scholarly journals The rare skeletal variation of the congenital bifid rib

2019 ◽  
Vol 54 (2) ◽  
pp. 372-374
Author(s):  
Gregory TSOUCALAS ◽  
◽  
Konstantinos RAZOS ◽  
Eleni PANAGOULI ◽  
Ekaterini KRIONI ◽  
...  
Keyword(s):  
Bifid Rib

Case of oculo-auriculo-vertebral spectrum: rare clinical features

2021 ◽  
Vol 14 (3) ◽  
pp. e234181
Author(s):  
Daisy Khera ◽  
Saurabh Agarwal ◽  
Prawin Kumar ◽  
Kuldeep Singh
Keyword(s):  
Multidisciplinary Approach ◽  
Loud Sound ◽  
The Family ◽  
Bifid Rib ◽  
Depressor Anguli Oris ◽  
Bone Anchored Hearing Aid ◽  
Canal Atresia ◽  
Brain Stem Evoked Response ◽  
Evoked Response Audiometry

A 2-month-old boy presented to us with bilateral microtia, left lower motor neuron facial palsy, micrognathia, hemivertebra, bifid rib, bifid thumb and absent/hypoplastic right-sided depressor anguli oris. He had bilateral external auditory canal atresia, although response to loud sound was present. Brain stem evoked response audiometry (BERA) was advised at 3 months of age. Karyotype was normal. We diagnosed him as a case of oculo-auriculo-vertebral spectrum. Child was discharged on request by the family with the plan for bone-anchored hearing aid after BERA and plan for pinna and ear canal reconstruction at a later age but child did not come for any follow-up visit. On telephonic enquiry, it was found that he is thriving well but has developmental delay including speech delay. We conclude that children presenting with external ear abnormalities should be screened for multiple congenital anomalies so that a multidisciplinary approach to management can be planned.

scholarly journals Multiple Keratocysts of the Mandible in Association with Multiple Basal Epithelioma, Jaw Cysts and Bifid Rib Syndrome: A Rare Case Report

2014 ◽  
Vol 5 (1) ◽  
pp. 39-41
Author(s):  
Shahanavaj Imam Husen Khaji ◽  
Gayathri H Kulkarni ◽  
Harish S Kulkarni ◽  
Suryakant B Metkari ◽  
Reshma Kulkarni
Keyword(s):  
Case Report ◽  
Basal Cell Carcinoma ◽  
Cell Carcinoma ◽  
Basal Cell ◽  
Rare Case ◽  
Odontogenic Tumor ◽  
Keratocystic Odontogenic Tumor ◽  
Jaw Cysts ◽  
Rare Case Report ◽  
Bifid Rib

ABSTRACT Nevoid basal cell carcinoma syndrome is a syndrome with wide variety of manifestations ranging from oral lesions to skeletal deformities. It calls for due responsibility of maxillofacial surgeon to diagnose the syndrome because very often they are the first health professionals to see the patient for the treatment of keratocystic odontogenic tumor. Keratocystic odontogenic tumor (KCOT) has been the topic of numerous investigators and is known for its potentially aggressive behavior and significant rate of recurrences. Keratocystic odontogenic tumor often occurs as a solitary lesion, and in some instances multiple keratocysts may occur in association with a syndrome called Gorlin-Goltz syndrome (nevoid basal cell carcinoma, jaw cyst bifid rib basal cell nevus syndrome). Here, we present a case of multiple keratocysts in the mandible in association with skeletal, ocular and cutaneous anomalies in the given clinical scenario which has profound relevance in the clinical dental practice. How to cite this article Kulkarni GH, Khaji SI, Kulkarni HS, Metkari SB, Kulkarni R. Multiple Keratocysts of the Mandible in Association with Multiple Basal Epithelioma, Jaw Cysts and Bifid Rib Syndrome: A Rare Case Report. Int J Head Neck Surg 2014;5(1):39-41.

Multiple Nevoid Basal-Cell Epithelioma, Jaw Cysts and Bifid Rib

1960 ◽  
Vol 262 (18) ◽  
pp. 908-912 ◽  
Author(s):  
Robert J. Gorlin ◽  
Robert W. Goltz
Keyword(s):  
Basal Cell ◽  
Jaw Cysts ◽  
Basal Cell Epithelioma ◽  
Bifid Rib

Bifid Rib Anomaly: A Case Report

2013 ◽  
Vol 10 (4) ◽  
pp. 202-203
Author(s):  
Emine Dibek Misirlioglu ◽  
Meliksah Keskin ◽  
Serap Ozmen ◽  
Ufuk Sevgican ◽  
İlknur Bostanci
Keyword(s):  
Case Report ◽  
Bifid Rib

Pseudo-Pseudo-Hypoparathyroidism and Basal-Cell Nevus Syndrome

1972 ◽  
Vol 21 (1-2) ◽  
pp. 94-98
Author(s):  
Luc Goeminne
Keyword(s):  
Spina Bifida ◽  
Basal Cell Carcinoma ◽  
Cell Carcinoma ◽  
Short Stature ◽  
Basal Cell ◽  
Spina Bifida Occulta ◽  
Congenital Muscular Torticollis ◽  
Basal Cell Nevus Syndrome ◽  
Bifid Rib ◽  
Muscular Torticollis

SummaryA case is described of pseudo-pseudo-hypoparathyroidism, with the following symptoms: round face, large forehead, relative backwardness, short stature, relative obesity, congenital muscular torticollis, cervical fused vertebrae, spina bifida occulta cervicalis, bifid rib, bilateral brachymetacarpy IV. Some of these also occur in the basal-cell nevus syndrome. The patient does not however show a basal-cell carcinoma, nor mandibula cysts.

scholarly journals Bifid Rib in a male cadaver : Serendipic or Syndromic

2018 ◽  
Vol 7 (02) ◽  
pp. 103-107
Author(s):  
Amit Purushottam Tirpude ◽  
Manisha R Gaikwad ◽  
Pradhnya Tirpude ◽  
Arpan Haldar ◽  
Mantu Jain
Keyword(s):  
Case Report ◽  
Transverse Colon ◽  
Anterior Part ◽  
Digital Camera ◽  
Intercostal Space ◽  
X Rays ◽  
Male Cadaver ◽  
Bifid Rib ◽  
Associated Abnormalities

AbstractBifid rib presents usually as an isolated and asymptomatic finding on x-rays and cadaveric dissections. This may be due to atypical process of segmentation of developing somites. Sometimes it may occur with other malformations. Aim of the case report presented here was to give a description of the characteristics ofbifidrib and to look for any associated abnormalities. During routine dissection, bifid rib was found in thoraco-abdominal region of a male cadaver. The dimensions of the bifid rib were measured with digital vernier calliper of resolution 0.01mm and photographed using a digital camera. Survey of other regions of the cadaver was done by dissection. Bifurcation of anterior part of right third rib enclosing an additional intercostal space was found. Follow-up dissection in other regions of the cadaver revealed characteristics of Crohn's disease of jejunum, ileum, and transverse colon and signs of dysmorphism of both the kidneys. The knowledge of such variations will be of use to the clinicians, radiologist and anatomist to investigate any incidental bifid rib finding.

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