Distal aortopulmonary window with aortic origin of the right pulmonary artery and interruption of the aortic arch (Berry syndrome): diagnosis by MR imaging.

1991 ◽  
Vol 157 (4) ◽  
pp. 835-836 ◽  
Author(s):  
S J Yoo ◽  
H Y Choi ◽  
I S Park ◽  
C Y Hong ◽  
M G Song ◽  
...  
Keyword(s):  
Mr Imaging ◽  
Pulmonary Artery ◽  
Aortic Arch ◽  
Aortopulmonary Window ◽  
Syndrome Diagnosis ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Berry Syndrome

scholarly journals Berry syndrome: a case report and literature review

2021 ◽  
Vol 21 (1) ◽  
Author(s):  
Wen-jing Bi ◽  
Yang-jie Xiao ◽  
Yue-jia Liu ◽  
Yang Hou ◽  
Wei-dong Ren
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Ductus Arteriosus ◽  
Main Pulmonary Artery ◽  
Ventricular Septum ◽  
Aortopulmonary Window ◽  
Intact Ventricular Septum ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Berry Syndrome

Abstract Background Berry syndrome, a rare combination of cardiac anomalies, consists of aortopulmonary window (APW); aortic origin of the right pulmonary artery; interrupted aortic arch (IAA) or hypoplastic aortic arch or coarctation of the aorta; and an intact ventricular septum. There is lack of review articles that elucidate the clinical features, diagnosis, treatment, and outcomes of Berry syndrome. This publication systematically reviews the 89 cases published since 1982 on Berry syndrome. Case presentation A 38-year-old woman presented with a loud murmur and cyanosis. Transthoracic echocardiography demonstrated a severely dilated aorta and main pulmonary artery with a large intervening defect. Distal to the APW, the ascending aorta gave rise to the right pulmonary artery. Additionally, a type A IAA, an intact ventricular septum, and a large patent ductus arteriosus were revealed. Computed tomography angiography with 3-dimensional reconstruction confirmed above findings. This is the first report of a patient of this age with Berry syndrome who did not undergo surgery. Conclusions Berry syndrome is a rare but well-identified and surgically correctable anomaly. Patients with Berry syndrome should be followed up for longer periods to better characterize long-term outcomes.

scholarly journals A Rare Case of Adult Aortopulmonary Window Combined with Anomalous Origin of the Right Pulmonary Artery from the Aorta Leading to Eisenmenger Syndrome

2021 ◽  
Vol 49 (1) ◽  
pp. 030006052098465
Author(s):  
Mingyue Cui ◽  
Binfeng Xia ◽  
Heru Wang ◽  
Haihui Liu ◽  
Xia Yin
Keyword(s):  
Pulmonary Artery ◽  
Rare Case ◽  
Congenital Heart ◽  
Respiratory Tract Infections ◽  
Anomalous Origin ◽  
Aortopulmonary Window ◽  
Eisenmenger Syndrome ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Tract Infections

Aortopulmonary window is a rare congenital heart disease that can increase pulmonary vascular resistance, exacerbate left-to-right shunt and lead to heart failure and respiratory tract infections. Most patients die during childhood. We report a 53-year-old male patient with a large aortopulmonary window combined with anomalous origin of the right pulmonary artery from the aorta, with Eisenmenger syndrome and without surgery.

scholarly journals A rare complication of myocardial ischaemia following single-stage repair in a case of Berry syndrome

2020 ◽  
Vol 31 (4) ◽  
pp. 576-577
Author(s):  
Mai Dinh Duyen ◽  
Maruti Y Haranal ◽  
Jeswant Dillon ◽  
Sivakumar Sivalingam
Keyword(s):  
Myocardial Ischaemia ◽  
Rare Complication ◽  
Aortopulmonary Window ◽  
Intact Ventricular Septum ◽  
Cardiac Lesion ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Hypoplastic Aortic Arch ◽  
Berry Syndrome ◽  
Repair Techniques

Abstract Berry syndrome is a rare congenital cardiac lesion consisting of a distal aortopulmonary window, the aortic origin of the right pulmonary artery (PA), intact ventricular septum and an interrupted or hypoplastic aortic arch. Different repair techniques have been described in the literature. We report a case of Berry syndrome, in whom myocardial ischaemia developed following direct implantation of the right PA to the main PA, which was resolved using an interposition tube graft.

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