽  
Median Cleft

Nasal retainers are common tools used in managing patients with cleft lip. The significance of nasal retainer in preventing nostril collapse or stenosis to maintain a symmetrical nose after the surgical procedures is already well known. We came up with a way to create a nasal retainer using a latex nelaton catheter. Custom-made nasal retainer using latex nelaton catheter was used postoperatively on a 10-month-old infant with median cleft lip after cheiloplasty. In postoperative day 7, her nostrils were large enough for premade silicone nasal retainer to fit. She was discharged with instructions given to use the retainer for 6 months. Custom-made nasal retainer can be used as an alternative to premade nasal retainers for patients with wide columella or small nostril cavities, or who cannot afford premade retainers.

Ectrodactyly, Ectodermal dysplasia, and Cleft lip-palate (EEC) syndrome without clefting: A rare case report

2012 ◽  
Vol 18 (2) ◽  
Author(s):  
Dipali Malvankar ◽  
S Sacchidanand ◽  
M Mallikarjun
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Cleft Lip ◽  
Ectodermal Dysplasia ◽  
Eec Syndrome ◽  
Rare Case Report ◽  
Cleft Lip Palate

Repair of Median Cleft Lip

2020 ◽  
pp. 147-151
Author(s):  
Wen-yan Wu ◽  
Jian-min Yao
Keyword(s):  
Cleft Lip ◽  
Median Cleft

scholarly journals Multiple Cephalic Malformations in a Calf

Animals ◽  
2020 ◽  
Vol 10 (9) ◽  
pp. 1532
Author(s):  
Di Muro G. ◽  
Cagnotti G. ◽  
Bellino C. ◽  
Capucchio M.T. ◽  
Colombino E. ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Congenital Malformations ◽  
Cleft Lip ◽  
Congenital Abnormalities ◽  
Presumptive Diagnosis ◽  
Intracranial Lesion ◽  
Median Cleft ◽  
The Central Nervous System ◽  
Similar Combination ◽  
Neurologic Findings

Congenital malformations of the central nervous system (CNS) can affect the CNS alone or the CNS and craniofacial structures. Here, we report an unusual and complex congenital cephalic malformation observed in a 3-day-old male crossbreed calf. Clinical examination disclosed a dome-shaped cranial vault, a flat face with a short snout, a median cleft lip, and increased intraorbital distance. The frontal region of the head was remarkable for a fluctuant, sac-like protrusion covered with haired skin. Neurologic findings suggested a multifocal intracranial lesion affecting the prosencephalon and the central vestibular system. While pathological and histopathological findings posited for a presumptive diagnosis of either hydranencephaly or holoprosencephaly associated with multiple congenital facial abnormalities, not all the findings could be definitely attributed to either of the two encephalic malformations alone. To our knowledge, a similar combination of severe congenital abnormalities affecting both the CNS and the craniofacial structures has not been reported in calves to date.

Median Cleft of the Upper Lip: A Rare Case

2010 ◽  
Vol 47 (6) ◽  
pp. 642-644 ◽  
Author(s):  
Nima P. Patel ◽  
M. Devi Prasad Tantri
Keyword(s):  
Rare Case ◽  
Upper Lip ◽  
Median Cleft

True Median Cleft Lip—15 Years of Review and Prevalence

2020 ◽  
Vol 57 (8) ◽  
pp. 1051-1054
Author(s):  
Muhammad Izzuddin Hamzan ◽  
Wan Azman Wan Sulaiman
Keyword(s):  
Surgical Treatment ◽  
Plastic Surgery ◽  
Cleft Lip ◽  
Descriptive Study ◽  
Definitive Treatment ◽  
Associated Anomalies ◽  
Facial Cleft ◽  
Surgical Protocol ◽  
Median Cleft

Objectives: The author presents 4 cases and attempts to analyze the prevalence of true median cleft lip (MCL) in one center. Embryology, associated anomalies, and surgical treatment are discussed. Design: A retrospective descriptive study. Setting: Hospital Universiti Sains Malaysia. Participants: All patients with congenital facial cleft deformities from 2005 to 2019 were retrieved from the Plastic Surgery OR Registry. All characteristics in interest were individually tabulated and evaluated. Four cases were reviewed and discussed. Outcome: Prevalence of true MCL. Results: Out of the 494 patients included in the study, only 4 (0.81%) were affected with a median cleft, and the prevalence of true median cleft was hence determined to be 3 (0.61%) among the cleft population. Conclusion: The prevalence of the true MCL is rare which makes it hard to categorize these clefts, and the surgical protocol needs to be established for the definitive treatment.

scholarly journals Presurgical naso-alveolar molding paired with cheiloplasty to treat median cleft lip deformity in holoprosencephaly

2020 ◽  
Vol 7 (1) ◽  
pp. 50-53
Author(s):  
Satoshi Takagi ◽  
Ayumu Tsukamoto ◽  
Yoshihisa Kawakami ◽  
Sachio Tamaoki ◽  
Hiroyuki Ohjimi
Keyword(s):  
Cleft Lip ◽  
Median Cleft

Lobar Holoprosencephaly with a Median Cleft: Case Report

2009 ◽  
Vol 46 (5) ◽  
pp. 549-554 ◽  
Author(s):  
Elżbieta Gawrych ◽  
Joanna Janiszewska-Olszowska ◽  
Anna Walecka ◽  
Maria Syryńska ◽  
Hanna Chojnacka
Keyword(s):  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Brain Abnormalities ◽  
Facial Deformity ◽  
Unique Case ◽  
Craniofacial Malformations ◽  
Live Births ◽  
Facial Defects ◽  
Median Cleft

Holoprosencephaly is a congenital abnormality of the prosencephalon associated with median facial defects. Its frequency is 1 in 250 pregnancies and 1 in 16,000 live births. The degree of facial deformity usually correlates with the severity of brain malformation. Early mortality is prevalent in severe forms. This report presents a child with lobar holoprosencephaly accompanied by median cleft lip and palate. The treatment and 9 months’ follow-up are presented. This unique case shows that holoprosencephaly may present different manifestations of craniofacial malformations, which are not always parallel to the severity of brain abnormalities. Patients with mild to moderate brain abnormalities may survive into childhood and beyond.

Sign in / Sign up

Export Citation Format

Share Document