scholarly journals Eight and a Half Syndrome: A Rare Case of Pontine Infarction

2021 ◽  
Vol 13 (2) ◽  
pp. 230-233
Author(s):  
Akkayasamy Kowsalya

Introduction: This case report describes “one-and-a-half” syndrome with supranuclear facial palsy. Case: 39 years old male hypertensive patient presented with right facial nerve palsy, internuclear ophthalmoplegia and conjugate gaze palsy. Neuroimaging showed acute posterior pontine infarct at medial longitudinal fasciculus, paramedian pontine  reticular formation, abducens nerve nucleus and seventh nerve fascicular zone. Observation: “One-and-a-half”syndrome is characterized by a lateral gaze palsy in one direction and internuclear ophthalmoplegia in the other. Our patient had Right sided one and a half syndrome along with the right facial nerve palsy.   Conclusion: Eight and a half syndrome is a rare manifestation of pontine infarction.

2008 ◽  
Vol 48 (2) ◽  
pp. 135-138
Author(s):  
Katsuhiko Ogawa ◽  
Masaki Tougou ◽  
Minoru Oishi ◽  
Satoshi Kamei ◽  
Tomohiko Mizutani

2016 ◽  
Vol 88 ◽  
pp. 689.e5-689.e8 ◽  
Author(s):  
Tej D. Azad ◽  
Anand Veeravagu ◽  
Carleton Eduardo Corrales ◽  
Kevin K. Chow ◽  
Nancy J. Fischbein ◽  
...  

2019 ◽  
Vol 47 (8) ◽  
pp. 4014-4018 ◽  
Author(s):  
Bo Zhang ◽  
Yunpeng Hao ◽  
Yanfeng Zhang ◽  
Nuo Yang ◽  
Hang Li ◽  
...  

Background Kawasaki disease (KD) is an acute multisystem vasculitic syndrome that predominantly affects infants and young children. Neurological complications are rare in patients with KD and the diagnosis is challenging. We report a case of KD that manifested as bilateral facial nerve palsy and meningitis. Case report A 6-month-old boy presented with a 10-day history of fever. Four days before admission, the patient developed a rash, conjunctival injection, perioral and perianal excoriation, and bilateral facial nerve palsy. Brain magnetic resonance imaging was normal. Echocardiography showed dilated coronary arteries and coronary artery aneurysms. A cerebrospinal fluid examination showed an elevated leukocyte count. A diagnosis of KD was made, and the patient was treated with gamma globulin and aspirin. The patient’s fever subsided on the following day and the right-sided facial nerve palsy was relieved 1 month later. An 18-month follow-up showed that the left-sided facial nerve palsy persisted and the patient’s condition remained stable. Conclusion KD manifesting as bilateral facial nerve palsy and meningitis is extremely rare. Clinicians should be aware of this condition, and early diagnosis and appropriate treatment should be emphasized.


2003 ◽  
Vol 26 (2) ◽  
pp. 207-209
Author(s):  
G. Aren

Mobius Syndrome is characterized by showing unilateral facial nerve palsy of the sixth and seventh nerves, lack of facial expression, inability to smile and to tightly close the right eyelids. In this report, a 7-year-old-boy with Mobius syndrome is presented. He had asymmetry of facial expression, anomalies of fingers and severe tooth decay. After dental treatment, the periodic re-care visits should be done according to the eruption pattern.


2007 ◽  
Vol 107 (5) ◽  
pp. 1039-1042 ◽  
Author(s):  
James K. Liu ◽  
Christina M. Sayama ◽  
Clough Shelton ◽  
Joel D. MacDonald

✓Some evidence in the literature supports the topical application of papaverine to the cochlear nerve to prevent internal auditory artery vasospasm and cochlear ischemia as a method of enhancing the ability to preserve hearing during acoustic neuroma surgery. The authors report a case of transient facial nerve palsy that occurred after papaverine was topically applied during a hearing preservation acoustic neuroma removal. A 58-year-old woman presented with tinnitus and serviceable sensorineural hearing loss in her right ear (speech reception threshold 15 dB, speech discrimination score 100%). Magnetic resonance imaging demonstrated a 1.5-cm acoustic neuroma in the right cerebellopontine angle (CPA). A retrosigmoid approach was performed to achieve gross-total resection of the tumor. During tumor removal, a solution of 3% papaverine soaked in a Gelfoam pledget was placed over the cochlear nerve. Shortly thereafter, the quality of the facial nerve stimulation deteriorated markedly. Electrical stimulation of the facial nerve did not elicit a response at the level of the brainstem but was observed to elicit a robust response more peripherally. There were no changes in auditory brainstem responses. Immediately after surgery, the patient had a House–Brackmann Grade V facial palsy on the right side. After several hours, this improved to a Grade I. At the 1-month follow-up examination, the patient exhibited normal facial nerve function and stable hearing. Intracisternal papaverine may cause a transient facial nerve palsy by producing a temporary conduction block of the facial nerve. This adverse effect should be recognized when topical papaverine is used during CPA surgery.


Author(s):  
Lham Dorjee ◽  
Manu C.B. ◽  
Suvamoy Chakraborty ◽  
Abijeet Bhatia

<p class="abstract">Tuberculosis (TB) of the temporal bone is a rare condition. Tubercular otomastoiditis presenting with Citelli’s abscess, facial nerve palsy and extensive bone destruction is an unusual condition. As far as we know this maybe the first reported case with the above diagnosis. A 26 year old male patient presented with chronic right ear discharge, decreased hearing and right side facial nerve palsy with tender fluctuant swelling in the right post aural region approximately 10×8 cm in dimension, posterior to the mastoid tip and extending into the occipital region, almost reaching up to the midline posteriorly. High resolution computed tomography (CT) scan of temporal bone and magnetic resonance imaging (MRI) of brain was done. He underwent right side mastoid exploration and drainage of the abscess under general anaesthesia. The specimens sent for investigations revealed acid fast bacilli suggestive of <em>Mycobacterium tuberculosis</em> and the patient was started on anti-tubercular therapy. In all cases of long-standing chronic otitis media (COM) especially in those with complications, possibility of TB should be ruled out. High index of suspicion is needed for early diagnosis and treatment and to prevent dreaded complications in such patients.</p>


F1000Research ◽  
2019 ◽  
Vol 8 ◽  
pp. 1734
Author(s):  
Richard Menzies-Wilson ◽  
Gentle Wong ◽  
Prodip Das

We present a rare case of a four-year-old boy with a botyroid embryonal rhabdomyosarcoma of the right middle ear. Rhabdomyosarcoma is a soft tissue malignancy which is thought to originate from embryonic mesenchymal cells of striated skeletal muscle.  It is a disease primarily of children and is exceptionally rare in parameningeal regions.  The diagnosis is often delayed and easily misdiagnosed as aural polyp. Therefore, advanced disease is common at the time of diagnosis.  A four-year-old boy presented with a four-month history of recurrent left ear blood and pus discharge, otalgia and fevers. He attended his GP three times and paediatric A&E 13 times where he received antibiotics for presumed otitis media and externa. He was eventually referred to the otolaryngology department and underwent an examination under anaesthesia of ear and excisional biopsy of a suspicious aural polyp.  Staging chest CT and PET scan showed no loco-regional spread or distal metastasis. Magnetic resonance imaging demonstrated absence of invasion into adjacent organs.  Histology confirmed embryonal rhabdomyosarcoma, botryoid subtype.  Subsequent to the initial excision of the polyp, he was started on an ifosfamine, vincristine and actinomycin (IVA) chemotherapy regime in three weekly cycles for nine cycles with concomitant radiotherapy. Two weeks subsequent to his first chemotherapy dose he presented with a House-Brackmann II-III facial nerve palsy but no other middle ear complications. He was started on intravenous antibiotics and dexamethasone. The facial nerve palsy incompletely resolved with treatment.


2020 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Alejandra Peña-Juárez ◽  
Miguel Angel Medina-Andrade ◽  
Itzel Estefani Ríos Olivares ◽  
José Luis Colín-Ortíz ◽  
Marco Antonio Yamazaki-Nakashimada ◽  
...  

2020 ◽  
Vol 30 (12) ◽  
pp. 1957-1959
Author(s):  
Ye Yuan ◽  
Na Lu

AbstractKawasaki disease is the leading cause of acquired heart disease in infants and young children. Kawasaki disease that manifests as facial nerve palsy is extremely rare, and the diagnosis is challenging. We report a 4-month-old girl with Kawasaki disease who presented with fever, redness and cracking in the lips and oral cavity, and a right facial nerve palsy. The infant received intravenous immunoglobulin, acetyl salicylic acid, and warfarin. The patient’s fever subsided on the following day, and the right-sided facial nerve palsy was relieved a month later.


2021 ◽  
Author(s):  
Julia Loureiro Gaudencio ◽  
Hilton Mariano Mariano da Silva Júnior ◽  
Pedro Neves Fortunato

Context: Ramsay Hunt syndrome is a condition caused by the Varicella-Zoster Virus in the geniculate ganglion and leads to peripheral facial nerve palsy and erythematous vesicular rash in the affected area. It is a rare disorder but is the second most common cause of peripheral facial nerve palsy without trauma. Cerebral venous thrombosis is a rare cerebrovascular disease and responsible for only 0.5% of all strokes. Among its causes are oral contraceptives, infection in the central nervous system, systemic inflammations, and thrombophilia. Case report: We report the case of a previously healthy 29 years old woman diagnosed with Ramsay Hunt syndrome followed by cerebral venous thrombosis two weeks later. Her first admission to the hospital was due to pain in the face and a pulsing type right hemicranial headache. It started in the cervical region and was irradiated to the right retroorbital and auricular area, with difficulty contracting the right eyelid, otalgia, and vertigo. She used oral contraceptives, had two cesarean deliveries, and quitted smoking at 20 years old. She had multidirectional and bilateral nystagmus with fast phase to the left, right peripheral face paralysis, and crusts in the right ear canal. The patient was treated with aciclovir and prednisone, with good recovery. Two weeks later, she returned because of two episodes of convulsion and headache. Brain CTA (computed tomography angiography) showed cerebral venous thrombosis. Conclusion: Cerebral venous thrombosis is a rare complication of Ramsay Hunt Syndrome. It is important to stay alert to the development of vascular complications in these patients.


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