scholarly journals Desmoplastic Fibroma of the Pediatric Cranium: An Aggressive Skull Tumor with Local Recurrence

2016 ◽  
Vol 56 (2) ◽  
pp. 85-88 ◽  
Author(s):  
Takao KOISO ◽  
Ai MUROI ◽  
Tetsuya YAMAMOTO ◽  
Noriaki SAKAMOTO ◽  
Akira MATSUMURA
2021 ◽  
Author(s):  
Kai Zhang ◽  
Wu Weibin ◽  
Guan Jiexia ◽  
Wu Yonghui ◽  
Chen Huiguo ◽  
...  

Abstract Background: Desmoplastic fibroma (DF) is a rare, benign tumor. The most common sites are the long tubular bones and mandible. Although generally considered a benign tumor, it can invade surrounding tissues and has a high rate of local recurrence after incomplete surgical excision. However, there is currently no stantard treatment. Here we present a novel case of DF in the left 6th rib in a 35-year-old man.Case presentation: The man presented to our center with left chest pain and swelling. Enhanced computed tomography (CT) showed a 4.5×2.0 cm mass on the left 6th rib with pathological fracture.Wide resection was performed. Open biopsy revealed that the tumor destroyed medullary cavity and partially broke through the bone cortex. Pathologically, the tumor was composed of spindle-shaped cells arranging in a woven pattern on a backgroung of abundant collagenous fiber. No β-catenin were detected. Based on the pathological and radiological findings, a final diagnosis of DF was made. No postoperative adjuvant treatments were administerded. Fortunately, there was no evidence of recurrence 22 months after surgery. Conclusions: DF originated from rib is a kind of extremly rare benign tumor but locally aggressive and show unique biologically features. Wide resection or total resection can effectively reduce the risk of local recurrence when compared with curettage. Rarity of the tumor favors documentation in literature.


2021 ◽  
Author(s):  
Kai Zhang ◽  
Wu Weibin ◽  
Guan Jiexia ◽  
Wu Yonghui ◽  
Chen Huiguo ◽  
...  

Abstract Background: Desmoplastic fibroma (DF) is a rare, benign tumor. The most common sites are the long tubular bones and mandible. Although generally considered a benign tumor, it can invade surrounding tissues and has a high rate of local recurrence after incomplete surgical excision. However, there is currently no stantard treatment. Here we present a novel case of DF in the left 6th rib in a 35-year-old man.Case presentation: The man presented to our center with left chest pain and swelling. Enhanced computed tomography (CT) showed a 4.5×2.0 cm mass on the left 6th rib with pathological fracture. Wide resection was performed. Open biopsy revealed that the tumor destroyed medullary cavity and partially broke through the bone cortex. Pathologically, the tumor was composed of spindle-shaped cells arranging in a woven pattern on a backgroung of abundant collagenous fiber. No β-catenin were detected. Based on the pathological and radiological findings, a final diagnosis of DF was made. No postoperative adjuvant treatments were administerded. Fortunately, there was no evidence of recurrence 22 months after surgery. Conclusions: DF originated from rib is a kind of extremly rare benign tumor but locally aggressive and show unique biologically features. Wide resection or total resection can effectively reduce the risk of local recurrence when compared with curettage. Rarity of the tumor favors documentation in literature.


2020 ◽  
Author(s):  
Azadehzeinab Titidej ◽  
Maryam Jolehar

Desmoplastic fibroma is a rare, benign fibrous tumor of bone which is locally aggressive. The mandible is the most prevalent affected of the facial bones. Nevertheless, reports of desmoplastic fibroma affecting the mandible are seldom in the literature. It causes bone destruction and has a high tendency for local recurrence. In this case report, we report a case of desmoplastic fibroma which is located in mandibular angle and extended to coronoid process, in 20-year-old female patient. © 2019 Tehran University of Medical Sciences. All rights reserved. Acta Med Iran 2019;57(7):456-460.


2004 ◽  
Vol 171 (4S) ◽  
pp. 14-14
Author(s):  
Dieter R. Echtle ◽  
Elizabeth M. Mueller ◽  
Detlef H. Frohneberg

JMS SKIMS ◽  
2012 ◽  
Vol 15 (1) ◽  
pp. 76-77
Author(s):  
Mohd Athar ◽  
K S Sodhi ◽  
S Kala ◽  
R K Maurya ◽  
S Chauhan ◽  
...  

Adenoid cystic carcinoma is a relatively uncommon tumour of salivary, glands and is characterised by a prolonged clinical course and a fatal outcome. It was first described as `cylindroma' by Billroth in 1859. Half of these tumors occur in glandular tissues other than the major salivary glands; principally in the hard palate, but they can also arise in the tongue and minor salivary glands. Unusual locations include the external auditory canal, nasopharynx, lacrimal glands, breast, vulva, esophagus, cervix and Cowper glands. The long natural history of this tumor and its tendency for local recurrence are well known. JMS 2012;15(1):76-77.


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