Plexiform Neurofibroma during Pregnancy, a Case Report from College Teaching Hospital, Kohalpur

Plexiform neurofibromas are rare variant (30%) of neurofibromatosis type 1 (NF-1) in which neurofibromas arise as large deforming masses from multiple nerve endings involving also connective tissues and skin folds. We report a case of 24 years old female, second gravida and one parity with diagnosis of plexiform neurofibromatosis made in previous pregnancy with remission of symptoms after pregnancy and accentuation during second pregnancy with positive pregnancy outcome.

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Plexiform Neurofibroma of Clitoris

Journal of Pediatric Genetics ◽

10.1055/s-0037-1602789 ◽

2017 ◽

Vol 06 (04) ◽

pp. 244-246 ◽

Cited By ~ 1

Author(s):

Dhanya Yesodharan ◽

Bindu Sudarsanan ◽

Annie Jojo ◽

Mohan Abraham ◽

Nisha Bhavani ◽

...

Keyword(s):

Differential Diagnosis ◽

Neurofibromatosis Type 1 ◽

Plexiform Neurofibroma ◽

Neurofibromatosis Type ◽

Plexiform Neurofibromatosis

AbstractThe most frequent genital presentation of neurofibromatosis in females is clitoromegaly. We report a case of a 5-year-old girl with neurofibromatosis type 1 with clitoral plexiform neurofibromatosis. Clitoroplasty was done, and the histopathology confirmed the diagnosis. Though rare, plexiform neurofibroma of clitoris should always be considered as a differential diagnosis in children with clitoromegaly before embarking on detailed investigations.

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Rare triad of periampullary carcinoid, duodenal gastrointestinal stromal tumor and plexiform neurofibroma at hepatic hilum in neurofibromatosis type 1: a case report

BMC Cancer ◽

10.1186/s12885-017-3567-z ◽

2017 ◽

Vol 17 (1) ◽

Cited By ~ 5

Author(s):

Nihed Abdessayed ◽

Rahul Gupta ◽

Sarra Mestiri ◽

Ahlem Bdioui ◽

Mounir Trimech ◽

...

Keyword(s):

Case Report ◽

Gastrointestinal Stromal Tumor ◽

Neurofibromatosis Type 1 ◽

Plexiform Neurofibroma ◽

Neurofibromatosis Type ◽

Stromal Tumor ◽

Hepatic Hilum

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Aggresive Mass Excision Through Nasolabial Fold Areain the Treatment of Facial Neurofibromatosis : Case Report

Jurnal Plastik Rekonstruksi ◽

10.14228/jpr.v1i1.32 ◽

1970 ◽

Vol 1 (1) ◽

Author(s):

Siti Handayani ◽

Kristaninta Bangun ◽

Fernita Leo Soetjipto Soepodo

Keyword(s):

Case Report ◽

Rare Disease ◽

Male Patient ◽

Neurofibromatosis Type 1 ◽

Neurofibromatosis Type ◽

Special Consideration ◽

Nasolabial Fold ◽

Von Recklinghausen’S Disease ◽

Plexiform Neurofibromatosis

Neurofibromatosis type 1 is a rare disease which can manifest itself by the development of plexiform neurofibromatosis, with craniofacial deformities. In this paper, we propose special consideration in excision nasolabial fold mass to help lifting procedures in neurofibromatosis patients. We are reporting two case, both presented with von Recklinghausen’s disease, a 21 years old male patient with neurofibromatosis in his right hemifacial for which he had been operated on five times previously at other center, and a 24 years old male with neurofibromatosis in his left hemifacial. After several stages of reconstruction which started with nasolabial fold mass excision, the result was satisfactory, by using the multiple stage repair, it was done until the end result is similar to anatomical form. The mass debulking procedures for these patients, which started with Nasolabial Fold mass excisison are continued with durable lifting procedures. This method gives results a satisfactory lifting procedure.

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