Right-sided Aortic Arch Associated with Congenital Heart Disease

Abstract Purpose Altered cerebral hemodynamics are involved in changes in head biometry in fetuses with congenital heart disease (CHD). We compared head growth in different CHD groups with published normative values and investigated whether CHD groups differ from each other in terms of head circumference (HC) development over gestational age (GA). Materials and Methods Retrospective cohort study consisting of 248 CHD fetuses. Subgroups were generated according to the expected ascending aorta oxygen saturation: Low placental blood content (BC) and therefore low oxygen delivery to the brain (group 1: n = 108), intermediate placental and systemic BC due to intracardiac mixing of blood (group 2: n = 103), high placental BC (group 3: n = 13) and low placental BC and low oxygen delivery to the brain without mixing of blood (group 4: n = 24). Furthermore, group 1 was divided into antegrade (n = 34) and retrograde (n = 74) flow through the aortic arch. Comparisons were made at a GA of 22, 30 and 38 weeks. Results Estimated values of zHC (z-score transformed) were not significantly different between the four CHD groups at the three time points in gestation (all p > 0.05). Within group 1 fetuses with retrograde aortic arch flow showed a significant negative association between HC and GA compared to reference values (b = –0.054, p < 0.001) and had significantly lower zHC values at 38 weeks (–0.836) compared to fetuses with antegrade flow (0.366, p = 0.009). Conclusion Our data do not confirm that CHD fetuses in general have a significantly smaller HC. HC becomes smaller throughout gestation depending on the direction of aortic arch flow.

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Autotissue Matrix Patch for Aortic Arch Reconstruction in Congenital Heart Disease—Histology of a Series of Human Explants

10.1055/s-0039-1678839 ◽

2019 ◽

Author(s):

J. Cleuziou ◽

K. Vitanova ◽

M. Sigler

Keyword(s):

Congenital Heart Disease ◽

Heart Disease ◽

Aortic Arch ◽

Congenital Heart ◽

Aortic Arch Reconstruction ◽

Arch Reconstruction ◽

Human Explants ◽

Matrix Patch

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Congenital heart disease and aortic arch variants associated with mutation in PHOX2B

Genetics in Medicine ◽

10.1038/gim.2018.34 ◽

2018 ◽

Vol 20 (12) ◽

pp. 1538-1543 ◽

Cited By ~ 4

Author(s):

Rachel C Lombardo ◽

Aleksey Porollo ◽

James F Cnota ◽

Robert J Hopkin

Keyword(s):

Congenital Heart Disease ◽

Heart Disease ◽

Aortic Arch ◽

Congenital Heart

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Isolated Interrupted Aortic Arch- A Complex Congenital heart disease

Cardiovascular Journal ◽

10.3329/cardio.v4i1.9400 ◽

1970 ◽

Vol 4 (1) ◽

pp. 102-104

Author(s):

A Shariar ◽

MA Huq ◽

NU Zakia ◽

M Salim ◽

SA Islam

Keyword(s):

Congenital Heart Disease ◽

Heart Disease ◽

Aortic Arch ◽

Congenital Heart ◽

Septal Defect ◽

Interrupted Aortic Arch ◽

Cardiac Anomaly ◽

Complex Congenital Heart Disease ◽

Type B ◽

Left Carotid Artery

Interrupted Aortic Arch (lAA) is the absence or discontinuation of a portion of the aortic arch. There are three types of Interrupted Aortic Arch,and they are classified according to the site of the interruption. lsolated IAA appears commonly in type B lAA,where the interruption occurs between the left carotid artery and the left subclavian artery.In such case there is no associated cardiac anomaly and the patient may not exhibit lethal form of presentation unless there is duct dependent circulation or ventricular septal defect. lsolated interrupted arch is relatively rare congenital anomaly and very few cases were reported in literature so far. Keywords: lnterrupted aortic arch; Complex congenital heart disease. DOI: http://dx.doi.org/10.3329/cardio.v4i1.9400 Cardiovasc. J. 2011; 4(1): 102-104

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Reconstruction of the aortic arch in an adolescent female with complex congenital heart disease

Cardiology in the Young ◽

10.1017/s1047951100002122 ◽

1994 ◽

Vol 4 (2) ◽

pp. 164-167

Author(s):

Rajiv Verma ◽

Delores Danilowicz ◽

Stephen Colvin

Keyword(s):

Congenital Heart Disease ◽

Heart Disease ◽

Aortic Arch ◽

Congenital Heart ◽

Complex Congenital Heart Disease ◽

Adolescent Female ◽

Ventricular Septal Defects ◽

Postoperative Course ◽

Septal Defects ◽

Complete Repair

AbstractCoarctations of the aortic arch are rare, and when found, they are often associated with other complex congenital heart disease. An adolescent female with multiple coarctations of the aortic arch and ventricular septal defects underwent complete repair, entailing replacement of the aortic arch with a homograft and closure of the ventricular septal defects. The postoperative course was complicated by a tear in the homograft, possibly related to sepsis. After its resolution, her hemodynamic results remain excellent.

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Tracheal compression due to an elongated aortic arch in patients with congenital heart disease: evaluation using multidetector-row CT

Pediatric Radiology ◽

10.1007/s00247-009-1319-1 ◽

2009 ◽

Vol 39 (10) ◽

pp. 1048-1053 ◽

Cited By ~ 11

Author(s):

Noriko Watanabe ◽

Yasunobu Hayabuchi ◽

Miki Inoue ◽

Miho Sakata ◽

Manal Mohamed Helmy Nabo ◽

...

Keyword(s):

Congenital Heart Disease ◽

Heart Disease ◽

Aortic Arch ◽

Congenital Heart ◽

Multidetector Row Ct ◽

Tracheal Compression ◽

Multidetector Row

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Assessment of CT angiographic findings in comparison with echocardiography findings of chest among patients with aortic arch anomalies

Monaldi Archives for Chest Disease ◽

10.4081/monaldi.2019.1120 ◽

2019 ◽

Vol 89 (3) ◽

Author(s):

Hussein Soleimantabar ◽

Sofia Sabouri ◽

Leila Khedmat ◽

Samira Salajeghe ◽

Behzad Memari ◽

...

Keyword(s):

Congenital Heart Disease ◽

Heart Disease ◽

Aortic Arch ◽

Ct Angiography ◽

Transthoracic Echocardiography ◽

Congenital Heart ◽

Acquisition Time ◽

Aortic Arch Anomalies ◽

Imaging Center ◽

Angiographic Findings

The objective of this study was to examine the findings of computed tomographic (CT) angiography in patients with aortic arch anomalies in comparison with transthoracic echocardiography findings who referred to a private imaging center in Tehran during 2009-2012. The cases included 203 patients with clinical symptoms or echocardiogram of congenital heart disease to assess the presence of aortic arch anomalies among patients referred to imaging center. This study is a retrospective study based on the CT angiographic findings in comparison with transthoracic echocardiography findings of chest among patients with aortic arch anomalies. In this study, 203 patients with congenital anomalies were enrolled in the study, among those, 107 patients were men and 96 were female. The most common anomaly of the aortic arch was found to be coarctation (19.7%), followed by right sided arch with mirror image branching (19.2%). Furthermore, the most common cardiac anomalies associated with aortic arch anomalies were VSD, PA and PDA. The sensitivity and specificity of transthoracic echocardiography in the diagnosis of aortic arch anomalies was 59% and 100% in comparison with CT angiography. In addition, the agreement between the two methods (kappa) in the diagnosis of aortic arch anomalies was 0.72. But, transthoracic echocardiography is the first diagnostic method for patients with congenital heart disease. In some patients, the ability of this method was limited to the detection of coronary artery anomalies and thoracic vessels. Therefore, CT is used for morphological evaluation of congenital heart disease (CHD) due to its main advantages including fast acquisition time, large anatomical coverage, high speed, and great spatial resolution. Moreover, CT is essential for proper evaluation of CHD regarding its high spatial and temporal resolution.

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